A case and literature review of orbital microcystic adnexal carcinoma

ABSTRACT

Microcystic adnexal carcinoma (MAC) is a very rare and locally aggressive sweat gland tumour. MAC has been well reported presenting as a periocular cutaneous lesion, rarely with subsequent direct orbital invasion and only once as a primary orbital lesion. Local recurrence is frequent after primary surgical excision and the role of adjuvant radiotherapy is ill-defined. We describe a case of orbital MAC treated successfully with radiotherapy after incomplete margin clearance post exenteration surgery and review the associated literature.

KEYWORDS:

• Microcystic adnexal carcinoma
• radiotherapy
• exenteration

Disclosure statement

The authors report no conflicts of interest. The authors alone are responsible for the content and writing of the paper.