Abstract
Type I Chiari deformity presents with diverse symptoms and signs which can be attributed to compression of structures at the foramen magnum. Bradycardia as a result of medullary compression has not been reported previously. A patient is described with type I Chiari deformity who presented with episodic profound sinus bradycardia for which a pacemaker was inserted before the diagnosis of cerebellar ectopia was finally made. Surgical decompression proved curative.