Necrotic Vasculitis in a Patient with Abdominal Fibromatosis and Guillain-Barré Syndrome

Abstract

The case of a 65-year-old woman presenting with Guillain-Barré syndrome is herein reported. Tomographic investigation revealed abdominal and retroperitoneal fibromatosis. During her hospitalization, renal involvement ensued, and subsequent renal biopsy demonstrated findings of crescentic pauci-immune glomerulonephritis negative for ANCA antibodies and with characteristics indicative of necrotic angiitis. The simultaneous existence of the three diseases in the same patient as well as the relation between necrotic vasculitis and G-B syndrome is speculated, and the relevant literature is reviewed.

Keywords:

• fibromatosis
• Guillain-Barré syndrome
• necrotic angiitis
• glomerulonephritis