Persistent Müllerian Duct Syndrome

Abstract

Persistent müllerian duct syndrome is a rare form of pseudohermaphroditism, in which well developed müllerian structures are present in an otherwise normal male, possibly resulting from absence of müllerian duct inhibiting factor. Two cases of the syndrome are presented. The diagnosis, as in most cases, was confirmed at herniorrhaphy or exploration for undescended testis.

Key words:

• cryptorchidism
• müllerian ducts
• pseudohermaphroditism.