Central Nervous System Involvement in Congenital Visceral Fibromatosis

Edward D. Adickes Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Paul Goodrich Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Joseph Auchmoedy Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Gayle Bickers Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Bruce Bowden Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Jack Koh Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Robert M. Nelson Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Robert M. Shuman Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

Richard B. Wilson Departments of Pathology and Laboratory Medicine, Pediatrics, Dermatology, Radiology, and Neurology, University of Nebraska Medical Center, Omaha, Nebraska, 68105

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Abstract

Congenital visceral myofibromatosis is an uncommon disorder characterized by multiple tumors of myofibroblastic origin in the neonatal period. The natural history of the disorder has been well delineated. The myofibro blast is the cell of origin of the tumor. This is a report of a patient in whom multiple mesenchymal tumors occurred in the CNS as well as in other organs. Light and electron microiscopic findings of the CNS lesions are similar to those of the somites and viscera.

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Central Nervous System Involvement in Congenital Visceral Fibromatosis

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Central Nervous System Involvement in Congenital Visceral Fibromatosis

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