Diffuse Pulmonary Arteriovenous Malformation in a Child with Polysplenia Syndrome

Sudesh Kapur Departments of Anatomic Pathology and Cardiology, Children's National Medical Center, Washington, DC, USA; Department of Pediatrics and Pathology, George Washington University School of Medicine, Washington, DC, USA

Jonathan Rome Departments of Anatomic Pathology and Cardiology, Children's National Medical Center, Washington, DC, USA; Department of Pediatrics and Pathology, George Washington University School of Medicine, Washington, DC, USA

Roma S. Chandra Departments of Anatomic Pathology and Cardiology, Children's National Medical Center, Washington, DC, USA; Department of Pediatrics and Pathology, George Washington University School of Medicine, Washington, DC, USA

Abstract

Pulmonary arteriovenous malformation (PAVM) is usually seen as a well-circumscribed cysticmass. In this communication we describe a diffuse arteriovenous malformation in a 5-month-old infant. The lesion was seen only at the microscopic level and was associated with abdominal heterotaxy, atrial situs solitus, polysplenia, interrupted inferior vena cava, atrial septal defect, and atrioventricular canal. This uncommon association may be within the spectrum of polysplenia syndrome.

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Diffuse Pulmonary Arteriovenous Malformation in a Child with Polysplenia Syndrome

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Diffuse Pulmonary Arteriovenous Malformation in a Child with Polysplenia Syndrome

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