545
Views
81
CrossRef citations to date
0
Altmetric
Review

Classification and therapeutic approaches in autoimmune hemolytic anemia: an update

Pages 607-618 | Published online: 10 Jan 2014

Keep up to date with the latest research on this topic with citation updates for this article.

Read on this site (4)

Luis Miguel Osorio-Toro, Jhon Herney Quintana-Ospina, Luis Álvaro Melo-Burbano, Paola Andrea Ruiz-Jiménez, Jorge Enrique Daza-Arana, Giovanna Patricia Rivas-Tafurt & Jorge Hernán Izquierdo-Loaiza. (2023) Autoimmune Hemolytic Anemia Caused by Cold Agglutinin Antibodies in Systemic Lupus erythematosus—a Rare Association: Case Report. Journal of Blood Medicine 14, pages 507-511.
Read now
Sigbjørn Berentsen, Alexander Röth, Ulla Randen, Bernd Jilma & Geir E Tjønnfjord. (2019) Cold agglutinin disease: current challenges and future prospects. Journal of Blood Medicine 10, pages 93-103.
Read now
Chattree Hantaweepant, Prat Pairattanakorn, Khemajira Karaketklang, Weerapat Owattanapanich & Yingyong Chinthammitr. (2019) Efficacy and safety of second-line treatment in Thai patients with primary warm-type autoimmune hemolytic anemia. Hematology 24:1, pages 720-726.
Read now
S. Ju. Smirnova, Ju. V. Sidorova, N. V. Tsvetaeva, O. F. Nikulina, B. V. Biderman, E. E. Nikulina, S. M. Kulikov & A. B. Sudarikov. (2016) Expansion of CD8+ cells in autoimmune hemolytic anemia. Autoimmunity 49:3, pages 147-154.
Read now

Articles from other publishers (77)

Jeremy W. Jacobs, Cristina A. Figueroa Villalba, Garrett S. Booth, Jennifer S. Woo, Laura D. Stephens & Brian D. Adkins. (2023) Clinical and epidemiological features of paroxysmal cold hemoglobinuria: a systematic review. Blood Advances 7:11, pages 2520-2527.
Crossref
Sigbjørn Berentsen, Bruno Fattizzo & Wilma Barcellini. (2023) The choice of new treatments in autoimmune hemolytic anemia: how to pick from the basket?. Frontiers in Immunology 14.
Crossref
Dafni MORIKI, Maria A. KARALEXI, Kassiani KEKKOU, Michalis KALOGIANNIS, Vassiliki PAPAEVANGELOU & Ioannis PETROCHEILOS. (2023) Rituximab as front-line treatment in refractory autoimmune hemolytic anemia. Minerva Pediatrics 74:6.
Crossref
Sigbjørn Berentsen. (2023) Sutimlimab for the Treatment of Cold Agglutinin Disease. HemaSphere 7:5, pages e879.
Crossref
Antimo Tessitore, Elena Putoto, Francesca RomanoFederico Verzegnassi, Egidio Barbi, Giorgio Cozzi & Emilia Parodi. (2022) Ittero, pallore e urine scure: e se fosse un’anemia emolitica autoimmune?. Medico e Bambino 41:7, pages 451-455.
Crossref
Omar Al jandale, Heba Jumah & Hasan Jamil. (2022) Hepatitis A virus infection is complicated by both pancytopenia and autoimmune hemolytic anemia (AIHA). Annals of Medicine and Surgery 78, pages 103765.
Crossref
Anthie Damianaki, Marianna Tzanoudaki, Maria Kanariou, Emmanouil Liatsis, Alexandros Panos, Alexandra Soldatou & Lydia Kossiva. (2022) Is Rituximab-Associated Hypogammaglobulinemia Always Linked to B-Cell Depletion?. Children 9:2, pages 295.
Crossref
Tyler A Finkenthal, Zackery Aldaher, Salman Ahmed & Louis DiValentin. (2021) Autoimmune Hemolytic Anemia Exacerbation Associated With COVID-19 Infection and Markedly Elevated Inflammatory Markers. Cureus.
Crossref
Jennifer Delun Williams, Ram K Jayaprakash, Heena Kithany & Mark Peter Tighe. (2021) How to use Donath-Landsteiner test to diagnose paroxysmal cold haemoglobinuria (PCH). Archives of disease in childhood - Education & practice edition, pages edpract-2020-319568.
Crossref
Vincenzo Roccaforte, Flavia Sciarini, Vanessa Proserpio, Ruggero Buonocore, Emanuela Marina Zavaroni, Silvia Burati, Marco Bussetti, Giammaria Liuzzi, Rosalba Monica Russo, Wanda Patrizia Porreca, Maria Luisa De Angelis, Carlo Federico Perno, Claudio Bonato & Stefano Pastori. (2021) Use of the reticulocyte channel warmed to 41 °C of the XN-9000 analyzer in samples with the presence of cold agglutinins. Hematology, Transfusion and Cell Therapy 43:2, pages 147-155.
Crossref
Nazaret Sánchez, Josune Zubicaray, Elena Sebastián, Eva Gálvez & Julián Sevilla. (2021) Anemia hemolítica autoinmune: revisión de casos. Anales de Pediatría 94:4, pages 206-212.
Crossref
María Nazaret Sánchez, Josune Zubicaray, Elena Sebastián, Eva Gálvez & Julián Sevilla. (2021) Autoimmune hemolytic anemia: Case review. Anales de Pediatría (English Edition) 94:4, pages 206-212.
Crossref
Aikaterini Voulgaridou & Theodosia A. Kalfa. (2021) Autoimmune Hemolytic Anemia in the Pediatric Setting. Journal of Clinical Medicine 10:2, pages 216.
Crossref
Shih-Hsuan Chao, Yuh-Lih Chang, Jiin-Cherng Yen, Hsien-Tzung Liao, Tsai-Hung Wu, Chia-Li Yu, Chang-Youh Tsai & Yueh-Ching Chou. (2020) Efficacy and safety of rituximab in autoimmune and microangiopathic hemolytic anemia: a systematic review and meta-analysis. Experimental Hematology & Oncology 9:1.
Crossref
Corie Borchert, Adam Herman, Megan Roth, Aimee C. Brooks & Steven G. Friedenberg. (2020) RNA sequencing of whole blood in dogs with primary immune-mediated hemolytic anemia (IMHA) reveals novel insights into disease pathogenesis. PLOS ONE 15:10, pages e0240975.
Crossref
Yuichiro Iwamoto, Takatoshi Anno, Katsumasa Koyama, Ryo Shirai, Hideaki Kaneto & Koichi Tomoda. (2020) Rapidly Exacerbating Autoimmune Hemolytic Anemia Together With Marked Cytokine Storm Triggered by Pneumonia Infection: A Case Report. Frontiers in Immunology 11.
Crossref
Ulrich Jäger, Wilma Barcellini, Catherine M. Broome, Morie A. Gertz, Anita Hill, Quentin A. Hill, Bernd Jilma, David J. Kuter, Marc Michel, Marco Montillo, Alexander Röth, Sacha S. Zeerleder & Sigbjørn Berentsen. (2020) Diagnosis and treatment of autoimmune hemolytic anemia in adults: Recommendations from the First International Consensus Meeting. Blood Reviews 41, pages 100648.
Crossref
Catherine M. Broome, Julia M. Cunningham, Megan Mullins, Xiaohui Jiang, Lauren C. Bylsma, Jon P. Fryzek & Adam Rosenthal. (2020) Increased risk of thrombotic events in cold agglutinin disease: A 10‐year retrospective analysis. Research and Practice in Thrombosis and Haemostasis 4:4, pages 628-635.
Crossref
M. Weli, A. Ben Hlima, R. Belhadj, B. Maalej, A. Elleuch, N. Mekki, L. Gargouri, T. Kamoun, M.-R. Barbouche & A. Mahfoudh. (2020) Diagnosis and management of autoimmune hemolytic anemia in children. Transfusion Clinique et Biologique 27:2, pages 61-64.
Crossref
Elena Aleksandrovna Poponina, E.V. Butina, A.V. Iovdii, O.D. Maksimov, G.A. Zaitseva & I.V. Paramonov. (2020) New Technology Capabilities of Direct Antiglobulin Test. Clinical oncohematology 13:4, pages 426-429.
Crossref
Dan-Tong Zhao, Yan-Min Liu, Ying Han, Hai-Ping Zhang, Yan Zhao & Hui-Ping Yan. (2020) Fluctuations of antimitochondrial antibodies and anti-gp210 antibody in a patient with primary biliary cholangitis and Sjögren syndrome with subsequent autoimmune hemolytic anemia. Medicine 99:3, pages e18856.
Crossref
Chunxia Chen, Lixin Wang, Bing Han, Li Qin & Binwu Ying. (2020) Autoimmune hemolytic anemia in hospitalized patients. Medicine 99:2, pages e18739.
Crossref
N. Jung, W.-J. Mayet, P.R. Mertens, J. Meyer (federführend)O.-A. Müller, M. Pfeifer, P. Schellinger, N. Weiss & C.-M. Wendtner. 2020. Rationelle Diagnostik und Therapie in der Inneren Medizin. Rationelle Diagnostik und Therapie in der Inneren Medizin B-1 B30-3 .
Ruth Perez. 2020. Rodak's Hematology. Rodak's Hematology 378 393 .
Øystein Sefland, Ulla Randen & Sigbjørn Berentsen. (2019) Development of Multiple Myeloma of the IgA Type in a Patient with Cold Agglutinin Disease: Transformation or Coincidence?. Case Reports in Hematology 2019, pages 1-6.
Crossref
Antoine Lafarge, R. Bertinchamp, C. Pichereau, S. Valade, A. Chermak, I. Theodose, E. Canet, V. Lemiale, B. Schlemmer, L. Galicier, E. Azoulay & E. Mariotte. (2018) Prognosis of autoimmune hemolytic anemia in critically ill patients. Annals of Hematology 98:3, pages 589-594.
Crossref
Sigbjørn Berentsen, Anita Hill, Quentin A. Hill, Tor Henrik Anderson Tvedt & Marc Michel. (2019) Novel insights into the treatment of complement-mediated hemolytic anemias. Therapeutic Advances in Hematology 10, pages 204062071987332.
Crossref
Nancy L. Van Buren. 2019. Transfusion Medicine and Hemostasis. Transfusion Medicine and Hemostasis 313 323 .
Isabella Menchetti, Yulia Lin, Christine Cserti-Gazdewich, Jenette Goldstein, Calvin Law, Alan Lazarus & Jeannie L. Callum. (2018) Complications of a severe autoimmune hemolytic anemia crisis: transfusional iron overload and gangrenous cholecystitis. Transfusion 58:12, pages 2777-2781.
Crossref
Alexandros Makis, Zoi Kanta, Dimitrios Kalogeropoulos & Nikoloaos Chaliasos. (2018) Anti-CD20 Treatment of Autoimmune Hemolytic Anemia Refractory to Corticosteroids and Azathioprine: A Pediatric Case Report and Mini Review. Case Reports in Hematology 2018, pages 1-7.
Crossref
Sigbjørn Berentsen. (2018) Complement Activation and Inhibition in Autoimmune Hemolytic Anemia: Focus on Cold Agglutinin Disease. Seminars in Hematology 55:3, pages 141-149.
Crossref
Ram Kalpatthi, Meredith A. Atkinson & Bradley A. Warady. 2018. Management of Anemia. Management of Anemia 199 218 .
Julia B. Felippe. 2017. Interpretation of Equine Laboratory Diagnostics. Interpretation of Equine Laboratory Diagnostics 243 249 .
Aryeh Shander, Mazyar Javidroozi & Gregg Lobel. (2017) Patient Blood Management in the Intensive Care Unit. Transfusion Medicine Reviews 31:4, pages 264-271.
Crossref
Silvia Gazzin, Flora Masutti, Libor Vitek & Claudio Tiribelli. (2017) The molecular basis of jaundice: An old symptom revisited. Liver International 37:8, pages 1094-1102.
Crossref
Megan MullinsXiaohui JiangLauren C. BylsmaJon P. FryzekHeidi ReichertEvan C. Chen, Shivaani Kummar & Adam Rosenthal. (2017) Cold agglutinin disease burden: a longitudinal analysis of anemia, medications, transfusions, and health care utilization. Blood Advances 1:13, pages 839-848.
Crossref
Mathieu Uzzan, Lionel Galicier, Jean-Marc Gornet, Eric Oksenhendler, Claire Fieschi, Matthieu Allez, Yoram Bouhnik, Julien Kirchgesner, David Boutboul, Xavier Treton, Laurence Gérard, Matthieu Mahévas, Jacques Cosnes & Aurélien Amiot. (2017) Autoimmune cytopenias associated with inflammatory bowel diseases: Insights from a multicenter retrospective cohort. Digestive and Liver Disease 49:4, pages 397-404.
Crossref
Marc Michel, Louis Terriou, Francoise Roudot-Thoraval, Mohamed Hamidou, Mikael Ebbo, Guillaume Le Guenno, Lionel Galicier, Sylvain Audia, Bruno Royer, Anne-Sophie Morin, Jean Marie Michot, Arnaud Jaccard, Laurent Frenzel, Mehdi Khellaf & Bertrand Godeau. (2017) A randomized and double-blind controlled trial evaluating the safety and efficacy of rituximab for warm auto-immune hemolytic anemia in adults (the RAIHA study). American Journal of Hematology 92:1, pages 23-27.
Crossref
Theodosia A. Kalfa. (2016) Warm antibody autoimmune hemolytic anemia. Hematology 2016:1, pages 690-697.
Crossref
Lauren PommertHayley FriedmanDavid WathenShermini Saini. (2016) Case 3: Acute Jaundice in a 16-year-old Boy. Pediatrics In Review 37:12, pages 542-545.
Crossref
Rong Fu, Siyang Yan, Xiaoming Wang, Guojin Wang, Wen Qu, Huaquan Wang, Yuhong Wu, Hong Liu, Jia Song, Jin Guan, Limin Xing, Erbao Ruan, Lijuan Li, Hui Liu & Zonghong Shao. (2016) A monocentric retrospective study comparing pulse cyclophosphamide therapy versus low dose rituximab in the treatment of refractory autoimmune hemolytic anemia in adults. International Journal of Hematology 104:4, pages 462-467.
Crossref
Rachel C. Chiaroni-Clarke, Jane E. Munro & Justine A. Ellis. (2016) Sex bias in paediatric autoimmune disease – Not just about sex hormones?. Journal of Autoimmunity 69, pages 12-23.
Crossref
Hajime Yasuda, Miyuki Tsutsui, Yasunori Ota, Kyohei Misawa, Akihiko Gotoh, Yasuharu Hamano & Norio Komatsu. (2016) Blastic plasmacytoid dendritic cell neoplasm accompanied by autoimmune hemolytic anemia achieving complete remission with hydroxyurea and steroids. Geriatrics & Gerontology International 16:3, pages 396-398.
Crossref
Wan‐Yi Hsu, Shyh‐Shin Chiou, Yu‐Mei Liao, Hsiu‐Lan Shu, Yu‐Sheng Zeng, Cheong‐Chew Wong & Pei‐Chin Lin. (2015) Successful management of multilineage autoimmune cytopenia complicated with severe infection and deep vein thrombosis in a patient with Hodgkin lymphoma post‐autologous hematopoietic stem cell transplantation. Pediatric Transplantation 20:1, pages 168-171.
Crossref
Emmanuel I. Gonzalez-Moreno, Sylvia A. Martinez-Cabriales, Miguel A. Cruz-Moreno, Omar D. Borjas-Almaguer, Carlos A. Cortez-Hernandez, Francisco J. Bosques-Padilla, Aldo A. Garza, Jose A. Gonzalez-Gonzalez, Diego Garcia-Compean, Jorge Ocampo-Candiani & Hector J. Maldonado-Garza. (2016) Primary biliary cholangitis associated with warm autoimmune hemolytic anemia. Journal of Digestive Diseases 17:2, pages 128-131.
Crossref
Thomas J. Divers. 2016. Equine Clinical Immunology. Equine Clinical Immunology 47 54 .
Valentina Giudice, Rosa Rosamilio, Idalucia Ferrara, Elisa Seneca, Bianca Serio & Carmine Selleri. (2016) Efficacy and safety of splenectomy in adult autoimmune hemolytic anemia. Open Medicine 11:1, pages 374-380.
Crossref
Aryeh Shander, Lena M. Napolitano & Margit Kaufman. 2016. Principles of Adult Surgical Critical Care. Principles of Adult Surgical Critical Care 295 312 .
Xiangmao Bu, Tenglong Zhang, Chunhong Wang, Tao Ren & Zhenke Wen. (2015) IL-33 reflects dynamics of disease activity in patients with autoimmune hemolytic anemia by regulating autoantibody production. Journal of Translational Medicine 13:1.
Crossref
M. Becheur, B. Bouslama, H. Slama & N.E.H. Toumi. (2015) Anémie hémolytique auto-immune de l’enfant. Transfusion Clinique et Biologique 22:5-6, pages 291-298.
Crossref
Bi-Juan LiXi YuanYuan-Jun Jiang Ning-LiXiang-Wu ShuKai-Liang Liu. (2015) Retrospective analysis of 30 severe autoimmune hemolytic anemia patients treated by whole blood exchange transfusion. Transfusion 55:9, pages 2231-2237.
Crossref
Chaturaka Rodrigo, Senaka Rajapakse & Lallindra Gooneratne. (2015) Rituximab in the treatment of autoimmune haemolytic anaemia. British Journal of Clinical Pharmacology 79:5, pages 709-719.
Crossref
I. V. Obraztsov & A. P. Vasilieva. (2015) Immune haemolysis in a patient after haematopoietic stem cell retransplantation: case report and a literature review. Russian Journal of Children Hematology and Oncology:1, pages 75-79.
Crossref
Sigbjørn Berentsen. (2015) Role of Complement in Autoimmune Hemolytic Anemia. Transfusion Medicine and Hemotherapy 42:5, pages 303-310.
Crossref
Abdulgabar Salama. (2015) Clinically and/or Serologically Misleading Findings Surrounding Immune Haemolytic Anaemias. Transfusion Medicine and Hemotherapy 42:5, pages 311-315.
Crossref
Sigbjørn Berentsen & Tatjana Sundic. (2015) Red Blood Cell Destruction in Autoimmune Hemolytic Anemia: Role of Complement and Potential New Targets for Therapy. BioMed Research International 2015, pages 1-11.
Crossref
Y. Wang, W. Zhou & Z. Zhang. (2014) Successful treatment of warm-type haemolytic anaemia with bortezomib in a rituximab-failed systemic lupus erythematosus patient. Rheumatology 54:1, pages 194-195.
Crossref
Loic Raffray, Marie-Catherine Receveur, Mathilde Beguet, Pierre Lauroua, Thierry Pistone & Denis Malvy. (2014) Severe delayed autoimmune haemolytic anaemia following artesunate administration in severe malaria: a case report. Malaria Journal 13:1.
Crossref
Mathilde Roumier, Valentine Loustau, Constance Guillaud, Laetitia Languille, Matthieu Mahevas, Mehdi Khellaf, Nicolas Limal, France Noizat-Pirenne, Bertrand Godeau & Marc Michel. (2014) Characteristics and outcome of warm autoimmune hemolytic anemia in adults: New insights based on a single-center experience with 60 patients. American Journal of Hematology 89:9, pages E150-E155.
Crossref
Angela Belsito, Dario Costa & Claudio Napoli. (2014) Blood group genotyping for patients with autoimmune hemolytic anemia. Translational Research 164:2, pages 177-178.
Crossref
J. M. Vagace, R. Bajo & G. Gervasini. (2014) Diagnostic and therapeutic challenges of primary autoimmune haemolytic anaemia in children. Archives of Disease in Childhood 99:7, pages 668-673.
Crossref
Ju Shi, Eileen L. Rose, Andrew Singh, Sami Hussain, Nancy E. Stagliano, Graham C. Parry & Sandip Panicker. (2014) TNT003, an inhibitor of the serine protease C1s, prevents complement activation induced by cold agglutinins. Blood 123:26, pages 4015-4022.
Crossref
Yanjun Wu, Jiaping Zhang & Jun Wu. (2014) Autoimmune hemolytic anemia occurred in burn patient: A case report. Burns 40:3, pages e9-e11.
Crossref
M. Michel. (2014) Warm autoimmune hemolytic anemia: Advances in pathophysiology and treatment. La Presse Médicale 43:4, pages e97-e104.
Crossref
Hyo Jeong ChangDong Hyun SinnSung Gyun ChoTae Hoon OhTae Joo JeonWon Chang ShinWon Choong Choi. (2014) Pure red-cell aplasia and autoimmune hemolytic anemia in a patient with acute hepatitis A. Clinical and Molecular Hepatology 20:2, pages 204.
Crossref
Abdulgabar Salama, Dirk Hartnack, Hans-Walter Lindemann, Hans-Joachim Lange, Mathias Rummel & Andreas Loew. (2014) The Effect of Erythropoiesis-Stimulating Agents in Patients with Therapy-Refractory Autoimmune Hemolytic Anemia. Transfusion Medicine and Hemotherapy 41:6, pages 462-468.
Crossref
J.E. Hendrickson & C.A. Tormey. 2014. Pathobiology of Human Disease. Pathobiology of Human Disease 3068 3080 .
David T. Teachey & Michele P. Lambert. (2013) Diagnosis and Management of Autoimmune Cytopenias in Childhood. Pediatric Clinics of North America 60:6, pages 1489-1511.
Crossref
Michael T. McEvoyAryeh Shander. (2013) Anemia, Bleeding, and Blood Transfusion in the Intensive Care Unit: Causes, Risks, Costs, and New Strategies. American Journal of Critical Care 22:6, pages eS1-eS13.
Crossref
Amy E. DeZern, Jeffrey Pu, Michael A. McDevitt, Richard J. Jones & Robert A. Brodsky. (2013) Burst-forming unit–erythroid assays to distinguish cellular bone marrow failure disorders. Experimental Hematology 41:9, pages 808-816.
Crossref
M. Khellaf & B. Godeau. (2013) Réanimation et cytopénies auto-immunes. Diagnostic et modalités de prise en chargeAutoimmune cytopenia in the intensive care unit: Diagnosis and management. Réanimation 22:5, pages 490-500.
Crossref
G K Wong, S Goldacker, C Winterhalter, B Grimbacher, H Chapel, M Lucas, D Alecsandru, D McEwen, I Quinti, H Martini, R E Schmidt, D Ernst, T Espanol, A Vidaller, J Carbone, E Fernandez-Cruz, V Lougaris, A Plebani, N Kutukculer, L I Gonzalez-Granado, R Contreras, S Kiani-Alikhan, M A A Ibrahim, J Litzman, A Jones, H B Gaspar, L Hammarstrom, U Baumann, K Warnatz & A P Huissoon. (2013) Outcomes of splenectomy in patients with common variable immunodeficiency (CVID): a survey of 45 patients. Clinical and Experimental Immunology 172:1, pages 63-72.
Crossref
Bertrand Godeau. 2013. Lupus érythémateux. Lupus érythémateux 283 287 .
Devika Lal & Christopher D. Hillyer. 2013. Transfusion Medicine and Hemostasis. Transfusion Medicine and Hemostasis 317 325 .
Lin Xu, Tenglong Zhang, Zhongmin Liu, Qinchuan Li, Zengguang Xu & Tao Ren. (2012) Critical role of Th17 cells in development of autoimmune hemolytic anemia. Experimental Hematology 40:12, pages 994-1004.e4.
Crossref
Daan Dierickx, Emilie Beke, Timothy Devos & André Delannoy. (2012) The Use of Monoclonal Antibodies in Immune-Mediated Hematologic Disorders. Medical Clinics of North America 96:3, pages 583-619.
Crossref
Sigbjørn Berentsen. (2012) Flere sykdommer med samme kliniske presentasjon. Tidsskrift for Den norske legeforening 132:8, pages 968-968.
Crossref

Reprints and Corporate Permissions

Please note: Selecting permissions does not provide access to the full text of the article, please see our help page How do I view content?

To request a reprint or corporate permissions for this article, please click on the relevant link below:

Academic Permissions

Please note: Selecting permissions does not provide access to the full text of the article, please see our help page How do I view content?

Obtain permissions instantly via Rightslink by clicking on the button below:

If you are unable to obtain permissions via Rightslink, please complete and submit this Permissions form. For more information, please visit our Permissions help page.