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Articles

Survival in patients with pulmonary arterial hypertension associated with systemic sclerosis from a Swedish single centre: prognosis still poor and prediction difficult

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Pages 127-132 | Accepted 13 Jul 2010, Published online: 21 Sep 2010

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I Bartosik, K Andréasson, M Starck, A Scheja & R Hesselstrand. (2014) Vascular events are risk factors for anal incontinence in systemic sclerosis: a study of morphology and functional properties measured by anal endosonography and manometry. Scandinavian Journal of Rheumatology 43:5, pages 391-397.
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David Kylhammar, Liselotte Persson, Roger Hesselstrand & Göran Rådegran. (2014) Prognosis and response to first-line single and combination therapy in pulmonary arterial hypertension. Scandinavian Cardiovascular Journal 48:4, pages 223-233.
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Yuichiro Shirai, Hidekata Yasuoka, Tsutomu Takeuchi, Toru Satoh & Masataka Kuwana. (2013) Intravenous epoprostenol treatment of patients with connective tissue disease and pulmonary arterial hypertension at a single center. Modern Rheumatology 23:6, pages 1211-1220.
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R Hesselstrand, A Scheja & DM Wuttge. (2012) Scleroderma renal crisis in a Swedish systemic sclerosis cohort: survival, renal outcome, and RNA polymerase III antibodies as a risk factor. Scandinavian Journal of Rheumatology 41:1, pages 39-43.
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A Borowiec, R Dabrowski, J Wozniak, S Jasek, T Chwyczko, I Kowalik, E Musiej-Nowakowska & H Szwed. (2012) Cardiovascular assessment of asymptomatic patients with juvenile-onset localized and systemic scleroderma: 10 years prospective observation. Scandinavian Journal of Rheumatology 41:1, pages 33-38.
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A Scheja, M Wildt, DM Wuttge & R Hesselstrand. (2011) Progressive capillary loss over a decade in patients with systemic sclerosis, in particular in patients with early digital ischaemic manifestations. Scandinavian Journal of Rheumatology 40:6, pages 457-461.
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Articles from other publishers (34)

Anji Xiong, Qingting Liu, Jiaxun Zhong, Yuzi Cao, Qilang Xiang, Ziyi Hu, Shifeng Zhou, Zhuoyao Song, Huini Chen, Yan Zhang, Hongxu Cui & Shiquan Shuai. (2022) Increased risk of mortality in systemic sclerosis-associated pulmonary hypertension: a systemic review and meta-analysis. Advances in Rheumatology 62:1.
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Bekir ÇALAPKORUR, Erkan DEMİRCİ, Samet KARAHAN, Kemal EROL & Tayfun AKALIN. (2022) Nailfold capillaroscopic pattern and modified Rodnan skin score associated with deterioration of right ventricle functions in systemic sclerosis patients without overt pulmonary hypertensionAşikâr pulmoner hipertansiyonu olmayan sistemik sklerozlu hastalarda tırnak kapilaroskopi bulguları ve modifiye Rodnan skoru sağ ventrikül fonksiyonlarında bozulma ile ilişkilidir. Journal of Medicine and Palliative Care 3:3, pages 188-194.
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Michael Hughes, Elisabetta Zanatta, Robert D Sandler, Jérôme Avouac & Yannick Allanore. (2022) Improvement with time of vascular outcomes in systemic sclerosis: a systematic review and meta-analysis study. Rheumatology 61:7, pages 2755-2769.
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Dirk M Wuttge, Anting L Carlsen, Gabriel Teku, Marie Wildt, Göran Rådegran, Mauno Vihinen, Niels H H Heegaard & Roger Hesselstrand. (2022) Circulating plasma microRNAs in systemic sclerosis-associated pulmonary arterial hypertension. Rheumatology 61:1, pages 309-318.
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Clara Hjalmarsson, Barbro Kjellström, Kjell Jansson, Magnus Nisell, David Kylhammar, Mohammad Kavianipour, Göran Rådegran, Stefan Söderberg, Gerhard Wikström, Dirk M. Wuttge & Roger Hesselstrand. (2021) Early risk prediction in idiopathic versus connective tissue disease-associated pulmonary arterial hypertension: call for a refined assessment . ERJ Open Research 7:3, pages 00854-2020.
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Zoe Brown, Susanna Proudman, Kathleen Morrisroe, Wendy Stevens, Dylan Hansen & Mandana Nikpour. (2021) Screening for the early detection of pulmonary arterial hypertension in patients with systemic sclerosis: A systematic review and meta-analysis of long-term outcomes. Seminars in Arthritis and Rheumatism 51:3, pages 495-512.
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Yuxuan Jiang, Matthew A. Turk & Janet E. Pope. (2020) Factors associated with pulmonary arterial hypertension (PAH) in systemic sclerosis (SSc). Autoimmunity Reviews 19:9, pages 102602.
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Colletti, Galardi, Santis, Guidelli, Giannatale, Luigi & Antinozzi. (2019) Exosomes in Systemic Sclerosis: Messengers Between Immune, Vascular and Fibrotic Components?. International Journal of Molecular Sciences 20:18, pages 4337.
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Michael H Lee & Todd M Bull. (2019) The role of pulmonary arterial hypertension-targeted therapy in systemic sclerosis. F1000Research 8, pages 2124.
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Bodil Ivarsson, Roger Hesselstrand, Göran Rådegran & Barbro Kjellström. (2018) Health-related quality of life, treatment adherence and psychosocial support in patients with pulmonary arterial hypertension or chronic thromboembolic pulmonary hypertension. Chronic Respiratory Disease 16, pages 147997231878790.
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Kathleen D. Kolstad, Shufeng Li, Virginia Steen, Lorinda Chung, Marcy B. Bolster, Mary Ellen Csuka, Chris T. Derk, Robyn T. Domsic, Aryeh Fischer, Tracy Frech, Richard Furie, Daniel Furst, Avram Z. Goldberg, Mardi Gomberg-Maitland, Jessica Gordon, Faye Hant, Nicholas Hill, Monique Hinchcliff, Evelyn Horn, Laura Hummers, Vivien Hsu, Susanna Kafaja, Firas Kassab, Dinesh Khanna, Thomas A. Medsger, Ioana Preston, Jerry Molitor, Lesley Saketkoo, Lee Shapiro, Elena Schiopu, Rick Silver, Robert Simms, John Varga & Frederick Wigley. (2018) Long-Term Outcomes in Systemic Sclerosis-Associated Pulmonary Arterial Hypertension From the Pulmonary Hypertension Assessment and Recognition of Outcomes in Scleroderma Registry (PHAROS). Chest 154:4, pages 862-871.
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Anna-Maria Hoffmann-Vold, Roger Hesselstrand, Håvard Fretheim, Thor Ueland, Arne K. Andreassen, Cathrine Brunborg, Vyacheslav Palchevskiy, Øyvind Midtvedt, Torhild Garen, Pål Aukrust, John A. Belperio & Øyvind Molberg. (2018) CCL21 as a Potential Serum Biomarker for Pulmonary Arterial Hypertension in Systemic Sclerosis. Arthritis & Rheumatology 70:10, pages 1644-1653.
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Anna-Maria Hoffmann-Vold, Håvard Fretheim, Øyvind Midtvedt, Karin Kilian, Marianne Angelshaug, Asad Chaudhary, Ragnar Gunnarsson, Cathrine Brunborg, Torhild Garen, Arne K Andreassen, Einar Gude & Øyvind Molberg. (2018) Frequencies of borderline pulmonary hypertension before and after the DETECT algorithm: results from a prospective systemic sclerosis cohort. Rheumatology 57:3, pages 480-487.
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Hiroyuki Nakamura, Masaru Kato, Toshitaka Nakaya, Michihiro Kono, Shun Tanimura, Takahiro Sato, Yuichiro Fujieda, Kenji Oku, Hiroshi Ohira, Toshiyuki Bohgaki, Shinsuke Yasuda, Ichizo Tsujino, Masaharu Nishimura & Tatsuya Atsumi. (2017) Decreased haptoglobin levels inversely correlated with pulmonary artery pressure in patients with pulmonary arterial hypertension. Medicine 96:43, pages e8349.
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Cinzia Rotondo, Emanuela Praino, Mariangela Nivuori, Francesca di Serio, Giovanni Lapadula & Florenzo Iannone. (2017) No changes in N-terminal pro-brain natriuretic peptide in a longitudinal cohort of patients with systemic sclerosis-associated pulmonary arterial hypertension on therapy with bosentan. International Journal of Rheumatic Diseases 20:1, pages 90-96.
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Nadera Methia, Samia Latreche, Omar Ait Mokhtar, Jean-Jacques Monsuez & Salim Benkhedda. (2016) Assessment for Pulmonary Artery Hypertension Using Clinical and Echocardiographic Criteria in Patients With Systemic Sclerosis. The American Journal of the Medical Sciences 352:4, pages 343-347.
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Lorenzo Cavagna, Veronica Codullo, Stefano Ghio, Carlo Alberto Scirè, Eleonora Guzzafame, Laura Scelsi, Silvia Rossi, Carlomaurizio Montecucco & Roberto Caporali. (2016) Undiagnosed connective tissue diseases. Medicine 95:39, pages e4827.
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Bodil Ivarsson, Björn Ekmehag & Trygve Sjöberg. (2016) Support Experienced by Patients Living with Pulmonary Arterial Hypertension and Chronic Thromboembolic Pulmonary Hypertension. Heart, Lung and Circulation 25:1, pages 35-40.
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Antonia Valenzuela, Saranya Nandagopal, Virginia D. Steen & Lorinda Chung. (2015) Monitoring and Diagnostic Approaches for Pulmonary Arterial Hypertension in Patients with Systemic Sclerosis. Rheumatic Disease Clinics of North America 41:3, pages 489-506.
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Sang Yeob LeeSang Woo YimJun Yong ParkWon Tae ChungSung Won Lee. (2015) Correlation of Cardiothoracic Ratio and Right Ventricular Systolic Pressure in Systemic Sclerosis. Journal of Rheumatic Diseases 22:1, pages 19.
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Lorinda Chung, Harrison W. Farber, Raymond Benza, Dave P. Miller, Lori Parsons, Paul M. Hassoun, Michael McGoon, Mark R. Nicolls & Roham T. Zamanian. (2014) Unique Predictors of Mortality in Patients With Pulmonary Arterial Hypertension Associated With Systemic Sclerosis in the REVEAL Registry. Chest 146:6, pages 1494-1504.
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Kristin B. Highland. (2014) Recent advances in scleroderma-associated pulmonary hypertension. Current Opinion in Rheumatology 26:6, pages 637-645.
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Mike O. Becker, Angela Kill, Marissa Kutsche, Jeannine Guenther, Angelika Rose, Christoph Tabeling, Martin Witzenrath, Anja A. Kühl, Harald Heidecke, Hossein A. Ghofrani, Henning Tiede, Ralph T. Schermuly, Nils Nickel, Marius M. Hoeper, Ivo Lukitsch, Maik Gollasch, Wolfgang M. Kuebler, Sebastian Bock, Gerd R. Burmester, Duska Dragun & Gabriela Riemekasten. (2014) Vascular Receptor Autoantibodies in Pulmonary Arterial Hypertension Associated with Systemic Sclerosis. American Journal of Respiratory and Critical Care Medicine 190:7, pages 808-817.
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Svetlana I. Nihtyanova, Benjamin E. Schreiber, Voon H. Ong, Daniel Rosenberg, Pia Moinzadeh, J. Gerrard Coghlan, Athol U. Wells & Christopher P. Denton. (2014) Prediction of Pulmonary Complications and Long-Term Survival in Systemic Sclerosis. Arthritis & Rheumatology 66:6, pages 1625-1635.
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Lorinda Chung, Robyn T. Domsic, Bharathi Lingala, Firas Alkassab, Marcy Bolster, M. E. Csuka, Chris Derk, Aryeh Fischer, Tracy Frech, Daniel E. Furst, Mardi Gomberg-Maitland, Monique Hinchcliff, Vivien Hsu, Laura K. Hummers, Dinesh Khanna, Thomas A. MedsgerJr.Jr., Jerry A. Molitor, Ioana R. Preston, Elena Schiopu, Lee Shapiro, Richard Silver, Robert Simms, John Varga, Jessica K. Gordon & Virginia D. Steen. (2014) Survival and Predictors of Mortality in Systemic Sclerosis-Associated Pulmonary Arterial Hypertension: Outcomes From the Pulmonary Hypertension Assessment and Recognition of Outcomes in Scleroderma Registry. Arthritis Care & Research 66:3, pages 489-495.
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Bodil Ivarsson, Björn EkmehagRoger HesselstrandGoran RadegranTrygve Sjöberg. (2014) Perceptions of Received Information, Social Support, and Coping in Patients with Pulmonary Arterial Hypertension or Chronic Thromboembolic Pulmonary Hypertension. Clinical Medicine Insights: Circulatory, Respiratory and Pulmonary Medicine 8, pages CCRPM.S18586.
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Ryan J. TedfordJames O. MuddReda E. GirgisStephen C. MathaiAri L. ZaimanTraci Housten-HarrisDanielle BoyceBenjamin W. KelemenAnita C. BacherAmi A. ShahLaura K. HummersFredrick M. WigleyStuart D. RussellRajeev SaggarRajan SaggarW. Lowell MaughanPaul M. HassounDavid A. Kass. (2013) Right Ventricular Dysfunction in Systemic Sclerosis–Associated Pulmonary Arterial Hypertension. Circulation: Heart Failure 6:5, pages 953-963.
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Guillaume Lefèvre, Luc Dauchet, Eric Hachulla, David Montani, Vincent Sobanski, Marc Lambert, Pierre-Yves Hatron, Marc Humbert & David Launay. (2013) Survival and Prognostic Factors in Systemic Sclerosis-Associated Pulmonary Hypertension: A Systematic Review and Meta-Analysis. Arthritis & Rheumatism 65:9, pages 2412-2423.
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Ami A. Shah & Fredrick M. Wigley. (2013) My Approach to the Treatment of Scleroderma. Mayo Clinic Proceedings 88:4, pages 377-393.
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Y. Shirai, H. Yasuoka, Y. Okano, T. Takeuchi, T. Satoh & M. Kuwana. (2012) Clinical characteristics and survival of Japanese patients with connective tissue disease and pulmonary arterial hypertension: a single-centre cohort. Rheumatology 51:10, pages 1846-1854.
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J. E. Pope. (2012) Survival is improving in systemic sclerosis: true or false?. Rheumatology 51:6, pages 959-961.
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Chintan S. Desai, Daniel C. Lee & Sanjiv J. Shah. (2011) Systemic sclerosis and the heart. Current Opinion in Rheumatology 23:6, pages 545-554.
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GANESH SUBRAMANIAN & SANJAY MEHTA. (2011) Treatment of Pulmonary Arterial Hypertension: Great Expectations!. The Journal of Rheumatology 38:3, pages 403-405.
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