Rare skin cancer: A population-based cancer registry descriptive study of 151 consecutive cases diagnosed between 1980 and 2004.

Figures & data

Table I.  Histological types of cutaneous sarcomas in the Doubs between 1980 and 2004.

Type of sarcomas	N	(%)	Localization
Dermatofibrosarcoma	31	52.5	Tr: 12; UL: 6; LL: 4; H: 7; UK: 2
Malignant fibrous histiocytoma	7	11.9	Tr: 2, UL: 2, H: 3
Atypical fibroxanthoma	1	1.7	H
Leiomyosarcoma	8	13.6	Tr: 3; LL: 3; UL: 1; H: 1
Liposarcoma	5	8.5	UL: 2; LL: 3
Epithelioid sarcoma	2	3.3	H: 2
Angiosarcoma	4	6.8	UL: 2; Tr: 2
Clear cell sarcoma	1	1.7	H

H: head; Tr: Trunk; UL: upper limb; LL: lower limb; UK: unknown.

Table II.  New cases and standardized incidence rate (SIR) and crude incidence (CI) of rare skin cancers; Ci: 95% confidence interval 95% per 100 000 persons per year in the Doubs from 1980 to 2004.

Periods	New cases	SIR	Ci min	Ci max	CI
1980–1984	8	0.25	0.07	0.43	0.33
1985–1989	10	0.32	0.11	0.53	0.41
1990–1994	28	0.83	0.50	1.15	1.14
1995–1999	40	1.03	0.69	1.38	1.61
2000–2004	65	1.50	1.09	1.91	2.56
1980–2004	151	0.82	0.68	0.96	1.23

Table III.  Standardized incidence rate (SIR) and crude incidence (CI) of rare skin cancers; Ci: 95% confidence interval per 100 000 persons per year in the Doubs from 1980 to 2004.

Types of tumours (n)	SIR	Ci min	Ci max	CI
Sarcoma (59)	0.37	0.27	0.47	0.48
Adnexal carcinoma (35)	0.16	0.10	0.22	0.28
Merkel cell carcinoma (27)	0.13	0.08	0.18	0.22
Paget's disease (27)	0.15	0.09	0.21	0.22