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Research Article

A roadmap to surgery in osteogenesis imperfecta: results of an international collaboration of patient organizations and interdisciplinary care teams

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Figures & data

Figure 1. Process to develop a roadmap to surgery in osteogenesis imperfecta with international collaboration of patient organizations and interdisciplinary care teams.

Figure 1. Process to develop a roadmap to surgery in osteogenesis imperfecta with international collaboration of patient organizations and interdisciplinary care teams.

Figure 2. Elements of an interdisciplinary approach for surgical decision-making.

Figure 2. Elements of an interdisciplinary approach for surgical decision-making.

Figure 3. a. 15-year-old female with OI type III, treated with bisphosphonates, ambulatory with multiple fractures over a pre-existing flexible nail.

b. Lateral closing wedge at the CORA, 4.5 mm flexible nail together with 6-hole 3.5 mm locking plate for length and rotational stability.

c. Union without recurrent fractures or deformity at 2 months’ follow-up.

d. Union without recurrent fractures or deformity at 2 years and 5 months’ follow-up.

Figure 3. a. 15-year-old female with OI type III, treated with bisphosphonates, ambulatory with multiple fractures over a pre-existing flexible nail.b. Lateral closing wedge at the CORA, 4.5 mm flexible nail together with 6-hole 3.5 mm locking plate for length and rotational stability.c. Union without recurrent fractures or deformity at 2 months’ follow-up.d. Union without recurrent fractures or deformity at 2 years and 5 months’ follow-up.

Figure 5. a. Severe deformity of the upper extremity in an 8-year-old patient with OI type III. Double osteotomy of the humerus and telescopic rodding was planned plus a double corrective radius and ulna osteotomy with a K-wire fixation inserted from opposite sides through the growth plates, thus allowing for telescoping.

b. Postoperative follow-up at 5 years. The amount of telescoping of the nail in the humerus corresponds with length without K-wire in radius and ulna due to growth.

Figure 5. a. Severe deformity of the upper extremity in an 8-year-old patient with OI type III. Double osteotomy of the humerus and telescopic rodding was planned plus a double corrective radius and ulna osteotomy with a K-wire fixation inserted from opposite sides through the growth plates, thus allowing for telescoping.b. Postoperative follow-up at 5 years. The amount of telescoping of the nail in the humerus corresponds with length without K-wire in radius and ulna due to growth.

Figure 7. Feedback loop for OI surgery.

Figure 7. Feedback loop for OI surgery.