Post syringomyelia progressive muscular atrophy: A late sequel to syringomyelia?

Figures & data

Table 1. Summary of clinical features of the 8 cases. For regions of neuraxis involvement, C—cervical, T—thoracic, LS—lumbosacral.

			Early clinical		Late clinical progression
Case no.	Age onset	Etiology of SM	Age at first surgical treatment	Clinical signs regions of spinal involvement at onset or time of early surgery	Symptoms progression late spinal regions involvement	Age at late evaluation	Interval initial onset to onset of progression
1	18	Chiari	31	Headache, shoulder weakness (C)	Motor, left arm only(C)	56	25 years
2		Chiari	52	Headache, Right hand sensory loss, leg weakness (C, T, LS)	Progressive motor atrophy and weakness. (C, T, LS)	72	20
3	52	Post-inflammatory	43	Leg weakness (C, T, LS)	Progressive pain, and sensory loss in left arm and both legs. (C,T,LS)	73	30
4	30	Chiari	36	Left arm and leg weakness (C, T, LS)	Weakness, Pain (C, T, LS)		20
5	39	Post trauma	39	Sensory UE, Motor (C, T)	Motor (C, T, LS)	64	25
6	38	Chiari	39	Headaches, sensory loss in right arm and both legs (C)	Progressive muscular atrophy of the hands, sensory loss legs. (C)	48	10
7	32	Chiari	32	Muscular atrophy and weakness both hands, R > L, sensory loss legs. (C, T, LS)	Pain, arms legs, Muscular atrophy of left arm. (C, T, LS)	52	20
8	12	Chiari	32	Sensory, pain (C, LS)	Motor UE, LE (C, LS)	39	20 years