Intravascular papillary endothelial hyperplasia of the periocular region

ABSTRACT

Intravascular papillary endothelial hyperplasia (IPEH) is a benign vascular lesion, typically found in the skin, consisting of a papillary proliferation of endothelial cells intimately related to a thrombus; it appears to be a rare variant of an organizing process. IPEH very rarely develops in the periocular region, with fewer than 20 such cases currently reported in the English language literature. We describe one of the largest ever case series of this uncommon lesion occurring in the periocular region and discuss its clinical features, imaging characteristics, and surgical management.

KEYWORDS:

• Endothelial
• hyperplasia
• mass
• orbit
• papillary

Disclosure statement

The authors report no conflicts of interest. The authors alone are responsible for the content and writing of the article.

Meeting presentations

The data included in this manuscript were presented at the Fall 2017 Meeting of the American Society of Ophthalmic Plastic and Reconstructive Surgery.

Proprietary interest statement

Dr. Rubinstein: none. Dr. Rafailov: none. Dr. Mirani: none. Dr. Lee: None. Dr. Langer: none.