Acquired auditory neuropathy spectrum disorder in a child with a brain tumour

Abstract

We present a case of unilateral acquired auditory neuropathy spectrum disorder (ANSD) due to an underlying cerebellar neoplasm. This is the third case in the literature of juvenile pilocytic astrocytoma presenting with auditory symptoms and mimicking the presentation of ANSD; it highlights the importance of imaging in acquired auditory neuropathy. We were able to make a diagnosis of acquired ANSD in our patient because he had a normal AABR in addition to his OAEs as part of his newborn hearing screen. Detailed neuro-otological assessment and radiological imaging is recommended in all cases of acquired ANSD in order to exclude an acquired compressive pathology.

Key words::

• otoacoustic emissions
• auditory brainstem response
• auditory neuropathy spectrum disorder
• pilocyctic astrocytoma

Declaration of interest: The authors report no conflicts of interest. The authors alone are responsible for the content and writing of the paper.