The audiological journey and early outcomes of twelve infants with auditory neuropathy spectrum disorder from birth to two years of age

References

• Attias J. & Raveh E. 2007. Transient deafness in young candidates for cochlear implants. Audiol Neurotol, 12, 325–333.
   PubMed Web of Science ®Google Scholar
• Berlin C.I. 1999. Auditory neuropathy: Using OAEs and ABRs from screening to management. Seminars in Hearing, 21, 307–315.
   Google Scholar
• Berlin C.I., Hood L.J., Morlet T., Wilensky D., Li L. et al. 2010. Multi-site diagnosis & management of 260 patients with auditory neuropathy/dys-synchrony (auditory neuropathy spectrum disorder). Int J Audiol, 49, 30–43.
   PubMed Web of Science ®Google Scholar
• Berlin C.I., Morlet T. & Hood L.J. 2003. Auditory neuropathy/dyssynchrony: Its diagnosis and management. Pediatr Clin North Am, 50, 331–340.
   PubMed Web of Science ®Google Scholar
• Berlin C.I., Morlet T. & Hood L.J. 2008. Management of individuals with auditory neuropathy spectrum disorder. In: J. Northern (ed.) Guidelines for Identification and Management of Infants and Young Children with Auditory Neuropathy Spectrum Disorder. Colorado, USA: Bill Daniels Center for Children’s Hearing, pp. 35–40.
   Google Scholar
• Byrne D., Dillon H., Tran K., Arlinger S., Wilbraham K. et al. 1994. An international comparison of long-term average speech spectra. J Acoust Soc Am, 96, 2108–2120.
   Web of Science ®Google Scholar
• Byrne D., Parkinson A. & Newall P. 1991. Hearing aid gain and frequency response requirements for the severely/profoundly hearing impaired. In: J. Bernthall, J. Hall & J. Tomblin (eds.) Yearbook of Speech, Language and Hearing. St. Louis: Mosby Year Book, pp. 287–288.
   Google Scholar
• Carter L., Golding M., Dillon H. & Seymour J. 2010. The detection of infant cortical auditory-evoked potentials (CAEPs) using statistical and visual detection techniques. J Am Acad Audiol, 21, 347–356.
   PubMed Web of Science ®Google Scholar
• Chang H., Dillon H., Carter L., Van Dun B. & Young S. 2012. The relationship between cortical auditory-evoked potential (CAEP) detection and estimated audibility in infants with sensorineural hearing loss. Int J Audiol, 51, 663–670.
   PubMed Web of Science ®Google Scholar
• Cone-Wesson B. & Wunderlich J. 2003. Auditory evoked potentials from the cortex: Audiology applications. Curr Opin Otolaryngol Head Neck Surg, 11, 372–377.
   PubMedGoogle Scholar
• Cone B. & Whitaker R. 2013. Dynamics of infant cortical auditory-evoked potentials (CAEPs) for tone and speech tokens. Int J Pediatr Otorhinolaryngol.
   PubMed Web of Science ®Google Scholar
• Dillon H. 2005. So, baby, how does it sound? Cortical assessment of infants with hearing aids. The Hearing Journal, 58, 12–17.
   Google Scholar
• Dillon H. 2012. Hearing Aids. New York: Thieme.
   Google Scholar
• Golding M., Dillon H., Seymour J. & Carter L. 2009. The detection of adult cortical auditory evoked potentials (CAEPs) using an automated statistic and visual detection. Int J Audiol, 48, 833–842.
   PubMed Web of Science ®Google Scholar
• Golding M., Pearce W., Seymour J., Cooper A., Ching T. et al. 2007. The relationship between obligatory cortical auditory-evoked potentials (CAEPs) and functional measures in young infants. J Am Acad Audiol, 18, 117–125.
   PubMed Web of Science ®Google Scholar
• Hayes D. 2008. Auditory neuropathy spectrum disorder. In: D. Hayes (ed.) Newborn Hearing Screening. Como, Italy: Bill Daniels Center for Children’s Hearing, pp. 1–9.
   Google Scholar
• Hayes D. & Sininger Y. 2008. Guidelines: Identification and management of infants and children with auditory neuropathy spectrum disorder Guidelines Development Conference. Lake Como, Italy, pp. 3–8.
   Google Scholar
• Hood L.J. 1998. Auditory neuropathy: What is it and what can we do about it? The Hearing Journal, 51, 10,12–13,16–18.
   Google Scholar
• JCIH 2007. Year 2007 Position statement: Principles and guidelines for early hearing detection and intervention programs. Pediatrics, 120, 898–921.
   PubMed Web of Science ®Google Scholar
• King A.M. 2010. The national protocol for paediatric amplification in Australia. Int J Audiol, 49, S64–S69.
   PubMed Web of Science ®Google Scholar
• Kraus N., Bradlow M.A., Cheatham M.A., Cunningham C.D., King C.D. et al. 2000. Consequences of neural asynchrony: A case of auditory neuropathy. Journal of the Association for Research in Otolaryngology, 1, 33–45.
   PubMed Web of Science ®Google Scholar
• Kumar A.U. & Jayaram M. 2005. Auditory processing in individuals with auditory neuropathy. Behavioral and Brain Functions, 1, 1–8.
   PubMedGoogle Scholar
• Kurtzberg D. 1989. Cortical event-related potential assessment of auditory system function. Seminars in Hearing, 10, 252–262.
   Google Scholar
• Kurtzberg D., Hilpert P.L., Kreuzer J.A. & Vaughan H.G. 1984. Differential maturation of cortical auditory-evoked potentials to speech sounds in normal full-term and very low-birthweight infants. Dev Med Child Neurol, 26, 466–475.
   PubMed Web of Science ®Google Scholar
• Kushnerenko E., Ceponiene R., Balan P., Fellman V., Huotilainen M. et al. 2002. Maturation of the auditory event-related potentials during the first year of life. Neuroreport, 13, 47–51.
   PubMed Web of Science ®Google Scholar
• Madden C., Rutter M., Hilbert L., Greinwald J. & Choo D. 2002. Clinical and audiological features in auditory neuropathy. Arch Otolaryngol Head Neck Surg, 128, 1026–1030.
   PubMed Web of Science ®Google Scholar
• Michalewski H.J., Starr A., Zeng F. & Dimitrijevic A. 2009. N100 cortical potentials accompanying disrupted auditory nerve activity in auditory neuropathy (AN): Effects of signal intensity and continuous noise. Clin Neurophysiol, 120, 1352–1363.
   PubMed Web of Science ®Google Scholar
• Moore J.M.P., Thompson G.P. & Folsom R.C.P. 1992. Auditory responsiveness of premature infants utilizing visual reinforcement audiometry (VRA). Ear Hear, 13, 187–194.
   PubMed Web of Science ®Google Scholar
• Narne V.K. & Vanaja C. 2008. Speech identification and cortical potentials in individuals with auditory neuropathy. Behavioral and Brain Functions, 4, 15.
   PubMed Web of Science ®Google Scholar
• Narne V.K. & Vanaja C.S. 2008. Speech identification and cortical potentials in individuals with auditory neuropathy. Behavioral and Brain Functions, 4.
   PubMed Web of Science ®Google Scholar
• Northern J. & Downs M. 1991. Behavioral hearing testing of children. In: J. Butler (ed.), Hearing in Children. Baltimore: Williams & Wilkins, pp. 139–187.
   Google Scholar
• Pasman J.W., Rotteveel J.J., Maassen B. & Visco Y.M. 1999. The maturation of auditory cortical evoked responses between (preterm) birth and 14 years of age. European Journal of Paediatric Neurology, 3, 79–82.
   PubMedGoogle Scholar
• Pearce W., Golding M. & Dillon H. 2007. Cortical auditory-evoked potentials in the assessment of auditory neuropathy: Two case studies. J Am Acad Audiol, 18, 380–390.
   PubMed Web of Science ®Google Scholar
• Psarommatis I., Riga M., Douros K., Koltsidopoulos P., Douniadakis D. et al. 2006. Transient infantile auditory neuropathy and its clinical implications. Int J Pediatr Otorhinolaryngol, 70, 1629–1637.
   PubMed Web of Science ®Google Scholar
• Purdy S.C., Katsch R. & Dillon H. 2005. Aided cortical auditory-evoked potentials for hearing instrument evaluation in infants. In: R.C. Seewald (ed.) A Sound Foundation Through Early Amplification. Warrenville, USA: Phonak.
   Google Scholar
• Rance G. 2005. Auditory neuropathy/dys-synchrony and its perceptual consequences. Trends in Amplification, 9, 1–43.
   PubMedGoogle Scholar
• Rance G., Cone-Wesson B., Wunderlich J. & Dowell R. 2002. Speech perception and cortical event related potentials in children with auditory neuropathy. Ear Hear, 23, 239–253.
   PubMed Web of Science ®Google Scholar
• Raveh E., Buller N., Badrana O. & Attias J. 2007. Auditory neuropathy: Clinical characteristics and therapeutic approach. Am J Otolaryngol, 28, 302–308.
   PubMed Web of Science ®Google Scholar
• Rose K., Hood L.J. & Berlin C.I. 2002. An overview of the evolution of auditory neuropathy: Its diagnosis & management. Perspectives on Hearing and Hearing Disorders in Childhood, 12, 3–35.
   Google Scholar
• Seewald R.C., Cornelisse L.E., Ramji K.V. et al. 1997.DSL v4.1 for Windows: A software implementation of the desired sensation level (DSL[i/o]) method for fitting linear gain and wide-dynamic-range.
   Google Scholar
• Sharma A., Cardon G., Henion K. & Roland P. 2011. Cortical maturation and behavioral outcomes in children with auditory neuropathy spectrum disorder. Intl J Audiol, 50, 98–106.
   PubMed Web of Science ®Google Scholar
• Sharma A., Dorman M.F. & Kral A. 2005. The influence of a sensitive period on central auditory development in children with unilateral and bilateral cochlear implants. Hear Res, 203, 134–143.
   PubMed Web of Science ®Google Scholar
• Sharma A., Nash A. & Dorman M. 2009. Cortical development, plasticity and re-organization in children with cochlear implants. J Commun Disord, 42, 272–279.
   PubMed Web of Science ®Google Scholar
• Sininger Y. & Oba S. 2001. Patients with auditory neuropathy: Who are they and what can they hear? In: Y. Sininger & A. Starr (eds.), Auditory Neuropathy: A New Perspective on Hearing Disorders. Canada: Singular, pp. 15–35.
   Google Scholar
• Starr A., McPherson D., Patterson J., Don M., Luxford W. et al. 1991. Absence of both auditory-evoked potentials and auditory percepts dependent on timing cues. Brain, 114, 1157.
   PubMed Web of Science ®Google Scholar
• Starr A., Michalewski H.J., Zeng F., Fuijikawa-Brooks S., Linthicum F. et al. 2003. Pathology and physiology of auditory neuropathy with a novel mutation in the MPZ gene (Tyr145→Ser). Brain, 126, 1604–1619.
   PubMed Web of Science ®Google Scholar
• Starr A., Picton T.W., Sininger Y., Hood L.J. & Berlin C.I. 1996. Auditory neuropathy. Brain, 119, 741–753.
   PubMed Web of Science ®Google Scholar
• Steinschneider M., Kurtzberg D. & Vaughan H.G. 1992. Event-related potentials in developmental neuropsychology. In: I. Rapin & S.J. Segalowitz (eds.) Child Neuropsychology. Amsterdam: Elsevier Science Publishers, pp. 239–299.
   Google Scholar
• Van Dun B., Carter L. & Dillon H. 2012. Sensitivity of cortical auditory-evoked potential detection for hearing-impaired infants in response to short speech sounds. Audiology Research, 2.
   PubMedGoogle Scholar
• Widen J. 1993. Adding objectivity to infant behavioral audiometry. Ear Hear, 14, 49–57.
   PubMed Web of Science ®Google Scholar
• Widen J., Folsom R., Cone-Wesson B., Carty L., Dunnell J. et al. 2000. Identification of neonatal hearing impairment: Hearing status at 8 to 12 months. Corrected age using a visual reinforcement audiometry protocol. Ear Hear, 21, 471–487.
   PubMed Web of Science ®Google Scholar
• Wunderlich J.L., Cone-Wesson B.K. & Shepherd R. 2006. Maturation of the cortical auditory evoked potential in infants and young children. Hear Res, 212, 185–202.
   PubMed Web of Science ®Google Scholar