Abstract
Purpose: To describe a rare case of intracranial inflammatory pseudotumor. Case Report: We describe a case of primary intracranial pseudotumor presenting with ophthalmoplegia. Seventeen well-documented cases reported in the literature are summarized. Conclusion: Inflammatory pseudotumor may present to the neuro-ophthalmologist as a visual field defect, monocular visual loss, or diplopia and may be associated with a monoclonal or polyclonal gammopathy.