Primary Malignant Fibrous Histiocytoma of the Spleen-an Extremely Rare Entity

Abstract

Malignant fibrous histiocytoma (MFH) is a frequently occurring soft tissue tumour with aggressive biological behaviour. Primary MFH of the spleen, however, is an exceedingly rare occurrence. Herein, we report a case of such a neoplasm in a 66-year-old female. The tumour was well localised within the spleen and the patient remains alive and well 34 months after splenectomy without any adjuvant therapy. A brief discussion and review of the few cases of primary splenic MFH previously reported in the English language literature is included.

Key Words:

• Spleen
• primary malignant
• histiocytoma.

Additional information

Notes on contributors

D. Mantas

D. Mantas, M.D., Ph.D. 2 Department of Propedeutic Surgery Laiko General Hospital Ag. Thoma 17, 11527 Goudi Athens, Greece Tel.: [phone] Fax: [phone] E-mail: [email protected]