TEVAR for Ruptured type B Aortic Dissection in a Patient with Turner Syndrome

Abstract

TEVAR has replaced open surgical repair as preferred treatment for complicated acute type B aortic dissection. But the literature on thoracic endovascular aortic repair (TEVAR) for ruptured type B dissection is scarce. Patients with Turner syndrome are at risk for aortic dissection and rupture at a young age with an immediate mortality rate of 63%. Only a few cases have been described and the best treatment is not yet established.

We present a case of a 49 year-old woman with Turner syndrome who suffered from a ruptured aortic dissection Stanford type B. A TEVAR procedure was performed, but the life of the patient could not be saved.

In this case report we discuss the lessons we learned as well as some unsolved questions about TEVAR for ruptured type B aortic dissection.

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Notes on contributors

I. Fourneau

Inge Fourneau, M.D., Ph.D., F.E.B.V.S. University Hospitals Leuven Department of Vascular Surgery Herestraat 49 3000 Leuven, Belgium Tel.: [phone] E-mail: [email protected]