OHVIRA syndrome presenting with acute abdomen findings treated with minimally invasive method: three case reports

Abstract

Background

One of the least common forms of Müllerian anomalies is Herlyn–Werner–Wunderlich syndrome (HWWS), characterized by uterus didelphys, obstructed hemi-vagina, and ipsilateral renal agenesis (OHVIRA). HWWS is also known as OHVIRA syndrome. Patients with OHVIRA syndrome generally present with increasing pelvic pain, dysmenorrhoea, and pelvic mass during puberty, shortly after menarche. These patients may be treated successfully with a minimally invasive method.

Case report

We present three previously asymptomatic patients with OHVIRA syndrome who presented with acute abdomen shortly after menarche. These patients were treated with a minimally invasive method.

Conclusion

Patients with OHVIRA syndrome may be treated with minimally invasive method after definitive diagnosis and, laparoscopy and laparotomy should be avoided as much as possible. Minimally invasive treatment modality is not only cost-effective, but also provides symptomatic relief and preserves fertility.

Keywords:

• Herlyn–Werner–Wunderlich syndrome
• OHVIRA
• müllerian anomaly
• acute abdomen
• minimally invasive method

Disclosure statement

The authors report no conflict of interest.