Abstract
Renal tubular diseases may be classified as primary and secondary. Secondary tubular diseases are a heterogenous group of hereditary and acquired disorders in which tubular insufficiency results from a more widespread disease. Primary tubular diseases are hereditary. Clinically, the five most important disorders in this group are renal tubular acidosis, nephrogenic diabetes insipidus, cystinuria, renal glucosuria and phosphoglucoaminoaciduria.