A Rare Ocular Manifestation of Adult Onset Still’s Disease: Purtscher’s-like Retinopathy

ABSTRACT

Adult-onset Still’s disease (AOSD) is a rare multisystemic immune-mediated disease of unknown etiology with quotidian spiking fever, evanescent rash, arthralgia, and multiple organ involvement. The few AOSD cases that have been reported developed Purtscher’s-like retinopathy associated with thrombotic microangiopathy (TMA). Here, we report Purtscher’s-like retinopathy without TMA in a patient with AOSD. A 29-year-old-man who presented for evaluation of blurred vision was diagnosed with AOSD based on Yamaguchi criteria. He had Purtscher’s-like retinopathy in his right eye. Lesions improved after steroid treatment. Although almost all reported AOSD cases with Purtscher’s-like retinopathy are associated with TMA, in this case such a complication was not encountered.

Keywords:

• Adult-onset Still’s disease
• corticosteroids
• microangiopathy
• Purtscher’s-like retinopathy
• Yamaguchi

DECLARATION OF INTEREST

The authors report no conflicts of interest. The authors alone are responsible for the content and writing of the paper.