Abstract
Purpose: To present a boy with unilateral duplication of the eye. Method: The case history is described from the first visit at birth to the age of 14 years. Results: A review of the literature shows that this malformation is compatible with life although malformations of the brain and epilepsy have been reported in all cases where a paediatric exam was described. We show that the malformation can appear as a synophthalmic eye in a single orbit or as two separate unilateral eyes in a separate orbit. Conclusion: We find the denomination, triophthalmia insufficient to differentiate between the two types and suggest a differentiation between unilateral synophthalmia and ipsilateral ocular duplication.