A Case of Rapidly Fatal Systemic Capillary Leak Syndrome in a Kidney Transplant Recipient

Summary

Idiopathic Systemic Capillary Leak Syndrome (SCLS) is a rare entity characterised by idiopathic ‘“creasing of capillary permeability associated with recurrent attacks of hypovolemic shock. We report the case of a 39-year-old man with a SCLS fourteen years after a cadaveric renal transplantation. The clinical evolution was rapidly fatal despite treatment with corticoids, aminophylline and terbutaline which are the most efficient drugs known to prevent attacks.