Abstract
The frequency of primary malignant tumors of the head and neck in childhood in a defined population is given. The need of early diagnosis is stressed. Fine needle aspiration biopsy is a valuable procedure. Extended surgery should, if possible, be carried out without delay and, if needed, be followed by prompt and adequate radiotherapeutic measures. The prognosis does not seem to be so pessimistic as is usually believed. An intense follow-up program and prophylaxis against upper respiratory tract infections for at least five years postoperatively combined with family planning measures are recommended. This policy has apparently up till now saved five of the patients. The most interesting one is a case with an alveolar rhabdomyosarcoma, who seems to be the first reported in literature to live four years after the diagnosis was established.