Ear Malformations in Cleidocranial Dysostosis

Abstract

A case is reported of a 13-year-old girl with familial cleidocranial dys-ostosis, pronounced ear malformations, and a conductive hearing loss. The right auricle was small and deformed and both external ear canals were atretic. Radiograms of the temporal bones showed dense calcification, atretic middle ears, and malformations of the auditory ossicles.