Abstract
Two chondrodystrophic males have developed a non-traumatic cerebrospinal rhinorrhea within their second decade. Hydrocephalus was the cause of cerebrospinal fluid leakage in both cases. To lower the intra-cranial pressure the neurosurgeon performed a ventriculocardiostomy. The fistula was closed by the rhinosurgical extradural route. With respect to the atrophic brain in cases of hydrocephalus, the fronto-nasal approach appeared to be the best and less traumatic way of exposing the frontal base of the skull.