Hereditary Deafness Syndromes with Onset in Adult Life

Abstract

The types of hereditary deafness in man can be separated from each other by the type of hearing loss and its age of onset, by the mode of transmission and by the associated defects caused by the abnormal gene. In this report we reviewed the clinical findings, laboratory findings, etiology, treatment, prognosis, and the diagnostic features of the 12 known types of hereditary deafness which begin in adult life.

Key Words:

• Auditory genetics
• Low-frequency hearing loss
• Otosclerosis
• Acoustic neurinomas
• Neural deafness