Abstract
A material of 165 Norwegian patients with cystic fibrosis (CF) is presented. 149 patients are still alive. The material is based on a central registry for CF with information gathered from yearly distribution of questionnaires. The mean age at diagnosis is high in Norway, even when screened infants are included. A further characteristic of the material is the striking male preponderance in the younger age groups, whereas there is no sex difference in the group of adult CF patients. Very striking is the low incidence and prevalence of chronic respiratory tract infections caused by Pseudomonas aeruginosa; the reason for this is unexplained.
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