Abstract
A 3-month-old baby boy presented with a right-sided abdominal mass that was shown on radiographic and ultrasonographic examination to be cystic and within the kidney. Histological examination of the right nephrectomy specimen showed it to be a congenital cystic mesoblastic nephroma. The patient made an uneventful recovery and there were no signs of recurrence eight years later. Though this tumour is extremely rare it should be considered as a differential diagnosis in infancy as its prognosis and treatment are different from those of other tumours.