Abstract
A 48-year-old man developed bilateral orbital myositis with almost complete loss of vision in both eyes from optic neuropathy. Computerized tomographic scans revealed marked contrast enhancement of extraocular muscles. It is assumed that physical compression due to enlarged extraocular muscles as well as adjacent inflammatory infiltration at the orbital apex caused optic neuropathy. Treatment with 200 mg of prednisolone for 2 days followed by oral taper dramatically improved eye movement restriction and visual disturbance.