Abstract
Craniofacial dysostosis is a progressive disease which is often not obvious in the neonatal period, but progresses rapidly to the familiar appearance in later childhood (Figs. 1,2). Whereas neurosurgeons have long been familiar with progressive cranial asymmetry secondary to premature fusion of calvarial sutures (scaphocephaly and brachycephaly), the pathodynamic basis of these entities was not previously related to the progressive deformity of craniofacial dysostosis.