Maffucci's Syndrome

Abstract

Maffucci's syndrome is a congenital, non-hereditary mesodermal dysplasia manifested as multiple enchondromas (Ollier's disease), skeletal deformities and hemangiomas. One case of this rare disease is reported. The patient, an 11-year-old boy, has generalized, severe skeletal deformities and secondary dwarfism. The vascular component is capillary hemangiomas.