Abstract
An Indian (Asian) patient with compound heterozygosity for Hb Riyadh and β-thalassemia is described. Hb Riyadh forms about 95% of the hemoglobin present. the clinico-pathological picture is identical to that of simple β-thalassemia trait confirming the harmless nature of the substitution β 120 (GH3) Lys↣Asn.