Congenital retinal non-attachment associated with the Dandy-Walker syndrome

Abstract

A male newborn patient is presented who suffered from congenital bilateral blindness because of malformations in the vitreous and retina; the right eye had malformed retina and choroid, and the left eye had a retrolental opacity, which was partially resorbed at the age of one month revealing extensive detachment of the peripheral retina. Neurologic examinations disclosed progressive hydrocephalus due to Dandy-Walker syndrome. Association of congenital retinal non-attachment and Dandy-Walker syndrome may form a separate clinical syndrome.

Key Words:

• Retinal nonattachment
• retrolental opacity
• hydrocephalus
• Dandy-Walker syndrome