Pulmonary AL amyloidosis in a patient with primary Sjögren syndrome

S. BannoSecond Department of Internal Medicine, Medical School, Nagoya City University, Nagoya, JapanCorrespondence[email protected]

Y. MatsumotoSecond Department of Internal Medicine, Medical School, Nagoya City University, Nagoya, Japan

Y. HayamiDepartment of Clinical Laboratory Medicine, Medical School, Nagoya City University, 1 Kawasumi, Mizuho-ku, Nagoya 460-8601, Japan

Y. SugiuraSecond Department of Internal Medicine, Medical School, Nagoya City University, Nagoya, Japan

T. YoshinouchiSecond Department of Internal Medicine, Medical School, Nagoya City University, Nagoya, Japan

R. UedaSecond Department of Internal Medicine, Medical School, Nagoya City University, Nagoya, Japan

Abstract

The condition of a 29-year-old woman with primary Sjögren syndrome (SS) was complicated by amyloid light chains- (AL-) type amyloidosis in the paranasal sinus. She had not complained of respiratory symptoms, but her chest computed tomography (CT) scan revealed bilateral multiple nodular shadows. Lung biopsy specimens using video-associated thoracoscopy showed amyloidoma in a subpleural nodular lesion and amyloid deposits in the interstitial parenchymal walls and pulmonary vessels. Pulmonary AL amyloidosis, presumably related to a chronic inflammatory lymphoproliferative process in SS, has rarely been reported.

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Pulmonary AL amyloidosis in a patient with primary Sjögren syndrome

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Pulmonary AL amyloidosis in a patient with primary Sjögren syndrome

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