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Special Review: IgG4-RD

IgG4-related periaortitis/periarteritis: An under-recognized condition that is potentially life-threatening

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Pages 240-250 | Received 12 Sep 2018, Accepted 02 Nov 2018, Published online: 08 Mar 2019

Keep up to date with the latest research on this topic with citation updates for this article.

Read on this site (3)

Weijia Wang, Xiaojing Kang, Yuan Ding, Lidan Mao, Abudureyimu Dilinuer & Wenzheng Li. (2023) IgG4-Related Disease Manifested as Cutaneous Plasmacytosis: A Case Report. Clinical, Cosmetic and Investigational Dermatology 16, pages 1997-2004.
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Yoshinori Takahashi, Ichiro Mizushima, Masahiro Konishi, Hiroyuki Kawahara, Hajime Sanada, Kazuyuki Suzuki, Akari Takeji, Satoshi Hara, Kiyoaki Ito, Hiroshi Fujii & Mitsuhiro Kawano. (2021) Involvement of two or more sets of lacrimal glands and/or major salivary glands is related to greater systemic disease activity due to multi-organ involvement in IgG4-related dacryoadenitis/sialadenitis. Modern Rheumatology 31:6, pages 1164-1170.
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Tiago Borges & Sérgio Silva. (2020) IgG4-related disease: How to place it in the spectrum of immune-mediated and rheumatologic disorders?. Modern Rheumatology 30:4, pages 609-616.
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Articles from other publishers (25)

Yujiro Kawakami, Yosuke Hirobe & Hiroshi Nakase. (2023) Immunoglobulin G4 ‐related periarteritis successfully diagnosed by endoscopic ultrasonography‐guided fine‐needle biopsy . Digestive Endoscopy 35:5.
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Jun Xu, Brittany Bettendorf, Mario D’Oria & Mel J. Sharafuddin. (2023) Multidisciplinary diagnosis and management of inflammatory aortic aneurysms. Journal of Vascular Surgery 78:1, pages 231-242.e2.
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Fumiaki Nakashima, Tsukasa Watanabe, Yoshiyuki Tomiyoshi, Kazuhisa Ejima, Takateru Ootsuka, Junichi Nojiri, Kazuma Fujimoto & Yoshitaka Hirooka. (2023) Importance of Awareness and Careful Follow-Up of Suspected IgG4-Related Periaortitis. International Heart Journal 64:1, pages 109-113.
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Masahiro Kogami, Yoshiyuki Abe, Taiki Ando, Ayako Makiyama, Ken Yamaji & Naoto Tamura. (2023) Performance of classification and diagnostic criteria for IgG4-related disease and comparison of patients with and without IgG4-related disease. Scientific Reports 13:1.
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Hideki Oka, Shuji Sumitomo, Hayato Shimizu, Maki Kanamori, Daisuke Yamashita, Hiroaki Nishioka & Koichiro Ohmura. (2023) A case of aortoduodenal fistula caused by IgG4-related periaortitis. Modern Rheumatology Case Reports 7:1, pages 188-191.
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Mitsuhiro Kawano, Yoh Zen, Takako Saeki, Lingli Dong, Wen Zhang, Emanuel Della-Torre, Philip A. Hart, Judith A. Ferry & John H. Stone. 2023. A Clinician's Pearls & Myths in Rheumatology. A Clinician's Pearls & Myths in Rheumatology 701 725 .
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Norihiro Ashihara, Masao Ota, Yasunari Fujinaga, Makiko Ozawa, Yasuhiro Kuraishi, Takayuki Watanabe, Hideaki Hamano, Satoru Joshita, Shigeyuki Kawa & Takeji Umemura. (2022) The levels of IL-1β and soluble IL-1 receptors in patients with IgG4-related periaortitis/periarteritis. Advances in Medical Sciences 67:2, pages 257-261.
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Tasuku Hada, Masashi Amano, Yuki Irie, Kenji Moriuchi, Atsushi Okada, Manabu Matsumoto, Hiroyuki Takahama, Makoto Amaki, Hideaki Kanzaki, Yoshihiko Ikeda, Kinta Hatakeyama, Kengo Kusano, Teruo Noguchi & Chisato Izumi. (2022) Left Ventricular Dysfunction Caused by IgG4-related Small Intramural Coronary Periarteritis. Internal Medicine 61:1, pages 59-63.
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Yu Chen, Shaozhe Cai, Lingli Dong & Hisanori Umehara. (2022) Update on classification, diagnosis, and management of immunoglobulin G4-related disease. Chinese Medical Journal 135:4, pages 381-392.
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Takafumi Kawanami, Haruka Kawanami-Iwao, Takanobu Takata, Yasuhito Ishigaki, Naohisa Tomosugi, Tsutomu Takegami, Hiroto Yanagisawa, Shino Fujimoto, Tomoyuki Sakai, Yoshimasa Fujita, Kazunori Yamada, Shuichi Mizuta, Hiroshi Kawabata, Toshihiro Fukushima, Yuko Hirose & Yasufumi Masaki. (2021) Comprehensive analysis of protein-expression changes specific to immunoglobulin G4-related disease. Clinica Chimica Acta 523, pages 45-57.
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Amrita Valluri, Juliana Sitta & Candace M. Howard. (2021) Multifocal IgG4-related aortitis and periaortitis simulating aortic dissection. Radiology Case Reports 16:8, pages 2274-2279.
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Ichiro Mizushima, Takahiro Yamano, Hiroyuki Kawahara, Shinya Hibino, Ryo Nishioka, Takeshi Zoshima, Satoshi Hara, Kiyoaki Ito, Hiroshi Fujii, Hideki Nomura & Mitsuhiro Kawano. (2021) Positive disease-specific autoantibodies have limited clinical significance in diagnosing IgG4-related disease in daily clinical practice. Rheumatology 60:7, pages 3317-3325.
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Hisanori Umehara, Kazuichi Okazaki, Shigeyuki Kawa, Hiroki Takahashi, Hiroshi Goto, Shoko Matsui, Nobukazu Ishizaka, Takashi Akamizu, Yasuharu Sato & Mitsuhiro Kawano. (2021) The 2020 Revised Comprehensive Diagnostic Criteria for IgG4-Related Disease. The Research Program for Intractable Disease by the Ministry of Health, Labour and Welfare (MHLW) Japan2020年 改訂 IgG4関連疾患包括診断基準―The 2020 Revised Comprehensive Diagnostic(RCD)Criteria for IgG4-RD ―厚生労働省難治性疾患等政策研究事業 IgG4関連疾患の診断基準並びに診療指針の確立を目指す研究班. Nihon Naika Gakkai Zasshi 110:5, pages 962-969.
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Aamina Shakir, Yurong Wheeler & Guha Krishnaswamy. (2021) The enigmatic immunoglobulin G4-related disease and its varied cardiovascular manifestations. Heart 107:10, pages 790-798.
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G. Saitakis & B.K. Chwalisz. (2021) The neurology of IGG4-related disease. Journal of the Neurological Sciences 424, pages 117420.
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George E. Fragoulis, Gerasimos Evangelatos & Maria G. Tektonidou. (2020) Vasculitis beyond aortitis in IgG4-related disease (IgG4-RD): case report and review of the literature. Clinical Rheumatology 40:3, pages 1167-1173.
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Annarosa Floreani, Kazuichi Okazaki, Kazushige Uchida & M. Eric Gershwin. (2021) IgG4-related disease: Changing epidemiology and new thoughts on a multisystem disease. Journal of Translational Autoimmunity 4, pages 100074.
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Linyi Peng, Panpan Zhang, Jieqiong Li, Zheng Liu, Hui Lu, Liang Zhu, Xiaorong Wang, Fei Teng, Xuemei Li, Huifang Guo, Yunyun Fei, Wen Zhang, Yan Zhao, Xiaofeng Zeng & Fengchun Zhang. (2020) IgG4-related aortitis/periaortitis and periarteritis: a distinct spectrum of IgG4-related disease. Arthritis Research & Therapy 22:1.
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Sanjiv Sharma, Niraj Nirmal Pandey, Mumun Sinha & S. H. Chandrashekhara. (2020) Etiology, Diagnosis and Management of Aortitis. CardioVascular and Interventional Radiology 43:12, pages 1821-1836.
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Noriko Oyama-Manabe, Osamu ManabeSatonori Tsuneta & Nobukazu Ishizaka. (2020) RadioGraphics Update: IgG4-related Cardiovascular Disease from the Aorta to the Coronary Arteries . RadioGraphics 40:7, pages E29-E32.
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T. Lenfant, J. Moroch, T. de Risi-Pugliese, J-B. Monfort, M. Benjoar, A. Barbaud & P. Senet. (2020) Phénomène de Raynaud avec thromboses artérielles au cours d'une maladie associée aux IgG4. La Revue de Médecine Interne 41:10, pages 708-713.
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Shokoufeh Hajsadeghi, Marziyeh Pakbaz, Morteza Hassanzadeh & Alireza Sadeghipour. (2020) A challenging case report of IgG4‐related systemic disease involving the heart and retroperitoneum with a literature review of similar heart lesions. Echocardiography 37:9, pages 1478-1484.
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Masahiko Hasegawa, Yuusuke Sakurai, Shunsuke Nakata, Kazutaka Horiuchi, Satsuki Komoda, Shinnichi Mizutani & Takeshi Yuasa. (2019) A Case of Ruptured Immunoglobulin G4-Related Periaortitis. Annals of Vascular Diseases 12:4, pages 545-547.
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Mitsuhiro Akiyama, Yuko Kaneko & Tsutomu Takeuchi. (2019) Characteristics and prognosis of IgG4-related periaortitis/periarteritis: A systematic literature review. Autoimmunity Reviews 18:9, pages 102354.
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