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Marie Viprey, Frédéric Mougeot, Alexandra Lelia Dima, Julie Haesebaert, Pauline Occelli, Isabelle Durieu, Héloïse Rouzé, Quitterie Reynaud & Sandrine Touzet. (2023) A Participatory Approach Involving Patients with Cystic Fibrosis and Healthcare Professionals for the Co-Design of an Adherence-Enhancing Intervention Toolkit. Patient Preference and Adherence 17, pages 995-1004.
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Kathryn E. Oliver, Marianne S. Carlon, Nicoletta Pedemonte & Miquéias Lopes-Pacheco. (2023) The revolution of personalized pharmacotherapies for cystic fibrosis: what does the future hold?. Expert Opinion on Pharmacotherapy 24:14, pages 1545-1565.
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Zumi Mehta, Khalid M. Kamal, Richard Miller, Jordan R. Covvey & Vincent Giannetti. (2021) Adherence to cystic fibrosis transmembrane conductance regulator (CFTR) modulators: analysis of a national specialty pharmacy database. Journal of Drug Assessment 10:1, pages 62-67.
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Mallory Schneider, Jessica Simpson & Kimberly Zlomke. (2021) A comparison study: caregiver functioning and family resilience among families of children with cystic fibrosis, asthma, and healthy controls. Children's Health Care 50:2, pages 142-158.
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Christina Murphy & Victoria A. Miller. (2020) Concurrent and longitudinal associations among parenting style, responsibility, and adherence in youth with Cystic Fibrosis. Children's Health Care 49:2, pages 153-167.
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Héloïse Rouzé, Marie Viprey, Samuel Allemann, Alexandra L Dima, Pascal Caillet, Angélique Denis, Stéphanie Poupon-Bourdy, Boubou Camara, Catherine Llerena, Philippe Reix, Isabelle Durieu, Quitterie Reynaud & Sandrine Touzet. (2019) Adherence to long-term therapies in cystic fibrosis: a French cross-sectional study linking prescribing, dispensing, and hospitalization data. Patient Preference and Adherence 13, pages 1497-1510.
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Carla Colombo, Paola Catastini, Anna Brivio, Benedetto Acone, Patricia Dang & Serena Quattrucci. (2018) Delphi poll to assess consensus on issues influencing long-term adherence to treatments in cystic fibrosis among Italian health care professionals. Patient Preference and Adherence 12, pages 2233-2241.
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Articles from other publishers (57)
Md Meraj Anjum, Krishna Kumar Patel, Sankha Bhattacharya, Dilip Kumar Arya, Prashant Pandey, Vijayakumar MR, Sanjay Singh & Paruvathanahalli Siddalingam Rajinikanth. (2023) Overcoming barriers in cystic fibrosis therapy through inhalational lipid nanoparticles: Challenges and advances. Journal of Drug Delivery Science and Technology 89, pages 105068.
Crossref
Crossref
Katherine B Hisert, Susan E Birket, John Paul Clancy, Damian G Downey, John F Engelhardt, Isabelle Fajac, Robert D Gray, Marrah E Lachowicz-Scroggins, Nicole Mayer-Hamblett, Patrick Thibodeau, Katherine L Tuggle, Claire E Wainwright & Kris De Boeck. (2023) Understanding and addressing the needs of people with cystic fibrosis in the era of CFTR modulator therapy. The Lancet Respiratory Medicine.
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Crossref
Francis J. Gilchrist, Stephanie Bui, Silvia Gartner, Susanna A. McColley, Harm Tiddens, Gary Ruiz, Florian Stehling, Muhsen Alani, Oksana Gurtovaya, Mark Bresnik, Timothy R. Watkins, Biliana Frankovic & Marianne Skov. (2023) ALPINE2: Efficacy and safety of 14-day vs 28-day inhaled aztreonam for Pa eradication in children with cystic fibrosis. Journal of Cystic Fibrosis.
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Crossref
Vanessa Fein, Christoph Maier, Anne Schlegtendal, Robin Denz, Cordula Koerner‐Rettberg & Folke Brinkmann. (2023) Risk factors for the deterioration of pulmonary function in primary ciliary dyskinesia. Pediatric Pulmonology 58:7, pages 1950-1958.
Crossref
Crossref
Ty Moore, Danya Nees, Brooke Hightower, Lydia Brock, Micah Kee, Audrey Wise, Benjamin Heigle, Ryan Ottwell, Micah Hartwell & Matt Vassar. (2023) Underreporting of patient-reported outcomes in cystic fibrosis randomized controlled trials using CONSORT-PRO and RoB 2.0. Respiratory Medicine and Research 83, pages 100962.
Crossref
Crossref
Lucy Perrem & Felix Ratjen. (2023) A new triple combination cystic fibrosis transmembrane regulator modulator. The Lancet Respiratory Medicine 11:6, pages 499-500.
Crossref
Crossref
Nathan Ward, Kathy Stiller & Anne E. Holland. (2022) Exercise and Airway Clearance Techniques in Cystic Fibrosis. Seminars in Respiratory and Critical Care Medicine 44:02, pages 209-216.
Crossref
Crossref
Emma Raywood, Harriet Shannon, Nicole Filipow, Gizem Tanriver, Sanja Stanojevic, Kunal Kapoor, Helen Douglas, Rachel O'Connor, Nicky Murray, Bridget Black & Eleanor Main. (2023) Quantity and quality of airway clearance in children and young people with cystic fibrosis. Journal of Cystic Fibrosis 22:2, pages 344-351.
Crossref
Crossref
Michael A. Rapoff, Christina Duncan & Cynthia KarlsonMichael A. Rapoff, Christina Duncan & Cynthia Karlson. 2023. Adherence to Pediatric Medical Regimens. Adherence to Pediatric Medical Regimens
1
23
.
Jessica Conti, Claudio Sorio & Paola Melotti. (2022) Organoid Technology and Its Role for Theratyping Applications in Cystic Fibrosis. Children 10:1, pages 4.
Crossref
Crossref
Rory A. Cameron, Daniel Office, Jessie Matthews, Mark Rowley, Janice Abbott, Nicholas J. Simmonds, Jennifer A. Whitty & Siobhán B. Carr. (2022) Treatment Preference Among People With Cystic Fibrosis. Chest 162:6, pages 1241-1254.
Crossref
Crossref
Clemente J. Britto, Felix Ratjen & John P. Clancy. (2022) Emerging Approaches to Monitor and Modify Care in the era of CFTR Modulators. Clinics in Chest Medicine 43:4, pages 631-646.
Crossref
Crossref
Elpis Hatziagorou, Katerina Manika, Syrmo Styliani Kyrvasili, Serafeim Chrysovalantis Kotoulas, Elisavet Anna Chrysochoou, Eleana Kouroukli, Maria Sionidou & John Tsanakas. (2022) Pulmonary medication adherence among children and adults with cystic fibrosis: Is there an association with disease severity?. Pediatric Pulmonology 57:12, pages 3017-3026.
Crossref
Crossref
Edwina C. Landau, Marieke Verkleij, Sonia Graziano, Alexandra L. Quittner, Anna M. Georgiopoulos, Beth A. Smith, Michael S. Schechter & Janice Abbott. (2022) Mental health screening in Cystic Fibrosis as an intervention: Patient and caregiver feedback on improving these processes. Respiratory Medicine 202, pages 106955.
Crossref
Crossref
Iris A. L. Silva, Onofrio Laselva & Miquéias Lopes-Pacheco. (2022) Advances in Preclinical In Vitro Models for the Translation of Precision Medicine for Cystic Fibrosis. Journal of Personalized Medicine 12:8, pages 1321.
Crossref
Crossref
Marlene Hutchings, Susan Kirkpatrick, Madelynne A Arden, Sarah J Drabble, Chin Maguire, Hannah Cantrill, Pauline Whelan, Zhe H Hoo & Martin J Wildman. (2022) Modelling Successful Self-Management in Adults With Cystic Fibrosis: Vicarious Self-Efficacy From Videos of ‘People Like Me’. Cureus.
Crossref
Crossref
Traci M. Kazmerski, Raksha Jain, MinJae Lee & Jennifer L. Taylor-Cousar. (2022) Parenthood impacts short-term health outcomes in people with cystic fibrosis. Journal of Cystic Fibrosis 21:4, pages 662-668.
Crossref
Crossref
André Schultz. (2022) Adherence to CF treatment can be improved with the right approach!. Thorax 77:5, pages 428-428.
Crossref
Crossref
Leila Taheri, Jila Mirlashari, Mohammadreza Modaresi & Ann Pederson. (2022) Cough in adolescent with cystic fibrosis, from nightmare to COVID-19 stigma: A qualitative thematic analysis. Journal of Pediatric Nursing 64, pages 119-125.
Crossref
Crossref
Özge Kenis‐Coskun, Ahsen N. Aksoy, Eda N. Kumaş, Aybike Yılmaz, Elifnur Güven, Hatice H. Ayaz, Tuğçe Sözer, Almala P. Ergenekon & Evrim Karadağ‐Saygı. (2022) The effect of telerehabilitation on quality of life, anxiety, and depression in children with cystic fibrosis and caregivers: A single‐blind randomized trial. Pediatric Pulmonology 57:5, pages 1262-1271.
Crossref
Crossref
Elvira Sondo, Federico Cresta, Cristina Pastorino, Valeria Tomati, Valeria Capurro, Emanuela Pesce, Mariateresa Lena, Michele Iacomino, Ave Maria Baffico, Domenico Coviello, Tiziano Bandiera, Federico Zara, Luis J. V. Galietta, Renata Bocciardi, Carlo Castellani & Nicoletta Pedemonte. (2022) The L467F-F508del Complex Allele Hampers Pharmacological Rescue of Mutant CFTR by Elexacaftor/Tezacaftor/Ivacaftor in Cystic Fibrosis Patients: The Value of the Ex Vivo Nasal Epithelial Model to Address Non-Responders to CFTR-Modulating Drugs. International Journal of Molecular Sciences 23:6, pages 3175.
Crossref
Crossref
Traci M. Kazmerski, Natalie E. West, Raksha Jain, Ahmet Uluer, Anna M. Georgiopoulos, Moira L. Aitken & Jennifer L. Taylor‐Cousar. (2021) Family‐building and parenting considerations for people with cystic fibrosis. Pediatric Pulmonology 57:S1.
Crossref
Crossref
Maria G. Grammatikopoulou, Tonia Vassilakou, Dimitrios G. Goulis, Xenophon Theodoridis, Meletios P. Nigdelis, Arianna Petalidou, Konstantinos Gkiouras, Dimitrios Poulimeneas, Olga Alexatou, Kyriaki Tsiroukidou, Georgios Marakis, Zoe Daniil & Dimitrios P. Bogdanos. (2021) Standards of Nutritional Care for Patients with Cystic Fibrosis: A Methodological Primer and AGREE II Analysis of Guidelines. Children 8:12, pages 1180.
Crossref
Crossref
Marjolaine Gauthier-Loiselle, Martin Cloutier, Walter Toro, Anish Patel, Sherry Shi, Mikhail Davidson, Matthias Bischof, Nicole LaMarca & Omar Dabbous. (2021) Nusinersen for Spinal Muscular Atrophy in the United States: Findings From a Retrospective Claims Database Analysis. Advances in Therapy 38:12, pages 5809-5828.
Crossref
Crossref
Karolinne Souza Monteiro, Thayla Amorim Santino, Smita Pakhale, Louise Balfour & Karla Morganna Pereira Pinto de Mendonça. (2021) Translation, cross-cultural adaptation and psychometric evaluation of the Brazilian version of the Cystic Fibrosis Knowledge Scale (CFKS). PLOS ONE 16:11, pages e0259232.
Crossref
Crossref
Taylor Baumann, Shailendra Das, Jill Ann Jarrell, Yuriko Nakashima-Paniagua, Edith Adriana Benitez, Maria Carolina Gazzaneo & Natalie Villafranco. (2021) Palliative Care in Pediatric Pulmonology. Children 8:9, pages 802.
Crossref
Crossref
Michael Pallin, Shanal Kumar, Chris Daley, Shrinkhala Dawadi, Paul Leong, Erin Carr & Georgia Soldatos. (2021) Continuous glucose monitoring indices predict poor FEV1 recovery following cystic fibrosis pulmonary exacerbations. Journal of Cystic Fibrosis 20:5, pages 785-791.
Crossref
Crossref
Olufunmilola Abraham, Sarah LeMay, Grace Nixon, Andrew Braun, Catherine Decker & Lisa Szela. (2021) Characterizing medication management and the role of pharmacists in caring for people living with cystic fibrosis: A work system approach. Journal of the American Pharmacists Association 61:5, pages 547-554.e2.
Crossref
Crossref
Massimo Maschio & Mirco Ros. (2021) Fibrosi cistica. Medico e Bambino 40:7, pages 1-6.
Crossref
Crossref
Susannah J. King, Audrey C. Tierney, Deirdre Edgeworth, Dominic Keating, Elyssa Williams, Tom Kotsimbos, Brenda M. Button & John W. Wilson. (2021) Body composition and weight changes after ivacaftor treatment in adults with cystic fibrosis carrying the G551 D cystic fibrosis transmembrane conductance regulator mutation: A double-blind, placebo-controlled, randomized, crossover study with open-label extension. Nutrition 85, pages 111124.
Crossref
Crossref
Afsoon Sepahzad, Deborah J. Morris-Rosendahl & Jane C. Davies. (2021) Cystic Fibrosis Lung Disease Modifiers and Their Relevance in the New Era of Precision Medicine. Genes 12:4, pages 562.
Crossref
Crossref
Jordan T. Banks, Margaret Rosenfeld, Lloyd Mancl & Donald L. Chi. (2020) Survey and electronic health record‐based medication use agreement in children with cystic fibrosis: A retrospective cross‐sectional study. International Journal of Paediatric Dentistry 31:2, pages 247-253.
Crossref
Crossref
M Di Paolo, L Hewitt, E Nwankwo, M Ni, A Vidal-Diaz, M C Fisher, D Armstrong-James & A Shah. (2021) A retrospective ‘real-world’ cohort study of azole therapeutic drug monitoring and evolution of antifungal resistance in cystic fibrosis. JAC-Antimicrobial Resistance 3:1.
Crossref
Crossref
. 2021. ERS Handbook of Paediatric Respiratory Medicine. ERS Handbook of Paediatric Respiratory Medicine
739
770
.
Marlies Wagner. 2021. ERS Handbook of Paediatric Respiratory Medicine. ERS Handbook of Paediatric Respiratory Medicine
747
752
.
Tamara del Corral, Roy La Touche, Maria Àngels Cebrià i Iranzo, Ricardo Olmos, Fernando Blanco-Royano & Ibai López-de-Uralde-Villanueva. (2020) Development and Validation of the AdT-Physio Scale: A Tool to Assess Adherence and Perception of Physical Therapist Intervention in Patients With Cystic Fibrosis. Physical Therapy 100:11, pages 2063-2074.
Crossref
Crossref
Daniel Hind, Sarah J Drabble, Madelynne A Arden, Laura Mandefield, Simon Waterhouse, Chin Maguire, Hannah Cantrill, Louisa Robinson, Daniel Beever, Alex Scott, Sam Keating, Marlene Hutchings, Judy Bradley, Julia Nightingale, Mark I Allenby, Jane Dewar, Pauline Whelan, John Ainsworth, Stephen J Walters, Martin J Wildman & Alicia O'Cathain. (2020) Feasibility study for supporting medication adherence for adults with cystic fibrosis: mixed-methods process evaluation. BMJ Open 10:10, pages e039089.
Crossref
Crossref
Cíntia Helena Santuzzi, Fernanda Mayrink Gonçalves Liberato, Samilly Ariany Corrêa Morau, Néville Ferreira Fachini de Oliveira & Lucas Rodrigues Nascimento. (2020) Adherence and barriers to general and respiratory exercises in cystic fibrosis. Pediatric Pulmonology 55:10, pages 2646-2652.
Crossref
Crossref
Marta San Miguel-Pagola, Gregory Reychler, María A. Cebrià i Iranzo, Marta Gómez-Romero, Fernando Díaz-Gutiérrez & Beatriz Herrero-Cortina. (2020) Impact of hypertonic saline nebulisation combined with oscillatory positive expiratory pressure on sputum expectoration and related symptoms in cystic fibrosis: a randomised crossover trial. Physiotherapy 107, pages 243-251.
Crossref
Crossref
Lucie Olivereau, Viviane Nave, Stephan Garcia, Marie Perceval, Muriel Rabilloud, Isabelle Durieu & Quitterie Reynaud. (2020) Adherence to lumacaftor-ivacaftor therapy in patients with cystic fibrosis in France. Journal of Cystic Fibrosis 19:3, pages 402-406.
Crossref
Crossref
Laura Cooley, Janella Hudson, Eileen Potter, Katherine F. Raymond, Cynthia George & Anna M. Georgiopoulos. (2020) Clinical communication preferences in cystic fibrosis and strategies to optimize care. Pediatric Pulmonology 55:4, pages 948-958.
Crossref
Crossref
Miquéias Lopes-Pacheco. (2020) CFTR Modulators: The Changing Face of Cystic Fibrosis in the Era of Precision Medicine. Frontiers in Pharmacology 10.
Crossref
Crossref
Bianca Sampaio Bonfim, Valmir Machado de Melo Filho, Fernanda Matos Fontenelle & Edna Lúcia Souza. (2020) TREATMENT ADHERENCE AMONG CHILDREN AND ADOLESCENTS IN A CYSTIC FIBROSIS REFERENCE CENTER. Revista Paulista de Pediatria 38.
Crossref
Crossref
Zhe Hui Hoo, Rachael Curley, Stephen J Walters, Michael J Campbell & Martin J Wildman. (2020) Exploring the implications of different approaches to estimate centre-level adherence using objective adherence data in an adult cystic fibrosis centre – a retrospective observational study. Journal of Cystic Fibrosis 19:1, pages 162-167.
Crossref
Crossref
Scott C Bell, Marcus A Mall, Hector Gutierrez, Milan Macek, Susan Madge, Jane C Davies, Pierre-Régis Burgel, Elizabeth Tullis, Claudio Castaños, Carlo Castellani, Catherine A Byrnes, Fiona Cathcart, Sanjay H Chotirmall, Rebecca Cosgriff, Irmgard Eichler, Isabelle Fajac, Christopher H Goss, Pavel Drevinek, Philip M Farrell, Anna M Gravelle, Trudy Havermans, Nicole Mayer-Hamblett, Nataliya Kashirskaya, Eitan Kerem, Joseph L Mathew, Edward F McKone, Lutz Naehrlich, Samya Z Nasr, Gabriela R Oates, Ciaran O'Neill, Ulrike Pypops, Karen S Raraigh, Steven M Rowe, Kevin W Southern, Sheila Sivam, Anne L Stephenson, Marco Zampoli & Felix Ratjen. (2020) The future of cystic fibrosis care: a global perspective. The Lancet Respiratory Medicine 8:1, pages 65-124.
Crossref
Crossref
Daniel Hind, Sarah J. Drabble, Madelynne A. Arden, Laura Mandefield, Simon Waterhouse, Chin Maguire, Hannah Cantrill, Louisa Robinson, Daniel Beever, Alexander J. Scott, Sam Keating, Marlene Hutchings, Judy Bradley, Julia Nightingale, Mark I. Allenby, Jane Dewar, Pauline Whelan, John Ainsworth, Stephen J. Walters, Alicia O’Cathain & Martin J. Wildman. (2019) Supporting medication adherence for adults with cystic fibrosis: a randomised feasibility study. BMC Pulmonary Medicine 19:1.
Crossref
Crossref
Manon F. Pritchard, Juliette L. Oakley, Charles D. Brilliant, Philip D. Rye, Julian Forton, Iolo J.M. Doull, Ian Ketchell, Katja E. Hill, David W. Thomas & Paul D. Lewis. (2019) Mucin structural interactions with an alginate oligomer mucolytic in cystic fibrosis sputum. Vibrational Spectroscopy 103, pages 102932.
Crossref
Crossref
Kevin W. Southern, John P. Clancy & Sarath Ranganathan. (2019) Aerosolized agents for airway clearance in cystic fibrosis. Pediatric Pulmonology 54:6, pages 858-864.
Crossref
Crossref
Daniel P. H. O’Toole, Gary J. Latchford, Alistair J.A. Duff, Rosemary Ball, Pamela McCormack, Paul S. McNamara, Keith G. Brownlee & Kevin W. Southern. (2018) Adherence to Aerosol Therapy in Young People With Cystic Fibrosis: Patient and Parent Perspectives Following Electronic Data Capture. Qualitative Health Research 29:6, pages 846-856.
Crossref
Crossref
Lauri A. LinderYelena P. WuCatherine Fiona MacphersonBrynn FowlerAndrew WilsonYeonjung JoSe-Hee JungBridget ParsonsRebecca Johnson. (2019) Oral Medication Adherence Among Adolescents and Young Adults with Cancer Before and Following Use of a Smartphone-Based Medication Reminder App. Journal of Adolescent and Young Adult Oncology 8:2, pages 122-130.
Crossref
Crossref
Melanie Sue Collins, Matthew O'Brien, Craig M. Schramm & Thomas S. Murray. (2019) Repeated hot water and steam disinfection of Pari LC Plus® nebulizers alter nebulizer output. Journal of Cystic Fibrosis 18:2, pages 233-235.
Crossref
Crossref
Zhe Hui Hoo, Benjamin Gardner, Madelynne A Arden, Simon Waterhouse, Stephen J Walters, Michael J Campbell, Daniel Hind, Chin Maguire, Jane Dewar & Martin J Wildman. (2019) Role of habit in treatment adherence among adults with cystic fibrosis. Thorax 74:2, pages 197-199.
Crossref
Crossref
Fabio Balli. (2018) Developing Digital Games to Address Airway Clearance Therapy in Children With Cystic Fibrosis: Participatory Design Process. JMIR Serious Games 6:4, pages e18.
Crossref
Crossref
Heather S. Kirkham, Francis Staskon, Nishita Hira, Darren McLane, Karl M. Kilgore, Alexis Parente, Seung Kim & Gregory S. Sawicki. (2018) Outcome evaluation of a pharmacy‐based therapy management program for patients with cystic fibrosis. Pediatric Pulmonology 53:6, pages 720-727.
Crossref
Crossref
Pablo S. Saldana, Jamie L. Pomeranz & Mary Ellen Young. (2018) More than a job: Career development of individuals with cystic fibrosis. Work 59:3, pages 425-437.
Crossref
Crossref
Aarti Shakkottai, Niko Kaciroti, Lauren Kasmikha & Samya Z. Nasr. (2018) Impact of home spirometry on medication adherence among adolescents with cystic fibrosis. Pediatric Pulmonology 53:4, pages 431-436.
Crossref
Crossref
J. Stuart Elborn. 2017. Acute Exacerbations of Pulmonary Diseases. Acute Exacerbations of Pulmonary Diseases
167
180
.