590
Views
111
CrossRef citations to date
0
Altmetric
Original Article

High metabolic level in patients with familial amyotrophic lateral sclerosis

, , , &
Pages 113-117 | Received 16 Mar 2008, Published online: 10 Jul 2009

Keep up to date with the latest research on this topic with citation updates for this article.

Read on this site (14)

Beata Chełstowska, Anna Barańczyk-Kuźma & Magdalena Kuźma-Kozakiewicz. (2021) Dyslipidemia in patients with amyotrophic lateral sclerosis – a case control retrospective study. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 22:3-4, pages 195-205.
Read now
Helene Blasco, Debora Lanznaster, Charlotte Veyrat-Durebex, Rudolf Hergesheimer, Patrick Vourch, Francois Maillot, Christian R. Andres, Pierre-François Pradat & Phillipe Corcia. (2020) Understanding and managing metabolic dysfunction in Amyotrophic Lateral Sclerosis. Expert Review of Neurotherapeutics 20:9, pages 907-919.
Read now
Shyuan T. Ngo, Ruben P.A. van Eijk, V. Chachay, Leonard H. van den Berg, Pamela A. McCombe, Robert D. Henderson & Frederik J. Steyn. (2019) Loss of appetite is associated with a loss of weight and fat mass in patients with amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 20:7-8, pages 497-505.
Read now
Pamela A. McCombe, Robert D. Henderson, Aven Lee, John D. Lee, Trent M. Woodruff, Restuadi Restuadi, Allan McRae, Naomi R. Wray, Shyuan Ngo & Frederik J. Steyn. (2019) Gut microbiota in ALS: possible role in pathogenesis?. Expert Review of Neurotherapeutics 19:9, pages 785-805.
Read now
Toshio Shimizu, Kazuko Ishikawa-Takata, Akiko Sakata, Utako Nagaoka, Noriko Ichihara, Chiho Ishida, Yuki Nakayama, Tetsuo Komori & Masatoyo Nishizawa. (2017) The measurement and estimation of total energy expenditure in Japanese patients with ALS: a doubly labelled water method study. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 18:1-2, pages 37-45.
Read now
Z.A. Ioannides, F.J. Steyn, J.D. Mi, R.D. Henderson, P.A. McCombe & S.T. Ngo. (2017) Predictions of resting energy expenditure in amyotrophic lateral sclerosis are greatly impacted by reductions in fat free mass. Cogent Medicine 4:1.
Read now
Elizabeth Gray, James R. Larkin, Tim D. W. Claridge, Kevin Talbot, Nicola R. Sibson & Martin R. Turner. (2015) The longitudinal cerebrospinal fluid metabolomic profile of amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 16:7-8, pages 456-463.
Read now
Kay A. Lawton, Meredith V. Brown, Danny Alexander, Zhen Li, Jacob E. Wulff, Robert Lawson, Matt Jaffa, Mike V. Milburn, John A. Ryals, Robert Bowser, Merit E. Cudkowicz & James D. Berry. (2014) Plasma metabolomic biomarker panel to distinguish patients with amyotrophic lateral sclerosis from disease mimics. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 15:5-6, pages 362-370.
Read now
. (2013) Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 14:sup2, pages 1-63.
Read now
Paul Gordon, Philippe Corcia & Vincent Meininger. (2013) New therapy options for amyotrophic lateral sclerosis. Expert Opinion on Pharmacotherapy 14:14, pages 1907-1917.
Read now
Éilis J. O'Reilly, Hao Wang, Marc G. Weisskopf, Kathryn C. Fitzgerald, Guido Falcone, Marjorie L. McCullough, Michael Thun, Yikyung Park, Laurence N. Kolonel & Alberto Ascherio. (2013) Premorbid body mass index and risk of amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 14:3, pages 205-211.
Read now
Jia Li, Jill M. Paulson, Felix D. Ye, Minhee Sung, Anthony N. Hollenberg & Seward B. Rutkove. (2012) Reducing systemic hypermetabolism by inducing hypothyroidism does not prolong survival in the SOD1-G93A mouse. Amyotrophic Lateral Sclerosis 13:4, pages 372-377.
Read now
Kay A. Lawton, Merit E. Cudkowicz, Meredith V. Brown, Danny Alexander, Rebecca Caffrey, Jacob E. Wulff, Robert Bowser, Robert Lawson, Matt Jaffa, Michael V. Milburn, John A. Ryals & James D. Berry. (2012) Biochemical alterations associated with ALS. Amyotrophic Lateral Sclerosis 13:1, pages 110-118.
Read now
. (2011) THEME 7 IN VIVO EXPERIMENTAL MODELS. Amyotrophic Lateral Sclerosis 12:sup1, pages 113-124.
Read now

Articles from other publishers (97)

Ikjae Lee, Hiroshi Mitsumoto, Seonjoo Lee, Edward Kasarskis, Michael Rosenbaum, Pam Factor‐Litvak & Jeri W. Nieves. (2023) Higher Glycemic Index and Glycemic Load Diet Is Associated with Slower Disease Progression in Amyotrophic Lateral Sclerosis. Annals of Neurology.
Crossref
Sarah Roscoe, Ellie Skinner, Elaine Kabucho Kibirige, Charmaine Childs, C. Elizabeth Weekes, Stephen Wootton, Scott Allen, Christopher McDermott & Theocharis Stavroulakis. (2023) A critical view of the use of predictive energy equations for the identification of hypermetabolism in motor neuron disease: A pilot study. Clinical Nutrition ESPEN 57, pages 739-748.
Crossref
Albert Ludolph, Luc Dupuis, Edward Kasarskis, Frederik Steyn, Shyuan Ngo & Christopher McDermott. (2023) Nutritional and metabolic factors in amyotrophic lateral sclerosis. Nature Reviews Neurology 19:9, pages 511-524.
Crossref
Cassandra Barone & Xin Qi. (2023) Altered Metabolism in Motor Neuron Diseases: Mechanism and Potential Therapeutic Target. Cells 12:11, pages 1536.
Crossref
Sebastian Michels, Deborah Kurz, Angela Rosenbohm, Raphael S. Peter, Steffen Just, Hansjörg Bäzner, Axel Börtlein, Christian Dettmers, Hans-Jürgen Gold, Andreas Kohler, Markus Naumann, Peter Ratzka, Albert C. Ludolph, Dietrich Rothenbacher, Gabriele Nagel & Johannes Dorst. (2023) Association of blood lipids with onset and prognosis of amyotrophic lateral sclerosis: results from the ALS Swabia registry. Journal of Neurology 270:6, pages 3082-3090.
Crossref
Matei Bolborea, Pauline Vercruysse, Tselmen Daria, Johanna C. Reiners, Najwa Ouali Alami, Simon J. Guillot, Stéphane Dieterlé, Jérôme Sinniger, Jelena Scekic-Zahirovic, Amela Londo, Hippolyte Arcay, Marc-Antoine Goy, Claudia Nelson de Tapia, Dietmar R. Thal, Kazumoto Shibuya, Ryo Otani, Kimihito Arai, Satoshi Kuwabara, Albert C. Ludolph, Francesco Roselli, Deniz Yilmazer-Hanke & Luc Dupuis. (2023) Loss of hypothalamic MCH decreases food intake in amyotrophic lateral sclerosis. Acta Neuropathologica 145:6, pages 773-791.
Crossref
Jessica Mandrioli, Elisabetta Zucchi, Ilaria Martinelli, Laura Van der Most, Giulia Gianferrari, Cristina Moglia, Umberto Manera, Luca Solero, Rosario Vasta, Antonio Canosa, Maurizio Grassano, Maura Brunetti, Letizia Mazzini, Fabiola De Marchi, Cecilia Simonini, Nicola Fini, Rossella Tupler, Marco Vinceti, Adriano Chiò & Andrea Calvo. (2022) Factors predicting disease progression in C9ORF72 ALS patients. Journal of Neurology 270:2, pages 877-890.
Crossref
Priyanka Sarkar, Ashish Kumar, Partha Sarathi Behera & Kavitha Thirumurugan. 2023. 415 455 .
Destiny Ogbu, Yongguo Zhang, Katerina Claud, Yinglin Xia & Jun Sun. (2022) Target Metabolites to Slow Down Progression of Amyotrophic Lateral Sclerosis in Mice. Metabolites 12:12, pages 1253.
Crossref
Pei He, Binjun He, Shu Li, Wen Chai, Wei Rao, Yu Zhu, Wenzhi Chen, Ping Zhang, Xiong Zhang, Haili Pan & Renshi Xu. (2022) Distribution Features and Potential Effects of Serotonin in the Cerebrum of SOD1 G93A Transgenic Mice. eneuro 9:6, pages ENEURO.0001-22.2022.
Crossref
Leanne Jiang & Shyuan T. Ngo. (2022) Altered TDP-43 Structure and Function: Key Insights into Aberrant RNA, Mitochondrial, and Cellular and Systemic Metabolism in Amyotrophic Lateral Sclerosis. Metabolites 12:8, pages 709.
Crossref
Sagar Verma, Shiffali Khurana, Abhishek Vats, Bandana Sahu, Nirmal Kumar Ganguly, Pradip Chakraborti, Mandaville Gourie-Devi & Vibha Taneja. (2022) Neuromuscular Junction Dysfunction in Amyotrophic Lateral Sclerosis. Molecular Neurobiology 59:3, pages 1502-1527.
Crossref
Ji He, Jiayu Fu, Wei Zhao, Chuan Ren, Ping Liu, Lu Chen, Dan Li, Lu Tang, Lequn Zhou, Yixuan Zhang, Xinran Ma, Gaoqi Zhang, Nan Li & Dongsheng Fan. (2021) Hypermetabolism associated with worse prognosis of amyotrophic lateral sclerosis. Journal of Neurology 269:3, pages 1447-1455.
Crossref
Daniela Calvetti & Erkki Somersalo. 2022. Encyclopedia of Computational Neuroscience. Encyclopedia of Computational Neuroscience 540 558 .
Tesfaye Wolde Tefera, Frederik J. Steyn, Shyuan T. Ngo & Karin Borges. (2021) CNS glucose metabolism in Amyotrophic Lateral Sclerosis: a therapeutic target?. Cell & Bioscience 11:1.
Crossref
Katarzyna Patrycja Dzik, Damian Józef Flis, Zofia Kinga Bytowska, Mateusz Jakub Karnia, Wieslaw Ziolkowski & Jan Jacek Kaczor. (2021) Swim Training Ameliorates Hyperlocomotion of ALS Mice and Increases Glutathione Peroxidase Activity in the Spinal Cord. International Journal of Molecular Sciences 22:21, pages 11614.
Crossref
Yuval Nash & Michal Sitty. (2021) Non-Motor Symptoms of Amyotrophic Lateral Sclerosis: A Multi-Faceted Disorder. Journal of Neuromuscular Diseases 8:4, pages 699-713.
Crossref
Letizia Mazzini, Fabiola De Marchi, Elena Niccolai, Jessica Mandrioli & Amedeo Amedei. 2021. Amyotrophic Lateral Sclerosis. Amyotrophic Lateral Sclerosis 141 158 .
Shyuan T. Ngo, Hao Wang, Robert D. Henderson, Cyril Bowers & Frederik J. Steyn. (2021) Ghrelin as a treatment for amyotrophic lateral sclerosis. Journal of Neuroendocrinology 33:7.
Crossref
Emanuele D’Amico, Giuseppe Grosso, Jeri W. Nieves, Aurora Zanghì, Pam Factor-Litvak & Hiroshi Mitsumoto. (2021) Metabolic Abnormalities, Dietary Risk Factors and Nutritional Management in Amyotrophic Lateral Sclerosis. Nutrients 13:7, pages 2273.
Crossref
Laura Ferri, Paola Ajdinaj, Marianna Gabriella Rispoli, Claudia Carrarini, Filomena Barbone, Damiano D’Ardes, Margherita Capasso, Antonio Di Muzio, Francesco Cipollone, Marco Onofrj & Laura Bonanni. (2021) Diabetes Mellitus and Amyotrophic Lateral Sclerosis: A Systematic Review. Biomolecules 11:6, pages 867.
Crossref
Cyril Quessada, Alexandra Bouscary, Frédérique René, Cristiana Valle, Alberto Ferri, Shyuan T. Ngo & Jean-Philippe Loeffler. (2021) Skeletal Muscle Metabolism: Origin or Prognostic Factor for Amyotrophic Lateral Sclerosis (ALS) Development?. Cells 10:6, pages 1449.
Crossref
Rongrong Han, Jing Liang & Bing Zhou. (2021) Glucose Metabolic Dysfunction in Neurodegenerative Diseases—New Mechanistic Insights and the Potential of Hypoxia as a Prospective Therapy Targeting Metabolic Reprogramming. International Journal of Molecular Sciences 22:11, pages 5887.
Crossref
Aksu Gunay, Heather H. Shin, Oge Gozutok, Mukesh Gautam & P. Hande Ozdinler. (2021) Importance of lipids for upper motor neuron health and disease. Seminars in Cell & Developmental Biology 112, pages 92-104.
Crossref
Alexandra Bouscary, Cyril Quessada, Frédérique René, Michael Spedding, Bradley J. Turner, Alexandre Henriques, Shyuan T. Ngo & Jean-Philippe Loeffler. (2021) Sphingolipids metabolism alteration in the central nervous system: Amyotrophic lateral sclerosis (ALS) and other neurodegenerative diseases. Seminars in Cell & Developmental Biology 112, pages 82-91.
Crossref
T.J. Tracey, S.E. Kirk, F.J. Steyn & S.T. Ngo. (2021) The role of lipids in the central nervous system and their pathological implications in amyotrophic lateral sclerosis. Seminars in Cell & Developmental Biology 112, pages 69-81.
Crossref
Kelby M. Killoy, Mariana Pehar, Benjamin A. Harlan & Marcelo R. Vargas. (2021) Altered expression of clock and clock‐controlled genes in a hSOD1‐linked amyotrophic lateral sclerosis mouse model. The FASEB Journal 35:2.
Crossref
Yangfan Cheng, Yongping Chen & Huifang Shang. (2021) Aberrations of biochemical indicators in amyotrophic lateral sclerosis: a systematic review and meta-analysis. Translational Neurodegeneration 10:1.
Crossref
IsaacG Onyango, JamesP Bennett & GorazdB Stokin. (2021) Regulation of neuronal bioenergetics as a therapeutic strategy in neurodegenerative diseases. Neural Regeneration Research 16:8, pages 1467.
Crossref
Koy Chong Ng Kee Kwong, Arpan R. Mehta, Maiken Nedergaard & Siddharthan Chandran. (2020) Defining novel functions for cerebrospinal fluid in ALS pathophysiology. Acta Neuropathologica Communications 8:1.
Crossref
Matilde Sassani, James J Alix, Christopher J McDermott, Kathleen Baster, Nigel Hoggard, Jim M Wild, Heather J Mortiboys, Pamela J Shaw, Iain D Wilkinson & Thomas M Jenkins. (2020) Magnetic resonance spectroscopy reveals mitochondrial dysfunction in amyotrophic lateral sclerosis. Brain 143:12, pages 3603-3618.
Crossref
Francesco Gentile, Pietro Emiliano Doneddu, Nilo Riva, Eduardo Nobile-Orazio & Angelo Quattrini. (2020) Diet, Microbiota and Brain Health: Unraveling the Network Intersecting Metabolism and Neurodegeneration. International Journal of Molecular Sciences 21:20, pages 7471.
Crossref
Pierre Jésus, Philippe Fayemendy, Benoit Marin, Marie Nicol, Huguette Sourisseau, Yves Boirie, Stéphane Walrand, Najate Achamrah, Moïse Coëffier, Pierre-Marie Preux, Géraldine Lautrette, Philippe Couratier & Jean-Claude Desport. (2020) Increased resting energy expenditure compared with predictive theoretical equations in amyotrophic lateral sclerosis. Nutrition 77, pages 110805.
Crossref
J. Schumacher, R. S. Peter, G. Nagel, D. Rothenbacher, A. Rosenbohm, A. C. Ludolph & J. Dorst. (2020) Statins, diabetes mellitus and prognosis of amyotrophic lateral sclerosis: data from 501 patients of a population‐based registry in southwest Germany. European Journal of Neurology 27:8, pages 1405-1414.
Crossref
Tiziana Petrozziello, Alexandra N. Mills, Sali M.K. Farhan, Kaly A. Mueller, Eric J. Granucci, Kelly E. Glajch, James Chan, Sheena Chew, James D. Berry & Ghazaleh Sadri‐Vakili. (2020) Lipocalin‐2 is increased in amyotrophic lateral sclerosis. Muscle & Nerve 62:2, pages 272-283.
Crossref
Tanya S. McDonald, Pamela A. McCombe, Trent M. Woodruff & John D. Lee. (2020) The potential interplay between energy metabolism and innate complement activation in amyotrophic lateral sclerosis. The FASEB Journal 34:6, pages 7225-7233.
Crossref
Silvia Scaricamazza, Illari Salvatori, Giacomo Giacovazzo, Jean Philippe Loeffler, Frederique Renè, Marco Rosina, Cyril Quessada, Daisy Proietti, Constantin Heil, Simona Rossi, Stefania Battistini, Fabio Giannini, Nila Volpi, Frederik J. Steyn, Shyuan T. Ngo, Elisabetta Ferraro, Luca Madaro, Roberto Coccurello, Cristiana Valle & Alberto Ferri. (2020) Skeletal-Muscle Metabolic Reprogramming in ALS-SOD1G93A Mice Predates Disease Onset and Is A Promising Therapeutic Target. iScience 23:5, pages 101087.
Crossref
Cristian A. Droppelmann, Danae Campos-Melo, Alexander J. Moszczynski, Hind Amzil & Michael J. Strong. (2019) TDP-43 aggregation inside micronuclei reveals a potential mechanism for protein inclusion formation in ALS. Scientific Reports 9:1.
Crossref
Mariana Dutra Brito, Gustavo Ferro Gomes da Silva, Erick Mutti Tilieri, Beatriz Grisolia Araujo, Michele Longoni Calió & Tatiana Rosado Rosenstock. (2019) Metabolic Alteration and Amyotrophic Lateral Sclerosis Outcome: A Systematic Review. Frontiers in Neurology 10.
Crossref
Elisa Lepore, Irene Casola, Gabriella Dobrowolny & Antonio Musarò. (2019) Neuromuscular Junction as an Entity of Nerve-Muscle Communication. Cells 8:8, pages 906.
Crossref
Alexandra Bouscary, Cyril Quessada, Althéa Mosbach, Noëlle Callizot, Michael Spedding, Jean-Philippe Loeffler & Alexandre Henriques. (2019) Ambroxol Hydrochloride Improves Motor Functions and Extends Survival in a Mouse Model of Familial Amyotrophic Lateral Sclerosis. Frontiers in Pharmacology 10.
Crossref
Pierre Jésus, Benoit Marin, Philippe Fayemendy, Marie Nicol, Géraldine Lautrette, Huguette Sourisseau, Pierre-Marie Preux, Philippe Couratier & Jean-Claude Desport. (2019) Resting energy expenditure equations in amyotrophic lateral sclerosis, creation of an ALS-specific equation. Clinical Nutrition 38:4, pages 1657-1665.
Crossref
Udaya Geetha Vijayakumar, Vanessa Milla, Mei Yu Cynthia Stafford, Anthony J. Bjourson, William Duddy & Stephanie Marie-Rose Duguez. (2019) A Systematic Review of Suggested Molecular Strata, Biomarkers and Their Tissue Sources in ALS. Frontiers in Neurology 10.
Crossref
Blanca I. Aldana. (2019) Microglia-Specific Metabolic Changes in Neurodegeneration. Journal of Molecular Biology 431:9, pages 1830-1842.
Crossref
Ping Zeng & Xiang Zhou. (2019) Causal effects of blood lipids on amyotrophic lateral sclerosis: a Mendelian randomization study. Human Molecular Genetics 28:4, pages 688-697.
Crossref
Rup Tandan, Waqar Waheed & Connor Scagnelli. 2019. Handbook of Famine, Starvation, and Nutrient Deprivation. Handbook of Famine, Starvation, and Nutrient Deprivation 981 1033 .
Rup Tandan, Waqar Waheed & Connor Scagnelli. 2019. Handbook of Famine, Starvation, and Nutrient Deprivation. Handbook of Famine, Starvation, and Nutrient Deprivation 1 53 .
Daniela Calvetti & Erkki Somersalo. 2018. Encyclopedia of Computational Neuroscience. Encyclopedia of Computational Neuroscience 1 19 .
Christian Lunetta, Andrea Lizio, Lucio Tremolizzo, Massimiliano Ruscica, Chiara Macchi, Nilo Riva, Patrick Weydt, Ettore Corradi, Paolo Magni & Valeria Sansone. (2018) Serum irisin is upregulated in patients affected by amyotrophic lateral sclerosis and correlates with functional and metabolic status. Journal of Neurology 265:12, pages 3001-3008.
Crossref
Frederik J Steyn, Zara A Ioannides, Ruben P A van Eijk, Susan Heggie, Kathryn A Thorpe, Amelia Ceslis, Saman Heshmat, Anjali K Henders, Naomi R Wray, Leonard H van den Berg, Robert D Henderson, Pamela A McCombe & Shyuan T Ngo. (2018) Hypermetabolism in ALS is associated with greater functional decline and shorter survival. Journal of Neurology, Neurosurgery & Psychiatry 89:10, pages 1016-1023.
Crossref
Gabriella Dobrowolny, Elisa Lepore, Martina Martini, Laura Barberi, Abigail Nunn, Bianca Maria Scicchitano & Antonio Musarò. (2018) Metabolic Changes Associated With Muscle Expression of SOD1G93A. Frontiers in Physiology 9.
Crossref
Alessia Antonini, Silvia Caioli, Luana Saba, Giulia Vindigni, Silvia Biocca, Nadia Canu & Cristina Zona. (2018) Membrane cholesterol depletion in cortical neurons highlights altered NMDA receptor functionality in a mouse model of amyotrophic lateral sclerosis. Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease 1864:2, pages 509-519.
Crossref
Pauline Vercruysse, Didier Vieau, David Blum, Åsa Petersén & Luc Dupuis. (2018) Hypothalamic Alterations in Neurodegenerative Diseases and Their Relation to Abnormal Energy Metabolism. Frontiers in Molecular Neuroscience 11.
Crossref
Alexandre Henriques, Vincent Croixmarie, Alexandra Bouscary, Althéa Mosbach, Céline Keime, Claire Boursier-Neyret, Bernard Walter, Michael Spedding & Jean-Philippe Loeffler. (2018) Sphingolipid Metabolism Is Dysregulated at Transcriptomic and Metabolic Levels in the Spinal Cord of an Animal Model of Amyotrophic Lateral Sclerosis. Frontiers in Molecular Neuroscience 10.
Crossref
Shachee Doshi, Preetika Gupta & Robert G. Kalb. (2017) Genetic induction of hypometabolism by ablation of MC4R does not suppress ALS-like phenotypes in the G93A mutant SOD1 mouse model. Scientific Reports 7:1.
Crossref
Illari Salvatori, Cristiana Valle, Alberto Ferri & Maria Teresa Carrì. (2017) SIRT3 and mitochondrial metabolism in neurodegenerative diseases. Neurochemistry International 109, pages 184-192.
Crossref
J.B. Delaye, F. Patin, E. Piver, C. Bruno, M. Vasse, P. Vourc'h, C.R. Andres, P. Corcia & H. Blasco. (2017) Low IDL-B and high LDL-1 subfraction levels in serum of ALS patients. Journal of the Neurological Sciences 380, pages 124-127.
Crossref
Alexandre Henriques, Mylene Huebecker, Hélène Blasco, Céline Keime, Christian R. Andres, Philippe Corcia, David A. Priestman, Frances M. Platt, Michael Spedding & Jean-Philippe Loeffler. (2017) Inhibition of β-Glucocerebrosidase Activity Preserves Motor Unit Integrity in a Mouse Model of Amyotrophic Lateral Sclerosis. Scientific Reports 7:1.
Crossref
Anne E Visser, Meinie Seelen, Alexander Hulsbergen, Joris de Graaf, Anneke J van der Kooi, Joost Raaphorst, Jan H Veldink & Leonard H van den Berg. (2017) Exploring the fitness hypothesis in ALS: a population-based case-control study of parental cause of death and lifespan. Journal of Neurology, Neurosurgery & Psychiatry 88:7, pages 550-556.
Crossref
Simonetta Camandola & Mark P Mattson. (2017) Brain metabolism in health, aging, and neurodegeneration. The EMBO Journal 36:11, pages 1474-1492.
Crossref
Daniela Mariosa, Niklas Hammar, Håkan Malmström, Caroline Ingre, Ingmar Jungner, Weimin Ye, Fang Fang & Göran Walldius. (2017) Blood biomarkers of carbohydrate, lipid, and apolipoprotein metabolisms and risk of amyotrophic lateral sclerosis: A more than 20-year follow-up of the Swedish AMORIS cohort. Annals of Neurology 81:5, pages 718-728.
Crossref
Theocharis Stavroulakis & Christopher J. McDermott. 2017. Nutrition in Neurologic Disorders. Nutrition in Neurologic Disorders 91 104 .
Esther V. Hobson & Christopher J. McDermott. (2016) Supportive and symptomatic management of amyotrophic lateral sclerosis. Nature Reviews Neurology 12:9, pages 526-538.
Crossref
Mónica Zufiría, Francisco Javier Gil-Bea, Roberto Fernández-Torrón, Juan José Poza, Jose Luis Muñoz-Blanco, Ricard Rojas-García, Javier Riancho & Adolfo López de Munain. (2016) ALS: A bucket of genes, environment, metabolism and unknown ingredients. Progress in Neurobiology 142, pages 104-129.
Crossref
Sagit Golko-Perez, Silvia Mandel, Tamar Amit, Lana Kupershmidt, Moussa B. H. Youdim & Orly Weinreb. (2015) Additive Neuroprotective Effects of the Multifunctional Iron Chelator M30 with Enriched Diet in a Mouse Model of Amyotrophic Lateral Sclerosis. Neurotoxicity Research 29:2, pages 208-217.
Crossref
Karen S. Coughlan, Luise Halang, Ina Woods & Jochen H. M. Prehn. (2016) A high fat jelly diet restores bioenergetic balance and extends lifespan in the presence of motor dysfunction and lumbar spinal cord motor neuron loss in TDP-43A315T/ C57BL/6J mice. Disease Models & Mechanisms.
Crossref
Zara A. Ioannides, Shyuan T. Ngo, Robert D. Henderson, Pamela A. McCombe & Frederik J. Steyn. (2016) Altered Metabolic Homeostasis in Amyotrophic Lateral Sclerosis: Mechanisms of Energy Imbalance and Contribution to Disease Progression. Neurodegenerative Diseases 16:5-6, pages 382-397.
Crossref
Anna Wuolikainen, Pär Jonsson, Maria Ahnlund, Henrik Antti, Stefan L. Marklund, Thomas Moritz, Lars Forsgren, Peter M. Andersen & Miles Trupp. (2016) Multi-platform mass spectrometry analysis of the CSF and plasma metabolomes of rigorously matched amyotrophic lateral sclerosis, Parkinson's disease and control subjects. Molecular BioSystems 12:4, pages 1287-1298.
Crossref
S.T. Ngo, F.J. Steyn, L. Huang, S. Mantovani, C.M.M. Pfluger, T.M. Woodruff, J.D. O'Sullivan, R.D. Henderson & P.A. McCombe. (2015) Altered expression of metabolic proteins and adipokines in patients with amyotrophic lateral sclerosis. Journal of the Neurological Sciences 357:1-2, pages 22-27.
Crossref
Alexandre Henriques, Hélène Blasco, Marie-Céline Fleury, Philippe Corcia, Andoni Echaniz-Laguna, Laura Robelin, Gabrielle Rudolf, Thiebault Lequeu, Martine Bergaentzle, Christian Gachet, Pierre-François Pradat, Eric Marchioni, Christian R. Andres, Christine Tranchant, Jose-Luis Gonzalez De Aguilar & Jean-Philippe Loeffler. (2015) Blood Cell Palmitoleate-Palmitate Ratio Is an Independent Prognostic Factor for Amyotrophic Lateral Sclerosis. PLOS ONE 10:7, pages e0131512.
Crossref
Giancarlo Logroscino, Rosanna Tortelli, Giovanni Rizzo, Benoît Marin, Pierre Marie Preux & Andrea Malaspina. (2015) Amyotrophic Lateral Sclerosis: An Aging-Related Disease. Current Geriatrics Reports 4:2, pages 142-153.
Crossref
Karen S. Coughlan, Mollie R. Mitchem, Marion C. Hogg & Jochen H.M. Prehn. (2015) “Preconditioning” with latrepirdine, an adenosine 5′-monophosphate-activated protein kinase activator, delays amyotrophic lateral sclerosis progression in SOD1G93A mice. Neurobiology of Aging 36:2, pages 1140-1150.
Crossref
S.T. Ngo & F.J. Steyn. (2015) The interplay between metabolic homeostasis and neurodegeneration: insights into the neurometabolic nature of amyotrophic lateral sclerosis. Cell Regeneration 4:1, pages 4:5.
Crossref
Rebekah M. AhmedMia MacMillanLauren BartleyGlenda M. HallidayMatthew C. KiernanJohn R. HodgesOlivier Piguet. (2014) Systemic metabolism in frontotemporal dementia. Neurology 83:20, pages 1812-1818.
Crossref
Katarzyna Kryściak, paweł Grieb & Jan Celichowski. (2014) Changes in motor unit properties in SOD1 (G93A) rats . Muscle & Nerve 50:4, pages 577-586.
Crossref
Maria A. Lim, Kendra K. Bence, Ishani Sandesara, Pénélope Andreux, Johan Auwerx, Jeff Ishibashi, Patrick Seale & Robert G. Kalb. (2014) Genetically altering organismal metabolism by leptin-deficiency benefits a mouse model of amyotrophic lateral sclerosis. Human Molecular Genetics 23:18, pages 4995-5008.
Crossref
Zhenzhen Zheng, Xiaoyan Guo, Rui Huang, Xueping Chen & Huifang Shang. (2014) An exploratory study of the association between thyroid hormone and survival of amyotrophic lateral sclerosis. Neurological Sciences 35:7, pages 1103-1108.
Crossref
Scott P. Allen, Sandeep Rajan, Lynn Duffy, Heather Mortiboys, Adrian Higginbottom, Andrew J. Grierson & Pamela J. Shaw. (2014) Superoxide dismutase 1 mutation in a cellular model of amyotrophic lateral sclerosis shifts energy generation from oxidative phosphorylation to glycolysis. Neurobiology of Aging 35:6, pages 1499-1509.
Crossref
S.T. Ngo, F.J. Steyn & P.A. McCombe. (2014) Body mass index and dietary intervention: Implications for prognosis of amyotrophic lateral sclerosis. Journal of the Neurological Sciences 340:1-2, pages 5-12.
Crossref
Hélène BlascoLydie Nadal-DesbaratsPierre-François PradatPaul H. GordonCatherine AntarCharlotte Veyrat-DurebexCaroline MoreauDavid DevosSylvie MavelPatrick EmondChristian R. AndresPhilippe Corcia. (2014) Untargeted 1 H-NMR metabolomics in CSF . Neurology 82:13, pages 1167-1174.
Crossref
Nirma D. Perera, Rebecca K. Sheean, John W. Scott, Bruce E. Kemp, Malcolm K. Horne & Bradley J. Turner. (2014) Mutant TDP-43 Deregulates AMPK Activation by PP2A in ALS Models. PLoS ONE 9:3, pages e90449.
Crossref
Yanling Sui, Zichun Zhao, Rong Liu, Bin Cai & Dongsheng Fan. (2014) Adenosine monophosphate-activated protein kinase activation enhances embryonic neural stem cell apoptosis in a mouse model of amyotrophic lateral sclerosis. Neural Regeneration Research 9:19, pages 1770.
Crossref
Alok Kumar, Devlina Ghosh & R. L. Singh. (2013) Amyotrophic Lateral Sclerosis and Metabolomics: Clinical Implication and Therapeutic Approach. Journal of Biomarkers 2013, pages 1-15.
Crossref
Valentina GalloPetra A. WarkMazda JenabNeil PearceCarol BrayneRoel VermeulenPeter M. AndersenGoran HallmansAndreas KyrozisNicola VanacoreMariam VahdaniniaVerena GroteRudolf KaaksAmalia MattielloH. Bas Bueno-de-MesquitaPetra H. PeetersRuth C. TravisJesper PeterssonOskar HanssonLarraitz ArriolaJuan-Manuel Jimenez-MartinAnne TjønnelandJytte HalkjærClaudia AgnoliCarlotta SacerdoteCatalina BonetAntonia TrichopoulouDiana GavrilaKim OvervadElisabete WeiderpassDomenico PalliJ. Ramón QuirósRosario TuminoKay-Tee KhawNicholas WarehamAurelio Barricante-GurreaVeronika FedirkoPietro FerrariFrançoise Clavel-ChapelonMarie-Christine Boutron-RuaultHeiner BoeingMatthaeus ViglLefkos MiddletonElio RiboliPaolo Vineis. (2013) Prediagnostic body fat and risk of death from amyotrophic lateral sclerosis. Neurology 80:9, pages 829-838.
Crossref
Beatrice Nefussy & Vivian E. Drory. 2013. Neurodegenerative Diseases: Integrative PPPM Approach as the Medicine of the Future. Neurodegenerative Diseases: Integrative PPPM Approach as the Medicine of the Future 205 233 .
Marlia M. Braun, Matt Osecheck & Nanette C. Joyce. (2012) Nutrition Assessment and Management in Amyotrophic Lateral Sclerosis. Physical Medicine and Rehabilitation Clinics of North America 23:4, pages 751-771.
Crossref
Guillaume Lehéricey, Nadine Le Forestier, Luc Dupuis, Jésus Gonzalez-Bermejo, Vincent Meininger & Pierre-François Pradat. (2012) Prise en charge nutritionnelle dans la sclérose latérale amyotrophique : un enjeu médical et éthique. La Presse Médicale 41:6, pages 560-574.
Crossref
M. A. Lim, M. A. Selak, Z. Xiang, D. Krainc, R. L. Neve, B. C. Kraemer, J. L. Watts & R. G. Kalb. (2012) Reduced Activity of AMP-Activated Protein Kinase Protects against Genetic Models of Motor Neuron Disease. The Journal of Neuroscience 32:3, pages 1123-1141.
Crossref
Benoît Marin, Pierre Jésus, Pierre-Marie Preux, Philippe Couratier & Jean-Claude Desport. (2011) Troubles nutritionnels lors de la sclérose latérale amyotrophique (SLA). Nutrition Clinique et Métabolisme 25:4, pages 205-216.
Crossref
Peter J.M. Weijs. (2011) Hypermetabolism, Is It Real? The Example of Amyotrophic Lateral Sclerosis. Journal of the American Dietetic Association 111:11, pages 1670-1673.
Crossref
Amy C. Ellis & Jeffrey Rosenfeld. (2011) Which Equation Best Predicts Energy Expenditure in Amyotrophic Lateral Sclerosis?. Journal of the American Dietetic Association 111:11, pages 1680-1687.
Crossref
L. Genton, V. Viatte, J.-P. Janssens, A.-C. Héritier & C. Pichard. (2011) Nutritional state, energy intakes and energy expenditure of amyotrophic lateral sclerosis (ALS) patients. Clinical Nutrition 30:5, pages 553-559.
Crossref
Sung-Min Kim, Heejaung Kim, Jee-Eun Kim, Kyung Seok Park, Jung-Joon Sung, Seung Hyun Kim & Kwang-Woo Lee. (2011) Amyotrophic Lateral Sclerosis Is Associated with Hypolipidemia at the Presymptomatic Stage in Mice. PLoS ONE 6:3, pages e17985.
Crossref
Matthew C Kiernan, Steve Vucic, Benjamin C Cheah, Martin R Turner, Andrew Eisen, Orla Hardiman, James R Burrell & Margaret C Zoing. (2011) Amyotrophic lateral sclerosis. The Lancet 377:9769, pages 942-955.
Crossref
P.-F. Pradat, S. Attarian, J.-P. Camdessanché, L. Carluer, P. Cintas, P. Corcia, A. Echaniz-Laguna, J. Gonzalez-Bermejo, N. Guy, G. Nicolas, T. Perez, M.-H. Soriani, N. Vandenberghe & A. Verschueren. (2010) La recherche sur la SLA en 2009 : compte rendu du groupe bibliographique de la coordination des centres SLA. Revue Neurologique 166:8-9, pages 683-698.
Crossref
Beatrice Nefussy & Vivian E. Drory. (2010) Moving toward a predictive and personalized clinical approach in amyotrophic lateral sclerosis: novel developments and future directions in diagnosis, genetics, pathogenesis and therapies. EPMA Journal 1:2, pages 329-341.
Crossref
Isabel Polanco Allué. (2010) Tratamiento nutricional del niño con trastorno neuromotor. Actividad Dietética 14:2, pages 59-66.
Crossref

Reprints and Corporate Permissions

Please note: Selecting permissions does not provide access to the full text of the article, please see our help page How do I view content?

To request a reprint or corporate permissions for this article, please click on the relevant link below:

Academic Permissions

Please note: Selecting permissions does not provide access to the full text of the article, please see our help page How do I view content?

Obtain permissions instantly via Rightslink by clicking on the button below:

If you are unable to obtain permissions via Rightslink, please complete and submit this Permissions form. For more information, please visit our Permissions help page.