Citations (34)
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Yujiro Maeoka, Ryan J. CorneliusJames A. McCormick. (2023) Cullin 3 and Blood Pressure Regulation: Insights From Familial Hyperkalemic Hypertension. Hypertension 80:5, pages 912-923.
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Ryan J. Cornelius, Yujiro Maeoka & James A. McCormick. (2023) Renal effects of cullin 3 mutations causing familial hyperkalemic hypertension. Current Opinion in Nephrology & Hypertension Publish Ahead of Print.
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Ju-hong Jang, Jeong Woong Lee, Min Ji Cho, Byungtae Hwang, Min-Gi Kwon, Dong-Hwan Kim, Nam-Kyung Lee, Jangwook Lee, Young-Jun Park, Yong Ryoul Yang, Jinchul Kim, Yong-Hoon Kim, Tae Hyeon An, Kyoung-Jin Oh, Kwang-Hee Bae, Jong-Gil Park & Jeong-Ki Min. (2022) KLHL3 deficiency in mice ameliorates obesity, insulin resistance, and nonalcoholic fatty liver disease by regulating energy expenditure. Experimental & Molecular Medicine 54:8, pages 1250-1261.
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Chien‐Ming Lin, Chih‐Chien Sung, Sung‐Sen Yang, Ying‐Chuan Chen, Shih‐Ming Huang & Shih‐Hua Lin. (2022) Generation and analysis of pseudohypoaldosteronism type II knock‐in mice caused by a nonsense KLHL3 mutation in the Kelch domain. The FASEB Journal 36:6.
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Franca Anglani, Leonardo Salviati, Matteo Cassina, Matteo Rigato, Laura Gobbi & Lorenzo A. Calò. (2021) Genotype–phenotype correlation in Gordon’s syndrome: report of two cases carrying novel heterozygous mutations. Journal of Nephrology 35:3, pages 859-862.
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Yujiro Maeoka, Mohammed Z. Ferdaus, Ryan J. Cornelius, Avika Sharma, Xiao-Tong Su, Lauren N. Miller, Joshua A. Robertson, Susan B. Gurley, Chao-Ling Yang, David H. Ellison & James A. McCormick. (2022) Combined Kelch-like 3 and Cullin 3 Degradation is a Central Mechanism in Familial Hyperkalemic Hypertension in Mice. Journal of the American Society of Nephrology 33:3, pages 584-600.
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María Castañeda‐Bueno, David H Ellison & Gerardo Gamba. (2021) Molecular mechanisms for the modulation of blood pressure and potassium homeostasis by the distal convoluted tubule. EMBO Molecular Medicine 14:2.
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Harish E. Chatrathi, Jason C. Collins, Lynne A. Wolfe, Thomas C. Markello, David R. Adams, William A. Gahl, Achim Werner & Prashant Sharma. (2022)
Novel
CUL3
Variant Causing Familial Hyperkalemic Hypertension Impairs Regulation and Function of Ubiquitin Ligase Activity
. Hypertension 79:1, pages 60-75.
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Chloé Rafael & Juliette Hadchouel. 2022. Hydro Saline Metabolism. Hydro Saline Metabolism
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43
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Rui Zhang, Simin Zhang, Yingying Luo, Meng Li, Xin Wen, Xiaoling Cai, Xueyao Han & Linong Ji. (2021) A case report of pseudohypoaldosteronism type II with a homozygous KLHL3 variant accompanied by hyperthyroidism. BMC Endocrine Disorders 21:1.
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Ya Zhang, Qin Guo, Gengru Jiang & Chong Zhang. (2021) Dysfunction of Cullin 3 RING E3 ubiquitin ligase causes vasoconstriction and increased sodium reabsorption in diabetes. Archives of Biochemistry and Biophysics 710, pages 109000.
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Nur Farah Meor Azlan, Maarten P. Koeners & Jinwei Zhang. (2021) Regulatory control of the Na–Cl co-transporter NCC and its therapeutic potential for hypertension. Acta Pharmaceutica Sinica B 11:5, pages 1117-1128.
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Adrián Rafael Murillo-de-Ozores, Alejandro Rodríguez-Gama, Héctor Carbajal-Contreras, Gerardo Gamba & María Castañeda-Bueno. (2021) WNK4 kinase: from structure to physiology. American Journal of Physiology-Renal Physiology 320:3, pages F378-F403.
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Manuel A. Anderegg, Giuseppe Albano, Daniela Hanke, Christine Deisl, Dominik E. Uehlinger, Simone Brandt, Rajesh Bhardwaj, Matthias A. Hediger & Daniel G. Fuster. (2021) The sodium/proton exchanger NHA2 regulates blood pressure through a WNK4-NCC dependent pathway in the kidney. Kidney International 99:2, pages 350-363.
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Qin Guo, Ya Zhang, Geng-Ru Jiang & Chong Zhang. (2021) Decreased KLHL3 expression is involved in the activation of WNK-OSR1/SPAK-NCC cascade in type 1 diabetic mice. Pflügers Archiv - European Journal of Physiology 473:2, pages 185-196.
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Yohei Arai, Kenichi Asano, Shintaro Mandai, Fumiaki Ando, Koichiro Susa, Takayasu Mori, Naohiro Nomura, Tatemitsu Rai, Masato Tanaka, Shinichi Uchida & Eisei Sohara. (2020) WNK1–TAK1 signaling suppresses lipopolysaccharide-induced cytokine production and classical activation in macrophages. Biochemical and Biophysical Research Communications 533:4, pages 1290-1297.
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Hélène Louis-Dit-Picard, Ilektra Kouranti, Chloé Rafael, Irmine Loisel-Ferreira, Maria Chavez-Canales, Waed Abdel-Khalek, Eduardo R. Argaiz, Stéphanie Baron, Sarah Vacle, Tiffany Migeon, Richard Coleman, Marcio Do Cruzeiro, Marguerite Hureaux, Nirubiah Thurairajasingam, Stéphane Decramer, Xavier Girerd, Kevin O’Shaugnessy, Paolo Mulatero, Gwenaëlle Roussey, Ivan Tack, Robert Unwin, Rosa Vargas-Poussou, Olivier Staub, Richard Grimm, Paul A. Welling, Gerardo Gamba, Eric Clauser, Juliette Hadchouel & Xavier Jeunemaitre. (2020) Mutation affecting the conserved acidic WNK1 motif causes inherited hyperkalemic hyperchloremic acidosis. Journal of Clinical Investigation 130:12, pages 6379-6394.
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Taisuke Furusho, Shinichi Uchida & Eisei Sohara. (2020) The WNK signaling pathway and salt-sensitive hypertension. Hypertension Research 43:8, pages 733-743.
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Taisuke Furusho, Eisei Sohara, Shintaro Mandai, Hiroaki Kikuchi, Naohiro Takahashi, Takuya Fujimaru, Hiroko Hashimoto, Yohei Arai, Fumiaki Ando, Moko Zeniya, Takayasu Mori, Koichiro Susa, Kiyoshi Isobe, Naohiro Nomura, Kohei Yamamoto, Tomokazu Okado, Tatemitsu Rai & Shinichi Uchida. (2020) Renal TNFα activates the WNK phosphorylation cascade and contributes to salt-sensitive hypertension in chronic kidney disease. Kidney International 97:4, pages 713-727.
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A. P. Garneau, S. Slimani, L. E. Tremblay, M. J. Fiola, A. A. Marcoux & P. Isenring. (2019) K+-Cl− cotransporter 1 (KCC1): a housekeeping membrane protein that plays key supplemental roles in hematopoietic and cancer cells. Journal of Hematology & Oncology 12:1.
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Holly Mabillard & John A. Sayer. (2019) The Molecular Genetics of Gordon Syndrome. Genes 10:12, pages 986.
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Xiaoxian Shi, Senfeng Xiang, Ji Cao, Hong Zhu, Bo Yang, Qiaojun He & Meidan Ying. (2019) Kelch-like proteins: Physiological functions and relationships with diseases. Pharmacological Research 148, pages 104404.
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Jenny van der Wijst, Hendrica Belge, René J. M. Bindels & Olivier Devuyst. (2019) Learning Physiology from Inherited Kidney Disorders. Physiological Reviews 99:3, pages 1575-1653.
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Mauricio Ostrosky-Frid, María Castañeda-Bueno & Gerardo Gamba. (2019) Regulation of the renal NaCl cotransporter by the WNK/SPAK pathway: lessons learned from genetically altered animals. American Journal of Physiology-Renal Physiology 316:1, pages F146-F158.
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Sayaka Yoshida, Yuya Araki, Takayasu Mori, Emi Sasaki, Yuri Kasagi, Kiyoshi Isobe, Koichiro Susa, Yuichi Inoue, Pascale Bomont, Tomokazu Okado, Tatemitsu Rai, Shinichi Uchida & Eisei Sohara. (2018) Decreased KLHL3 expression is involved in the pathogenesis of pseudohypoaldosteronism type II caused by cullin 3 mutation in vivo. Clinical and Experimental Nephrology 22:6, pages 1251-1257.
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Ryan J. Cornelius, Jinge Si, Catherina A. Cuevas, Jonathan W. Nelson, Brittany D.K. Gratreak, Ruggero Pardi, Chao-Ling Yang & David H. Ellison. (2018) Renal COP9 Signalosome Deficiency Alters CUL3-KLHL3-WNK Signaling Pathway. Journal of the American Society of Nephrology 29:11, pages 2627-2640.
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Hiroko Hashimoto, Naohiro Nomura, Wakana Shoda, Kiyoshi Isobe, Hiroaki Kikuchi, Kouhei Yamamoto, Takuya Fujimaru, Fumiaki Ando, Takayasu Mori, Tomokazu Okado, Tatemitsu Rai, Shinichi Uchida & Eisei Sohara. (2018) Metformin increases urinary sodium excretion by reducing phosphorylation of the sodium-chloride cotransporter. Metabolism 85, pages 23-31.
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Lu Qiu, Meng Wang, Yuping Zhu, Yuancai Xiang & Yiguo Zhang. (2018) A Naturally-Occurring Dominant-Negative Inhibitor of Keap1 Competitively against Its Negative Regulation of Nrf2. International Journal of Molecular Sciences 19:8, pages 2150.
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Shintaro Mandai, Takayasu Mori, Naohiro Nomura, Taisuke Furusho, Yohei Arai, Hiroaki Kikuchi, Emi Sasaki, Eisei Sohara, Tatemitsu Rai & Shinichi Uchida. (2018) WNK1 regulates skeletal muscle cell hypertrophy by modulating the nuclear localization and transcriptional activity of FOXO4. Scientific Reports 8:1.
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Mohammed Z. Ferdaus & James A. McCormick. (2018)
Mechanisms and controversies in mutant
Cul3
-mediated familial hyperkalemic hypertension
. American Journal of Physiology-Renal Physiology 314:5, pages F915-F920.
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Ji Cheng, Jianping Guo, Zhiwei Wang, Brian J. North, Kaixiong Tao, Xiangpeng Dai & Wenyi Wei. (2018) Functional analysis of Cullin 3 E3 ligases in tumorigenesis. Biochimica et Biophysica Acta (BBA) - Reviews on Cancer 1869:1, pages 11-28.
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Mohammed Z. Ferdaus, Lauren N. Miller, Larry N. Agbor, Turgay Saritas, Jeffrey D. Singer, Curt D. Sigmund & James A. McCormick. (2017) Mutant Cullin 3 causes familial hyperkalemic hypertension via dominant effects. JCI Insight 2:24.
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Koichiro Susa, Eisei Sohara, Daiei Takahashi, Tomokazu Okado, Tatemitsu Rai & Shinichi Uchida. (2017) WNK4 is indispensable for the pathogenesis of pseudohypoaldosteronism type II caused by mutant KLHL3. Biochemical and Biophysical Research Communications 491:3, pages 727-732.
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Yuri Kasagi, Daiei Takahashi, Tomomi Aida, Hidenori Nishida, Naohiro Nomura, Moko Zeniya, Takayasu Mori, Emi Sasaki, Fumiaki Ando, Tatemitsu Rai, Shinichi Uchida & Eisei Sohara. (2017) Impaired degradation of medullary WNK4 in the kidneys of KLHL2 knockout mice. Biochemical and Biophysical Research Communications 487:2, pages 368-374.
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