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Human Mitochondrial Leucyl-tRNA Synthetase Corrects Mitochondrial Dysfunctions Due to the tRNALeu(UUR) A3243G Mutation, Associated with Mitochondrial Encephalomyopathy, Lactic Acidosis, and Stroke-Like Symptoms and Diabetes

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Pages 2147-2154 | Received 16 Dec 2009, Accepted 22 Feb 2010, Published online: 20 Mar 2023

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Pingping Jiang, Meng Wang, Ling Xue, Yun Xiao, Jialing Yu, Hui Wang, Juan Yao, Hao Liu, Yanyan Peng, Hanqing Liu, Haiying Li, Ye Chen & Min-Xin Guan. (2016) A Hypertension-Associated tRNAAla Mutation Alters tRNA Metabolism and Mitochondrial Function. Molecular and Cellular Biology 36:14, pages 1920-1930.
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