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Original Research

Survival in the Swedish cohort with alpha-1-antitrypsin deficiency, up to the age of 43–45 years

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Pages 525-530 | Published online: 28 Feb 2019

Keep up to date with the latest research on this topic with citation updates for this article.

Read on this site (4)

David Nygren, Ulrica Mölstad, Hans Thulesius, Magnus Hillman, Lars Mikael Broman, Hanan Tanash, Mona Landin-Olsson, Magnus Rasmussen & Maria Thunander. (2022) Low Prevalence of Mild Alpha-1-Antitrypsin Deficiency in Hospitalized COVID-19-Patients. International Journal of General Medicine 15, pages 5843-5848.
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Georg Rüdiger Schramm, Behrouz Mostafavi, Eeva Piitulainen, Per Wollmer & Hanan A Tanash. (2021) Lung Function and Health Status in Individuals with Severe Alpha-1-Antitrypsin Deficiency at the Age of 42. International Journal of Chronic Obstructive Pulmonary Disease 16, pages 3477-3485.
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Anita Pye, Sheeba Khan, Tony Whitehouse & Alice M Turner. (2021) Personalizing liver targeted treatments and transplantation for patients with alpha-1 antitrypsin deficiency. Expert Review of Precision Medicine and Drug Development 6:1, pages 65-78.
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Joanna Chorostowska-Wynimko, Miriam Barrecheguren, Ilaria Ferrarotti, Timm Greulich, Robert A Sandhaus & Michael Campos. (2020) New Patient-Centric Approaches to the Management of Alpha-1 Antitrypsin Deficiency. International Journal of Chronic Obstructive Pulmonary Disease 15, pages 345-355.
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Articles from other publishers (10)

Daniel Q. Huang, Kai En Chan, Caitlyn Tan, Rebecca Wenling Zeng, Benjamin Koh, Elden Yen Hng Ong, Charlotte Chung Hui Ong, Christen En Ya Ong, Darren J. H. Tan, Wen Hui Lim, Elina Cho, Eunice X. X. Tan, Margaret L. P. Teng, Cheng Han Ng, Benjamin Nah, Mei Chin Lim, Mark Muthiah, Virginia C. Clark & Rohit Loomba. (2023) Meta‐analysis: Prevalence of significant or advanced fibrosis in adults with alpha‐1‐antitrypsin deficiency. Alimentary Pharmacology & Therapeutics.
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J.-F. Mornex. (2022) Le déficit en alpha 1-antitrypsine. Revue des Maladies Respiratoires 39:8, pages 698-707.
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J.-F. Mornex, M. Balduyck, M. Bouchecareilh, A. Cuvelier, R. Epaud, M. Kerjouan, O. Le Rouzic, C. Pison, L. Plantier, M.-C. Pujazon, M. Reynaud-Gaubert, A. Toutain, B. Trumbic, M.-C. Willemin, M. Zysman, O. Brun, M. Campana, F. Chabot, V. Chamouard, M. Dechomet, J. Fauve, B. Girerd, C. Gnakamene, S. Lefrançois, J.-N. Lombard, B. Maitre, C. Maynié-François, A. Moerman, A. Payancé, P. Reix, D. Revel, M.-P. Revel, M. Schuers, P. Terrioux, D. Theron, F. Willersinn, V. Cottin & H. Mal. (2022) Atteinte pulmonaire du déficit en alpha-1 antitrypsine. Recommandations pratiques pour le diagnostic et la prise en charge. Revue des Maladies Respiratoires 39:7, pages 633-656.
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Anandini Suri, Dhiren Patel & Jeffrey H. Teckman. (2022) Alpha-1 Antitrypsin Deficiency Liver Disease. Clinics in Liver Disease 26:3, pages 391-402.
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Malin Fromme, Carolin V. Schneider, Christian Trautwein, Nicola Brunetti-Pierri & Pavel Strnad. (2022) Alpha-1 antitrypsin deficiency: A re-surfacing adult liver disorder. Journal of Hepatology 76:4, pages 946-958.
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Malin Fromme, Carolin V Schneider, Vitor Pereira, Karim Hamesch, Monica Pons, Matthias C Reichert, Federica Benini, Paul Ellis, Katrine H Thorhauge, Mattias Mandorfer, Barbara Burbaum, Vivien Woditsch, Joanna Chorostowska-Wynimko, Jef Verbeek, Frederik Nevens, Joan Genesca, Marc Miravitlles, Alexa Nuñez, Benedikt Schaefer, Heinz Zoller, Sabina Janciauskiene, Nélia Abreu, Luís Jasmins, Rui Gaspar, Rodrigo Liberal, Guilherme Macedo, Ravi Mahadeva, Catarina Gomes, Kai Markus Schneider, Michael Trauner, Aleksander Krag, Bibek Gooptu, Douglas Thorburn, Aileen Marshall, John R Hurst, David A Lomas, Frank Lammert, Nadine T Gaisa, Virginia Clark, William Griffiths, Christian Trautwein, Alice M Turner, Noel G McElvaney & Pavel Strnad. (2022) Hepatobiliary phenotypes of adults with alpha-1 antitrypsin deficiency. Gut 71:2, pages 415-423.
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Lloyd Steele, Charlie D. Mitchell, Alexa R. Shipman & Kate E. Shipman. (2022) Alpha-1 antitrypsin deficiency–associated panniculitis: A potentially challenging diagnosis but an important one for patients. Journal of the American Academy of Dermatology 86:2, pages e67-e68.
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Daiki Abukawa. 2021. Introduction to Biliary Atresia. Introduction to Biliary Atresia 113 121 .
Carolin V. Schneider, Karim Hamesch, Annika Gross, Mattias Mandorfer, Linda S. Moeller, Vitor Pereira, Monica Pons, Pawel Kuca, Matthias C. Reichert, Federica Benini, Barbara Burbaum, Jessica Voss, Marla Gutberlet, Vivien Woditsch, Cecilia Lindhauer, Malin Fromme, Julia Kümpers, Lisa Bewersdorf, Benedikt Schaefer, Mohammed Eslam, Robert Bals, Sabina Janciauskiene, Joana Carvão, Daniel Neureiter, Biaohuan Zhou, Katharina Wöran, Heike Bantel, Andreas Geier, Timm Dirrichs, Felix Stickel, Alexander Teumer, Jef Verbeek, Frederik Nevens, Olivier Govaere, Marcin Krawczyk, Tania Roskams, Johannes Haybaeck, Georg Lurje, Joanna Chorostowska-Wynimko, Joan Genesca, Thomas Reiberger, Frank Lammert, Aleksander Krag, Jacob George, Quentin M. Anstee, Michael Trauner, Christian Datz, Nadine T. Gaisa, Helmut Denk, Christian Trautwein, Elmar Aigner & Pavel Strnad. (2020) Liver Phenotypes of European Adults Heterozygous or Homozygous for Pi∗Z Variant of AAT (Pi∗MZ vs Pi∗ZZ genotype) and Noncarriers. Gastroenterology 159:2, pages 534-548.e11.
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Pavel StrnadNoel G. McElvaneyDavid A. Lomas. (2020) Alpha 1 -Antitrypsin Deficiency . New England Journal of Medicine 382:15, pages 1443-1455.
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