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Review

Alpha 1 Antitrypsin Therapy in Patients with Alpha 1 Antitrypsin Deficiency: Perspectives from a Registry Study and Practical Considerations for Self-Administration During the COVID-19 Pandemic

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Pages 2983-2996 | Published online: 01 Nov 2021

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María Torres-Durán, José Luis López-Campos, Myriam Calle Rubio, Carmen Montero-Martínez, Ana Priegue Carrera, Rosanel Amaro Rodríguez, Miriam Barrecheguren, María Ángeles Barrio Guirado, Francisco Javier Callejas-González, Francisco Casas-Maldonado, Layla Diab-Cáceres, Pilar García-Meseguer, José María Hernández-Pérez, Lourdes Lázaro-Asegurado, Cristina Martínez-González, Carlos Martínez Rivera, Francisco Javier Michel, José-Bruno Montoro-Ronsano, Raquel Sánchez, Marta Ortiz-Pica, Isabel Parra, José Pablo Quintero García, María del Rosario Ruiz-Serrano-de la Espada, Begoña Tortajada-Goitia & Marc Miravitlles. (2023) Recommendations for the Implementation of the Self-Administration of Alpha-1 Antitrypsin. International Journal of Chronic Obstructive Pulmonary Disease 18, pages 1691-1700.
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Annalisa Bianchera, Esraa’a Alomari, Annalisa Michielon, Gianluca Bazzoli, Nicoletta Ronda, Giovanni Pighini, Ilaria Zanotti, Carmine Giorgio, Andrea Mozzarelli, Ruggero Bettini & Stefano Bruno. (2022) Recombinant Alpha-1 Antitrypsin as Dry Powder for Pulmonary Administration: A Formulative Proof of Concept. Pharmaceutics 14:12, pages 2754.
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Franziska C. Trudzinski, Maria Ada Presotto, Emanuel Buck, Felix J. F. Herth & Markus Ries. (2022) Orphan drug development in alpha-1 antitypsin deficiency. Scientific Reports 12:1.
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Sangeetha Thangavelu, Balamuralikrishnan Balasubramanian, Sampathkumar Palanisamy, Velayuthaprabhu Shanmugam, Senthilkumar Natchiappan, Syed Ibrahim Kalibulla, Baskaran Rathinasamy & Vijaya Anand Arumugam. (2022) Characterization and phytoconstituents of Petroselinum crispum (Mill) and Coriandrum sativum (Linn) and their impacts on inflammation—An in vitro analysis against human adenocarcinoma cells with molecular docking. South African Journal of Botany 146, pages 776-788.
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Ivanna Shymanska, Оlena Trutiak, Оlena Lychkovska, Halyna Makukh & Hayane Akopyan. (2022) Genetic testing of allelic variants of PIZ (GLU342Lys, RS28929474) and PIS (GLU264Val, RS17580) of SERPINA1 gene in children with bronchial asthma. EUREKA: Life Sciences:2, pages 36-44.
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Jacob Colello, Anna Ptasinski, Xiang Zhan, Sundeep Kaur & Timothy Craig. (2022) Assessment of Patient Perspectives and Barriers to Self-Infusion of Augmentation Therapy for Alpha-1 Antitrypsin Deficiency During the COVID-19 Pandemic. Pulmonary Therapy 8:1, pages 95-103.
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Federica Boraldi, Francesco Demetrio Lofaro, Andrea Cossarizza & Daniela Quaglino. (2022) The “Elastic Perspective” of SARS-CoV-2 Infection and the Role of Intrinsic and Extrinsic Factors. International Journal of Molecular Sciences 23:3, pages 1559.
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