124
Views
24
CrossRef citations to date
0
Altmetric
Review

The impact of alpha-1 antitrypsin augmentation therapy on neutrophil-driven respiratory disease in deficient individuals

, , , &
Pages 123-134 | Published online: 26 Mar 2018

Keep up to date with the latest research on this topic with citation updates for this article.

Read on this site (1)

Priya S Chukowry, Ross Gareth Edgar & Alice M Turner. (2019) Alpha 1 antitrypsin deficiency: a rare multisystem disease, predominantly affecting the lung. Expert Opinion on Orphan Drugs 7:7-8, pages 315-326.
Read now

Articles from other publishers (23)

Ara Jo & Dae Woo Kim. (2023) Neutrophil Extracellular Traps in Airway Diseases: Pathological Roles and Therapeutic Implications. International Journal of Molecular Sciences 24:5, pages 5034.
Crossref
Nurdan Kokturk, Nazli Khodayari, Jorge Lascano, E. Leonard Riley & Mark L. Brantly. (2023) Lung Inflammation in alpha-1-antitrypsin deficient individuals with normal lung function. Respiratory Research 24:1.
Crossref
Annalisa Bianchera, Esraa’a Alomari, Annalisa Michielon, Gianluca Bazzoli, Nicoletta Ronda, Giovanni Pighini, Ilaria Zanotti, Carmine Giorgio, Andrea Mozzarelli, Ruggero Bettini & Stefano Bruno. (2022) Recombinant Alpha-1 Antitrypsin as Dry Powder for Pulmonary Administration: A Formulative Proof of Concept. Pharmaceutics 14:12, pages 2754.
Crossref
Hamad Ghaleb Dailah. (2022) Therapeutic Potential of Small Molecules Targeting Oxidative Stress in the Treatment of Chronic Obstructive Pulmonary Disease (COPD): A Comprehensive Review. Molecules 27:17, pages 5542.
Crossref
Alon Gimmon, Lior Sherker, Lena Kojukarov, Melodie Zaknoun, Yotam Lior, Tova Fadel, Ronen Schuster, Eli C. Lewis & Eldad Silberstein. (2022) Accelerated Wound Border Closure Using a Microemulsion Containing Non-Inhibitory Recombinant α1-Antitrypsin. International Journal of Molecular Sciences 23:13, pages 7364.
Crossref
Petr Šálek, Jana Dvořáková, Sviatoslav Hladysh, Diana Oleshchuk, Ewa Pavlova, Jan Kučka & Vladimír Proks. (2022) Stimuli-responsive polypeptide nanogels for trypsin inhibition. Beilstein Journal of Nanotechnology 13, pages 538-548.
Crossref
Jungnam Lee, Naweed Mohammad, Yuanqing Lu, Keunsoo Kang, Kyudong Han & Mark Brantly. (2022) Alu RNA induces NLRP3 expression through TLR7 activation in α-1-antitrypsin–deficient macrophages. JCI Insight 7:12.
Crossref
Malik Bisserier, Xiao-Qing Sun, Shahood Fazal, Irene C. Turnbull, Sébastien Bonnet & Lahouaria Hadri. (2022) Novel Insights into the Therapeutic Potential of Lung-Targeted Gene Transfer in the Most Common Respiratory Diseases. Cells 11:6, pages 984.
Crossref
Annalisa Bianchera, Esraa Alomari & Stefano Bruno. (2022) Augmentation Therapy with Alpha-1 Antitrypsin: Present and Future of Production, Formulation, and Delivery. Current Medicinal Chemistry 29:3, pages 385-410.
Crossref
John Charles Rotondo, Giorgio Aquila, Lucia Oton-Gonzalez, Rita Selvatici, Paola Rizzo, Monica De Mattei, Rita Pavasini, Mauro Tognon, Gianluca Calogero Campo & Fernanda Martini. (2021) Methylation of SERPINA1 gene promoter may predict chronic obstructive pulmonary disease in patients affected by acute coronary syndrome. Clinical Epigenetics 13:1.
Crossref
Timo Burster, Zhadyra Mustafa, Dinara Myrzakhmetova, Anuar Zhanapiya & Michal Zimecki. (2021) Hindrance of the Proteolytic Activity of Neutrophil-Derived Serine Proteases by Serine Protease Inhibitors as a Management of Cardiovascular Diseases and Chronic Inflammation. Frontiers in Chemistry 9.
Crossref
Abdul-Hamid Emwas, Mawadda Alghrably, Manel Dhahri, Abeer Sharfalddin, Rawiah Alsiary, Mariusz Jaremko, Gavino Faa, Marcello Campagna, Terenzio Congiu, Monica Piras, Marco Piludu, Giuseppina Pichiri, Pierpaolo Coni & Joanna Izabela Lachowicz. (2021) Living with the enemy: from protein-misfolding pathologies we know, to those we want to know. Ageing Research Reviews 70, pages 101391.
Crossref
David J. Wilkinson. (2021) Serpins in cartilage and osteoarthritis: what do we know?. Biochemical Society Transactions 49:2, pages 1013-1026.
Crossref
Benjamin David, Mona Bafadhel, Leo Koenderman & Antony De Soyza. (2021) Eosinophilic inflammation in COPD: from an inflammatory marker to a treatable trait. Thorax 76:2, pages 188-195.
Crossref
Matthew J. McNulty, David Z. Silberstein, Brooks T. Kuhn, Hal S. Padgett, Somen Nandi, Karen A. McDonald & Carroll E. Cross. (2021) Alpha-1 antitrypsin deficiency and recombinant protein sources with focus on plant sources: Updates, challenges and perspectives. Free Radical Biology and Medicine 163, pages 10-30.
Crossref
Tao Wan & Yuan Ping. (2021) Delivery of genome-editing biomacromolecules for treatment of lung genetic disorders. Advanced Drug Delivery Reviews 168, pages 196-216.
Crossref
Shvetank Bhatt, Jovita Kanoujia, A. N. Nagappa & K. Sreedhara R. Pai. 2021. Targeting Cellular Signalling Pathways in Lung Diseases. Targeting Cellular Signalling Pathways in Lung Diseases 127 146 .
Lucia Beltran-Camacho, Margarita Jimenez-Palomares, Marta Rojas-Torres, Ismael Sanchez-Gomar, Antonio Rosal-Vela, Sara Eslava-Alcon, Mª Carmen Perez-Segura, Ana Serrano, Borja Antequera-González, Jose Angel Alonso-Piñero, Almudena González-Rovira, Mª Jesús Extremera-García, Manuel Rodriguez-Piñero, Rafael Moreno-Luna, Martin Røssel Larsen & Mª Carmen Durán-Ruiz. (2020) Identification of the initial molecular changes in response to circulating angiogenic cells-mediated therapy in critical limb ischemia. Stem Cell Research & Therapy 11:1.
Crossref
Ronen Schuster, Noa Motola-Kalay, Boris M. Baranovski, Liliana Bar, Naveh Tov, Michal Stein, Eli C. Lewis, Michal Ayalon & Yuval Sagiv. (2020) Distinct anti-inflammatory properties of alpha1-antitrypsin and corticosteroids reveal unique underlying mechanisms of action. Cellular Immunology 356, pages 104177.
Crossref
Simona Viglio, Paolo Iadarola, Maura D’Amato & Jan Stolk. (2020) Methods of Purification and Application Procedures of Alpha1 Antitrypsin: A Long-Lasting History. Molecules 25:17, pages 4014.
Crossref
Esra Karatas & Marion Bouchecareilh. (2020) Alpha 1-Antitrypsin Deficiency: A Disorder of Proteostasis-Mediated Protein Folding and Trafficking Pathways. International Journal of Molecular Sciences 21:4, pages 1493.
Crossref
Jana Kleinerova, Patricia Ging, Colin Rutherford, Iain Lawrie, Sara Winward, Donna Eaton, Karen C. Redmond & Jim J. Egan. (2019) The withdrawal of replacement therapy and outcomes in alpha-1 antitrypsin deficiency lung transplant recipients. European Respiratory Journal 53:5, pages 1900055.
Crossref
Emer P. Reeves, Danielle M. Dunlea, Karen McQuillan, Ciara A. O’Dwyer, Tomás P. Carroll, Radka Saldova, Prithvi Reddy Akepati, Mark R. Wormald, Oliver J. McElvaney, Vipatsorn Shutchaidat, Michael Henry, Paula Meleady, Joanne Keenan, Derek C. Liberti, Darrell N. Kotton, Pauline M. Rudd, Andrew A. Wilson & Noel G. McElvaney. (2019) Circulating Truncated Alpha-1 Antitrypsin Glycoprotein in Patient Plasma Retains Anti-Inflammatory Capacity. The Journal of Immunology 202:8, pages 2240-2253.
Crossref