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Hemoglobin
international journal for hemoglobin research
Volume 1, 1977 - Issue 8
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Original Article

Differences in Affinity of Variant β Chains for a Chains: A Possible Explanation for the Variation in the Percentages of β Chain Variants in Heterozygotes

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Pages 861-873 | Received 25 May 1977, Accepted 02 Aug 1977, Published online: 07 Jul 2009

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S. A. Liebhaber. (1989) α Thalassemia. Hemoglobin 13:7-8, pages 685-731.
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B. L. Anderson Fernandes. (1989) HB N-Baltimore or β95(FG2)LYS→GLU in Portugal. Hemoglobin 13:1, pages 83-87.
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L. N. Shulman & H. F. Bunn. (1988) Hb Deer Lodge in a Caucasian American: Effect of Iron Deficiency on Level of Variant. Hemoglobin 12:2, pages 197-199.
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S. Rahbar, G. Nozari, R. Chillar & R. Bruce Wallace. (1988) Further Evidence for a Post-Translational Phenomenon in the Interaction of α-Thalassemia with Sickle Cell Trait. Hemoglobin 12:1, pages 71-76.
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G. Martinez, R. Ferreira, A. Hernandez, A. Di Rienzo & B. Colombo. (1986) Association of HB H Disease with Sickle-Trait. Hemoglobin 10:4, pages 421-425.
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K. D. Lanclos, A. Kutlar, F. Kutlar, P. J. Ojwang, A. L. Reese & T. H. J. Huisman. (1986) The Effect of α-Thalassemia on the Level of Hybrid Hemoglobin Variants in Heterozygotes. Hemoglobin 10:4, pages 401-416.
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Samir K. Ballas & Deborah K. Park. (1985) Biosynthetic Evidence for Stability of Hb N-Baltimore. Hemoglobin 9:5, pages 489-494.
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K. C. Carstairs, A. Raulfs, A. Kutlar, S. S. Chen, B. B. Webber, J. B. Wilson & T. H. J. Huisman. (1985) Hb Fort Worth Or α227 (B8)Glu→Glyβ2 in a Black Family from Canada. Hemoglobin 9:2, pages 201-205.
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Wanda J. Whitten & Donald L. Rucknagel. (1981) The Proportion of HB A2 is Higher in Sickle Cell Trait Than in Normal Homozygotes. Hemoglobin 5:4, pages 371-378.
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Donald R. Harkness. (1980) Hematological and Clinical Features of Sickle Cell Diseases: a Review. Hemoglobin 4:3-4, pages 313-334.
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M. Marinucci, F. Mavilio, L. Tentori & A. Bestetti. (1979) Occurrence of Hb J Paris in An Italian Family and Recombination Studies on the Free Abnormal α-Chain. Hemoglobin 3:6, pages 465-469.
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S. Musumeci, G. Schiliro, A. Fisher, A. Musco, M. Maritiucci, F. Mavilio, P. P. Fontanarosa & L. Tentori. (1979) Hb J Baltimore (β 16 (A13) Gly ↣ Asp) in Association with β-Thalassemia in a Sicilian Family. Hemoglobin 3:6, pages 459-464.
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G. Brittenham, B. Lozoff, J. W. Harris, N. V. S. Nayudu, M. Gravely, J. B. Wilson, H. Lam & T. H. J. Huisman. (1978) Hemoglobin Hofu or αβ [126 (H4) Val → Glu] Found in Combination with Hemoglobin S. Hemoglobin 2:6, pages 541-549.
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E. P. Orringer, A. Felice, A. Reese, J. B. Wilson, H. Lam, M. E. Gravely & T. H. J. Huisman. (1978) Hb Nottingham (α;2β;2 (FG5) 98 VAL→GLY) in a Caucasian Male: Clinical and Biosynthetic Studies. Hemoglobin 2:4, pages 315-332.
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C. C. Qiu & E. C. Abraham. (2006) Evidence for posttranslational control of fetal hemoglobin synthesis. American Journal of Hematology 29:1, pages 58-59.
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C.-C. Qiu, J. Kasten-Jolly & E.C. Abraham. (1988) Human red cell acetyltransferase. Life Sciences 42:26, pages 2739-2748.
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I. Kirschner-Zilber, E. Setter & N. Shaklai. (1987) Association of hemoglobin chains with the cell membrane as a cause of red cell distortion in thalassemia. Biochemical Medicine and Metabolic Biology 38:1, pages 19-31.
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T.H.J. Huisman. (1987) Separation of hemoglobins and hemoglobin chains by high-performance liquid chromatography. Journal of Chromatography B: Biomedical Sciences and Applications 418, pages 277-304.
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J. Kasten-Jolly & E.C. Abraham. (1987) Influence of ?-chain amino-terminal acetylation on subunit assembly of human fetal hemoglobin. Biochimica et Biophysica Acta (BBA) - Protein Structure and Molecular Enzymology 913:1, pages 89-91.
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Junius G. AdamsIIIIII, Marsha V. Newman, Martin H. Steinberg & Joseph Desimone. (1986) Effect of Lead and Ethanol upon ?-Globin Synthesis in Sickle Reticulocytes. The American Journal of the Medical Sciences 292:5, pages 299-305.
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A. E. Felice, M. P. Cleek, E. M. Marino, K. M. McKie, V. C. McKie, B. K. Chang & T. H. J. Huisman. (1986) Different ? globin gene deletions among Black Americans. Human Genetics 73:3, pages 221-224.
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N T Mrabet, M J McDonald, S Turci, R Sarkar, A Szabo & H F Bunn. (1986) Electrostatic attraction governs the dimer assembly of human hemoglobin.. Journal of Biological Chemistry 261:11, pages 5222-5228.
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H. Franklin Bunn & Melisenda J. McDonald. (1983) Electrostatic interactions in the assembly of haemoglobin. Nature 306:5942, pages 498-500.
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Titus H. J. Huisman. (2006) Percentages of abnormal hemoglobins in adults with a heterozygosity for an α‐chain and/or a β‐chain variant. American Journal of Hematology 14:4, pages 393-404.
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Gisela Martínez & Rolando Menéndez. (1983) Differences in affinity of β and δ hemoglobin chains for α chains a possible explanation for the variation in the percentages of hemoglobin A2 in thalassemia and other disorders. Biochimica et Biophysica Acta (BBA) - Protein Structure and Molecular Enzymology 743:2, pages 256-259.
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T. H. J. Huisman, M. E. Gravely, J. B. Wilson, B. Webber, A. E. Felice & A. Miller. (2006) Interaction of the β chain variant hemoglobin leslie and the α chain variant hemoglobin montgomery in a black female. American Journal of Hematology 8:2, pages 139-147.
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