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Hemoglobin
international journal for hemoglobin research
Volume 15, 1991 - Issue 4
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Original Article

High Prevalence of α-Thalassemia in a Black Population of Brazil

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Pages 309-311 | Received 04 Jan 1991, Accepted 03 May 1991, Published online: 07 Jul 2009

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Read on this site (7)

Robéria M. Pontes, Elaine S. Costa, Patrícia F. R. Siqueira, Jussara F. F. Medeiros, Andréa Soares, Fabiana V. de Mello, Maria C. Maioli, Isaac L. S. Filho, Liliane R. Alves, Marcelo G. P. Land & Marcos K. Fleury. (2017) Protector effect of α-thalassaemia on cholecystitis and cholecystectomy in sickle cell disease. Hematology 22:7, pages 444-449.
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Januária Fonseca Matos, Luci Maria Sant'Ana Dusse, Rachel Versiani Bressane Stubbert, Mônica Ribeiro Ferreira, Wendel Coura-Vital, Ana Paula Salles Moura Fernandes, José Roberto de Faria, Karina Braga Gomes Borges & Maria das Graças Carvalho. (2013) Comparison of discriminative indices for iron deficiency anemia and β thalassemia trait in a Brazilian population. Hematology 18:3, pages 169-174.
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Kleber Yotsumoto Fertrin & Fernando Ferreira Costa. (2010) Genomic polymorphisms in sickle cell disease: implications for clinical diversity and treatment. Expert Review of Hematology 3:4, pages 443-458.
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Nadia M. Silva, Cinira S. Soledade, Fernando F. Costa & Maria F. Sonati. (2002) α-THALASSEMIA DOES NOT SIGNIFICANTLY CONTRIBUTE TO THE LOW MCV LEVEL OF Hb C TRAIT. Hemoglobin 26:3, pages 305-309.
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S. F. Fonseca, J. Kerbauy, C. Escrivao, M. S. Figueiredo, R. Cancado, V. R. Arruda, S. T. O. Saad & F. F. Costa. (1998) Genetic Analysis of β-Thalassemia Major and β-Thalassemia Intermedia in Brazil. Hemoglobin 22:3, pages 197-207.
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M. F. Sonati, E. M. Kimura, H. Z. W. Grotto, S. A. Gervasio & F. F. Costa. (1996) Hereditary Hemoglobinopathies in a Population from so. Hemoglobin 20:2, pages 175-179.
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M. J. Peres, L. Romão, H. Carreiro, I. Picanço, L. Batalha, H. A. Magalhães, M. C. Martins & J. Lavinha. (1995) Molecular Basis of A-Thalassa in Portugal. Hemoglobin 19:6, pages 343-352.
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Articles from other publishers (21)

Patricia F. R. Siqueira, Marcos K. Fleury, Robéria M. Pontes, Renata S. P. Silva, Elaine S. Costa & Marcelo G. P. Land. (2022) Novel Decision Tool for More Severe α-Thalassemia Genotypes Screening with Functional Loss of Two or More α-Globin Genes: A Diagnostic Test Study. Diagnostics 12:12, pages 3008.
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Natália O. Mota, Elza M. Kimura, Roberta D. Ferreira, Gisele A. Pedroso, Dulcinéia M. Albuquerque, Daniela M. Ribeiro, Magnun N. N. Santos, Cristina M. Bittar, Fernando F. Costa & Maria de Fatima Sonati. (2017) Rare α0-thalassemia deletions detected by MLPA in five unrelated Brazilian patients. Genetics and Molecular Biology 40:4, pages 768-773.
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Januária F. Matos, Luci M.S. Dusse, Karina B.G. Borges, Ricardo L.V. de Castro, Wendel Coura-Vital & Maria das G. Carvalho. (2017) Response to the assessment of the Matos & Carvalho index by Hoffmann and Urrechaga. Revista Brasileira de Hematologia e Hemoterapia 39:3, pages 290-291.
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Roberta Dorta Ferreira, Natália de Oliveira Mota, Elza Myiuki Kimura, Gisele Audrei Pedroso & Maria de Fatima Sonati. (2017) A combination of the -α3.7 and --MEDII alleles causing hemoglobin H disease in a Brazilian patient. Revista Brasileira de Hematologia e Hemoterapia 39:1, pages 80-83.
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Eliana LitsukoTomimatsu Shimauti, Danilo Grunig Humberto Silva, Eniuce Menezes de Souza, Eduardo Alves de Almeida, Francismar Prestes Leal & Claudia Regina Bonini-Domingos. (2015) Prevalence of βS-globin gene haplotypes, α-thalassemia (3.7 kb deletion) and redox status in patients with sickle cell anemia in the state of Paraná, Brazil. Genetics and Molecular Biology 38:3, pages 316-323.
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Cristiane Fernandes de Freitas Tavares, Jacqueline da Silva Guimarães & Ana Maria de Souza. (2015) Prevalence of hemoglobinopathies in school children: the importance of using confirmatory methods. Brazilian Journal of Pharmaceutical Sciences 51:2, pages 361-366.
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Jacqueline S. Guimarães, Juçara G. Cominal, Ana Cristina Silva-Pinto, Gordana Olbina, Yelena Z. Ginzburg, Vijay Nandi, Mark Westerman, Stefano Rivella & Ana Maria de Souza. (2015) Altered erythropoiesis and iron metabolism in carriers of thalassemia. European Journal of Haematology 94:6, pages 511-518.
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Roberta Faria Camilo-Araújo, Olga Maria Silverio Amancio, Maria Stella Figueiredo, Ana Carolina Cabanãs-Pedro & Josefina Aparecida Pellegrini Braga. (2014) Molecular analysis and association with clinical and laboratory manifestations in children with sickle cell anemia. Revista Brasileira de Hematologia e Hemoterapia 36:5, pages 334-339.
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Farid Menaa. (2013) Stroke in sickle cell anemia patients: A need for multidisciplinary approaches. Atherosclerosis 229:2, pages 496-503.
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Gustavo Henrique de Medeiros Alcoforado, Christiane Medeiros Bezerra, Telma Maria Araújo Moura Lemos, Denise Madureira de Oliveira, Elza Miyuki Kimura, Fernando Ferreira Costa, Maria de Fátima Sonati & Tereza Maria Dantas de Medeiros. (2012) Prevalence of α-thalassemia 3.7 kb deletion in the adult population of Rio Grande do Norte, Brazil. Genetics and Molecular Biology 35:3, pages 594-598.
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Greice Lemos Cardoso, Silvania Yukiko Lins Takanashi & João Farias Guerreiro. (2012) Inherited hemoglobin disorders in an Afro-Amazonian community: Saracura. Genetics and Molecular Biology 35:3, pages 553-556.
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C.N. Suemasu, E.M. Kimura, D.M. Oliveira, M.A.C. Bezerra, A.S. Araújo, F.F. Costa & M.F. Sonati. (2011) Characterization of alpha thalassemic genotypes by multiplex ligation-dependent probe amplification in the Brazilian population. Brazilian Journal of Medical and Biological Research 44:1, pages 16-22.
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Sandrine C. Wagner, Simone M. de Castro, Tatiana P. Gonzalez, Ana P. Santin, Leticia Filippon, Carina F. Zaleski, Laura A. Azevedo, Bruna Amorin, Sidia M. Callegari-Jacques & Mara H. Hutz. (2010) Prevalence of common α-thalassemia determinants in south Brazil: importance for the diagnosis of microcytic anemia. Genetics and Molecular Biology 33:4, pages 641-645.
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Elisângela Vitória Adorno, Ângela Zanette, Isa Lyra, Magda Oliveira Seixas, Mitermayer Galvão Reis & Marilda Souza Gonçalves. (2008) Clinical and molecular characteristics of sickle cell anemia in the northeast of Brazil. Genetics and Molecular Biology 31:3, pages 621-625.
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Julio A. da Luz, Mónica Sans, Elza Miyuki Kimura, Dulcinéia Martins Albuquerque, Maria de Fatima Sonati & Fernando Ferreira Costa. (2006) alpha-thalassemia, HbS, and beta-globin gene cluster haplotypes in two Afro-Uruguayan sub-populations from northern and southern Uruguay. Genetics and Molecular Biology 29:4, pages 595-600.
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Isa Menezes Lyra, Marilda Souza Gonçalves, Joseffina A. Pellegrinei Braga, Maria de Fátima Gesteira, Maria Helena Carvalho, Sara Terezinha Olalla Saad, Maria Stella Figueiredo & Fernando Ferreira Costa. (2005) Clinical, hematological, and molecular characterization of sickle cell anemia pediatric patients from two different cities in Brazil. Cadernos de Saúde Pública 21:4, pages 1287-1290.
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Elisângela Vitória Adorno, Fábio David Couto, José Pereira de Moura Neto, Joelma Figueiredo Menezes, Marco Rêgo, Mitermayer Galvão dos Reis & Marilda Souza Gonçalves. (2005) Hemoglobinopathies in newborns from Salvador, Bahia, Northeast Brazil. Cadernos de Saúde Pública 21:1, pages 292-298.
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E. Borges, M.R.S.C. Wenning, E.M. Kimura, S.A. Gervásio, F.F. Costa & M.F. Sonati. (2001) High prevalence of alpha-thalassemia among individuals with microcytosis and hypochromia without anemia. Brazilian Journal of Medical and Biological Research 34:6, pages 759-762.
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M.R.S.C. Wenning, E.M. Kimura, F.F. Costa, S.T.O. Saad, S. Gervásio, S.B. de Jorge, E. Borges, N.M. Silva & M.F. Sonati. (2000) alpha-Globin genes: thalassemic and structural alterations in a Brazilian population. Brazilian Journal of Medical and Biological Research 33:9, pages 1041-1045.
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M.S. Figueiredo, J. Kerbauy, M.S. Gonçalves, V.R. Arruda, S.T.O. Saad, M.F. Sonati, T. Stoming & F.F. Costa. (1996) Effect of α-thalassemia and β-globin gene cluster haplotypes on the hematological and clinical features of sickle-cell anemia in Brazil. American Journal of Hematology 53:2, pages 72-76.
Crossref
Mariane B. Compri, Newton C. Polimeno, Mércia B. Stella & Antônio S. Ramalho. (1996) Programa comunitário de hemoglobinopatias hereditárias em população estudantil brasileira. Revista de Saúde Pública 30:2, pages 187-195.
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