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ORIGINAL RESEARCH

Health-Related Quality of Life in Patients with Alpha-1 Antitrypsin Deficiency: The French Experience

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Joanna Chorostowska-Wynimko, Miriam Barrecheguren, Ilaria Ferrarotti, Timm Greulich, Robert A Sandhaus & Michael Campos. (2020) New Patient-Centric Approaches to the Management of Alpha-1 Antitrypsin Deficiency. International Journal of Chronic Obstructive Pulmonary Disease 15, pages 345-355.
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Jeanne Marie Perotin, Sylvie Leroy, Charles Hugo Marquette, Hervé Mal, Hervé Dutau, Arnaud Bourdin, Jean Michel Vergnon, Christophe Pison, Coralie Barbe & Gaëtan Deslee. (2018) Endobronchial coil treatment in severe emphysema patients with alpha-1 antitrypsin deficiency. International Journal of Chronic Obstructive Pulmonary Disease 13, pages 3645-3649.
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Nikolas Bernhard, Philipp M Lepper, Claus Vogelmeier, Martina Seibert, Stefan Wagenpfeil, Robert Bals & Sebastian Fähndrich. (2017) Deterioration of quality of life is associated with the exacerbation frequency in individuals with alpha-1-antitrypsin deficiency – analysis from the German Registry. International Journal of Chronic Obstructive Pulmonary Disease 12, pages 1427-1437.
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Articles from other publishers (14)

Jean-François Mornex, Julie Traclet, Olivier Guillaud, Magali Dechomet, Christine Lombard, Mathias Ruiz, Didier Revel, Philippe Reix & Vincent Cottin. (2023) Alpha1-antitrypsin deficiency: An updated review. La Presse Médicale 52:3, pages 104170.
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S.A. Papiris, M. Veith, A.I. Papaioannou, V. Apollonatou, I. Ferrarotti, S. Ottaviani, A. Tzouvelekis, V. Tzilas, N. Rovina, G. Stratakos, I. Gerogianni, Z. Daniil, L. Kolilekas, K. Dimakou, G. Pitsidianakis, N. Tzanakis, S. Tryfon, F. Fragopoulos, E.M. Antonogiannaki, A. Lazaratou, E. Fouka, D. Papakosta, P. Emmanouil, N. Anagnostopoulos, T. Karampitsakos, K. Vlami, M. Kallieri, P. Lyberopoulos, S. Loukides, D. Bouros, A. Bush, M. Balduyck, C. Lombard, V. Cottin, J.F. Mornex, C.F. Vogelmeier, T. Greulich & E.D. Manali. (2023) Alpha1-antitrypsin deficiency in Greece: Focus on rare variants. Pulmonology.
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J.-F. Mornex. (2022) Le déficit en alpha 1-antitrypsine. Revue des Maladies Respiratoires 39:8, pages 698-707.
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Marc Miravitlles, Mike Herepath, Asim Priyendu, Sheetal Sharma, Tatiana Vilchez, Oliver Vit, Michaela Haensel, Virginie Lepage, Helena Gens & Timm Greulich. (2022) Disease burden associated with alpha-1 antitrypsin deficiency: systematic and structured literature reviews. European Respiratory Review 31:163, pages 210262.
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Cláudia Henrique da Costa, Arnaldo José Noronha Filho, Rosa Maria Fernambel Marques e Silva, Thaís Ferrari da Cruz, Valeria de Oliveira Monteiro, Margareth Pio & Rogério Lopes Rufino. (2019) Alpha 1-antitrypsin deficiency in patients with chronic obstructive pulmonary disease patients: is systematic screening necessary?. BMC Research Notes 12:1.
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Ildikó Horváth, Maria Canotilho, Jan Chlumský, Joanna Chorostowska-Wynimko, Luciano Corda, Eric Derom, Joachim H. Ficker, Meinhard Kneussl, Marc Miravitlles, Maria Sucena, Gabriel Thabut, Alice M. Turner, Emily van ’t Wout & N. Gerard McElvaney. (2019) Diagnosis and management of α 1 -antitrypsin deficiency in Europe: an expert survey . ERJ Open Research 5:1, pages 00171-2018.
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Franck F. Rahaghi & Marc Miravitlles. (2017) Long-term clinical outcomes following treatment with alpha 1-proteinase inhibitor for COPD associated with alpha-1 antitrypsin deficiency: a look at the evidence. Respiratory Research 18:1.
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G. Thabut. (2017) Cas clinique n° 4 : Emphysème et déficit en alpha-1 antitrypsine. Revue des Maladies Respiratoires Actualités 9:1, pages 29-31.
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Margarida Torres Redondo, Elsa Campoa, Luis Ruano & Maria Sucena. (2017) Calidad de vida relacionada con la salud en pacientes con déficit de α1 antitripsina: estudio transversal. Archivos de Bronconeumología 53:2, pages 49-54.
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Margarida Torres Redondo, Elsa Campoa, Luis Ruano & Maria Sucena. (2017) Health-Related Quality of Life in Patients With Alpha-1 Antitrypsin Deficiency: A Cross Sectional Study. Archivos de Bronconeumología (English Edition) 53:2, pages 49-54.
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Ignacio Blanco. 2017. Blanco's Overview of Alpha-1 Antitrypsin Deficiency. Blanco's Overview of Alpha-1 Antitrypsin Deficiency 193 206 .
Ignacio Blanco. 2017. Blanco's Overview of Alpha-1 Antitrypsin Deficiency. Blanco's Overview of Alpha-1 Antitrypsin Deficiency 115 128 .
Ignacio Blanco. 2017. Blanco's Overview of Alpha-1 Antitrypsin Deficiency. Blanco's Overview of Alpha-1 Antitrypsin Deficiency 1 11 .
Kate McKeage & Katherine A. Lyseng-Williamson. (2016) Human α1-proteinase inhibitor (Respreeza®) in α1-antitrypsin deficiency emphysema: a guide to its use in the EU. Drugs & Therapy Perspectives 32:10, pages 422-427.
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