Mucinous cystic liver neoplasm with invasive component and sarcomatous differentiation

Abstract

Background

Hepatobiliary mucinous cystic neoplasms (MCN) harbor an invasive carcinoma in 16% of the cases, mainly tubular type, but occasionally sarcomatoid or undifferentiated, these entities being frankly rare.

Methods

We present the case of a liver MCN with an invasive component and sarcomatous degeneration.

Results

The patient was treated surgically with subsequent adjuvant chemotherapy (capecitabine), presenting tumor progression after three months with peritoneal carcinomatosis and liver recurrence. The patient died due to liver failure 4 months after surgery.

Conclusion

MCN with an invasive component and sarcomatous degeneration are very rare, present advanced stages, show aggressive behavior, and have a poor prognosis.

Keywords:

• Mucinous cystic liver neoplasm
• sarcomatous differentiation
• liver surgery
• Pancreatic cystic neoplasm

Disclosure statement

No potential conflict of interest was reported by the authors.

Additional information

Funding

The authors reported there is no funding associated with the work featured in this article.