Neurological Manifestations in Familial Mediterranean Fever: a Genotype-Phenotype Correlation Study

Figures & data

Table 1 Neurological Manifestation in FMF

PRES	Ataxia
Cerebro-vascular disease	Headache
Demyelinating diseases	Tremor
Seizure and febrile seizure	Breath holding
Focal paresis	Syncope
Visual disease	Meningitis recurrent^Citation10,Citation11
Vertigo	Pseudo tumor cerebral^Citation12

Table 2 Neurological Manifestations of Patients Regarding MEFV Results

Group	MEFV+	MEFV-	Total	P-value
Symptom	No (%)	No (%)	No (%)
Headache	69 (36.89)	78 (69.90)	147 (47.26)	0.041
Vertigo	50 (26.7)	33 (26.6)	83 (26.7)	0.975
Paresthesia	36 (19.3)	36 (29)	72 (23.2)	0.045
Tremor	27 (14.4)	26 (21)	53 (17)	0.134
Disorientation	21 (11.2)	19 (15.3)	40 (12.9)	0.291
Breath holding	9 (4.8)	14 (11.3)	23 (7.4)	0.033
Syncope	4 (2.1)	4 (3.2)	8 (2.6)	0.553
Epilepsy (seizure)	5 (2.7)	2 (1.6)	7 (2.3)	0.537
Ataxia	1 (0.5)	4 (3.2)	5 (1.6)	0.064
Total	187	124	311

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