Long term follow-up of congenital infantile fibrosarcoma of the orbital region

ABSTRACT

We present the long-term follow-up of a case of periorbital congenital infantile fibrosarcoma (CIFS) treated with chemotherapy and surgery. The tumor was detected on a routine prenatal ultrasound at 30 weeks of gestation and diagnosed via an orbital biopsy day 9 postnatal age. The patient underwent chemotherapy and surgical debulking within the first 3 months of life and has maintained complete tumor remission for 7 years. The case highlights that early recognition and prompt treatment of periorbital CIFS can lead to complete long-term remission of this uncommon malignancy.

KEYWORDS:

• Congenital infantile fibrosarcoma of orbit
• orbital disease
• orbital surgery

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The authors report no conflicts of interest. The authors alone are responsible for the content and writing of the article.

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Funding

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