Abstract
Background: Primary progressive aphasia (PPA) is a progressive language disorder in which aphasia is the first and most prominent symptom of degenerative brain disease. PPA has received increasing attention in the scientific literature over the past 30 years, but there remains a relative lack of awareness and understanding of it in the wider clinical community. As editors of the volume, Clinical Perspectives on Primary Progressive Aphasia, we invited the contributing authors to provide an up-to-date survey of research on a range of topics that are relevant to clinical practice in PPA.
Aims: The aim of this article is to address some key questions that may arise when an individual receives a diagnosis of PPA and to direct readers to additional sources of information in this volume and elsewhere that will allow them to gain further knowledge about topics of interest.
Main Contribution: We address the following questions: (1) What is PPA? (2) How is PPA diagnosed? (3) What happens to a person’s language when they have PPA? (4) How will the disease progress over time? (5) How does PPA impact a person’s life and the life of their family and friends? (6) What treatments and support are available? (7) What other services should we be providing?
Conclusions: Considerable progress has been made in our understanding of PPA and the relationship between the symptomatology, progression, pathology, and genetics of PPA. However, there are many challenges remaining, particularly in terms of ensuring that people with PPA and their families and friends receive optimal information and support at diagnosis and appropriate interventions and/or management strategies throughout their journey with PPA.
We wish to thank all the authors who have contributed so generously to this volume on Clinical Perspectives on Primary Progressive Aphasia and the people with primary progressive aphasia and their families and friends who have given their time to further our understanding of PPA, its effects on language and cognition, their impact and their potential treatment, by participating in research. We also wish to thank Chris Code and the editorial team at Psychology Press for their support and Cathleen Taylor, Senior Speech Pathologist at War Memorial Hospital Sydney, for many collegial years considering and implementing options for speech pathology service provision for people with PPA. During the preparation of this article and volume, Lyndsey Nickels was funded by Australian Research Council Future Fellowship number FT120100102. Karen Croot worked on the preparation of this volume while on a Visiting Fellowship at the Centre for Advanced Studies at the Ludwig Maximilians University, Munich, Germany.