Sexuality and quality of life in congenital hypogonadisms

Abstract

Turner syndrome and idiopathic congenital hypogonadism including Kallmann syndrome are conditions associated to a large number of widely known comorbidities that need a medical support forever. One of the characteristics shared by both conditions is the lack of sexual development that influencing the sexuality functioning and quality of life of the affected women. Few studies have been conducted to assess these topics, but they need to be considered in the treatment to all women with hypogonadism. This review on the major medical issues and psychological aspects, also focus in the present knowledge about sexual function and quality of life of women with Turner syndrome and idiopathic congenital hypogonadism, which aims to help in the comprehensive management of these patients.

Chinese abstract

特纳综合征和特发性先天性性腺功能减退症, 包括卡尔曼综合征, 这两种疾病是包含了大量广为人知的相关合并症的综合征, 需要永久的医疗支持。他们二者所共有的特征之一是性发育的缺乏, 进而影响女性患者的性功能和生活质量。目前很少有研究来评估这些问题, 但是在所有性腺功能减退症的女性患者的治疗中, 确实应该考虑。这里主要回顾了医学方面和心理方面的问题, 也关注了现有的关于Turner综合征和特发性先天性性腺功能减退患者的性功能和生活质量方面的知识, 旨在提高这些患者的综合管理。

Keywords:

• Idiopathic hypogonadotropic hypogonadism
• Kallmann syndrome
• quality of life
• sexual function
• Turner syndrome

Declaration of interest

The authors report no conflicts of interest. The authors alone are responsible for the content and writing of this article.